ICD-10-CM Instructional Notes · Guidelines Section I.A.13 · FY 2027 354 Codes
ICD-10-CM Etiology and Manifestation Codes ICD-10-CM
Some conditions have an underlying cause (the etiology) and effects in other body systems (the manifestations). ICD-10-CM codes them in pairs: a “use additional code” note at the etiology code and a “code first” note at the manifestation code, with the etiology always sequenced first. Most manifestation codes say so in their title (“in diseases classified elsewhere”); FY 2027 has 354 of them, and none may be reported as the first-listed or principal diagnosis.
✓ From the official FY 2027 ICD-10-CM Tabular ListDefinitions follow the Official Guidelines, Section I.A
354
Manifestation Codes
227
Code First Notes
73
Use Additional Code Notes
401
Code Pairs Named
How the convention works Section I.A.13
The Guidelines’ example is dementia with Parkinson’s disease. In the Alphabetic Index a code from category G20 is listed first, followed by F02.80 or F02.81- in brackets. G20 represents the underlying etiology, Parkinson’s disease, and must be sequenced first; F02.80 and F02.81- represent the manifestation of dementia in diseases classified elsewhere. The code in brackets is always sequenced second.
Some manifestation codes do not have “in diseases classified elsewhere” in the title; the same notes and the same sequencing rule apply to them.
ICD-10-CM
Manifestation Codes and What to Code First 354 codes
354 of 354 shown
Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)5 codes
- D63 Anemia in chronic diseases classified elsewhere Non-billable
- D63.8 Anemia in other chronic diseases classified elsewhere
- D72.18 Eosinophilia in diseases classified elsewhere Code first C93.1-
- D77 Other disorders of blood and blood-forming organs in diseases classified elsewhere
- D84.81 Immunodeficiency due to conditions classified elsewhere
Chapter 5: Mental and behavioural disorders (F01–F99)34 codes
- F02 Dementia in other diseases classified elsewhere Non-billable
- F02.8 Dementia in other diseases classified elsewhere, unspecified severity Non-billable
- F02.80 Dementia in other diseases classified elsewhere, unspecified severity, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety
- F02.81 Dementia in other diseases classified elsewhere, unspecified severity, with behavioral disturbance Non-billable
- F02.811 Dementia in other diseases classified elsewhere, unspecified severity, with agitation
- F02.818 Dementia in other diseases classified elsewhere, unspecified severity, with other behavioral disturbance
- F02.82 Dementia in other diseases classified elsewhere, unspecified severity, with psychotic disturbance
- F02.83 Dementia in other diseases classified elsewhere, unspecified severity, with mood disturbance
- F02.84 Dementia in other diseases classified elsewhere, unspecified severity, with anxiety
- F02.A Dementia in other diseases classified elsewhere, mild Non-billable
- F02.A0 Dementia in other diseases classified elsewhere, mild, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety
- F02.A1 Dementia in other diseases classified elsewhere, mild, with behavioral disturbance Non-billable
- F02.A11 Dementia in other diseases classified elsewhere, mild, with agitation
- F02.A18 Dementia in other diseases classified elsewhere, mild, with other behavioral disturbance
- F02.A2 Dementia in other diseases classified elsewhere, mild, with psychotic disturbance
- F02.A3 Dementia in other diseases classified elsewhere, mild, with mood disturbance
- F02.A4 Dementia in other diseases classified elsewhere, mild, with anxiety
- F02.B Dementia in other diseases classified elsewhere, moderate Non-billable
- F02.B0 Dementia in other diseases classified elsewhere, moderate, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety
- F02.B1 Dementia in other diseases classified elsewhere, moderate, with behavioral disturbance Non-billable
- F02.B11 Dementia in other diseases classified elsewhere, moderate, with agitation
- F02.B18 Dementia in other diseases classified elsewhere, moderate, with other behavioral disturbance
- F02.B2 Dementia in other diseases classified elsewhere, moderate, with psychotic disturbance
- F02.B3 Dementia in other diseases classified elsewhere, moderate, with mood disturbance
- F02.B4 Dementia in other diseases classified elsewhere, moderate, with anxiety
- F02.C Dementia in other diseases classified elsewhere, severe Non-billable
- F02.C0 Dementia in other diseases classified elsewhere, severe, without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety
- F02.C1 Dementia in other diseases classified elsewhere, severe, with behavioral disturbance Non-billable
- F02.C11 Dementia in other diseases classified elsewhere, severe, with agitation
- F02.C18 Dementia in other diseases classified elsewhere, severe, with other behavioral disturbance
- F02.C2 Dementia in other diseases classified elsewhere, severe, with psychotic disturbance
- F02.C3 Dementia in other diseases classified elsewhere, severe, with mood disturbance
- F02.C4 Dementia in other diseases classified elsewhere, severe, with anxiety
- F54 Psychological and behavioral factors associated with disorders or diseases classified elsewhere
Chapter 6: Diseases of the nervous system (G00–G99)35 codes
- G01 Meningitis in bacterial diseases classified elsewhere
- G02 Meningitis in other infectious and parasitic diseases classified elsewhere Paired from B39
- G05 Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere Non-billable
- G05.3 Encephalitis and encephalomyelitis in diseases classified elsewhere Paired from M32.19
- G05.4 Myelitis in diseases classified elsewhere
- G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere Code first B65.-
- G13 Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere Non-billable
- G13.8 Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
- G26 Extrapyramidal and movement disorders in diseases classified elsewhere
- G32 Other degenerative disorders of nervous system in diseases classified elsewhere Non-billable
- G32.0 Subacute combined degeneration of spinal cord in diseases classified elsewhere
- G32.8 Other specified degenerative disorders of nervous system in diseases classified elsewhere Non-billable
- G32.81 Cerebellar ataxia in diseases classified elsewhere Paired from K90.0
- G32.89 Other specified degenerative disorders of nervous system in diseases classified elsewhere
- G47.27 Circadian rhythm sleep disorder in conditions classified elsewhere
- G47.36 Sleep related hypoventilation in conditions classified elsewhere
- G47.37 Central sleep apnea in conditions classified elsewhere
- G47.42 Narcolepsy in conditions classified elsewhere Non-billable
- G47.421 Narcolepsy in conditions classified elsewhere with cataplexy
- G47.429 Narcolepsy in conditions classified elsewhere without cataplexy
- G47.54 Parasomnia in conditions classified elsewhere
- G53 Cranial nerve disorders in diseases classified elsewhere
- G55 Nerve root and plexus compressions in diseases classified elsewhere
- G59 Mononeuropathy in diseases classified elsewhere
- G63 Polyneuropathy in diseases classified elsewhere
- G70.81 Lambert-Eaton syndrome in disease classified elsewhere
- G73 Disorders of myoneural junction and muscle in diseases classified elsewhere Non-billable
- G73.3 Myasthenic syndromes in other diseases classified elsewhere
- G73.7 Myopathy in diseases classified elsewhere
- G91.4 Hydrocephalus in diseases classified elsewhere Paired from E88.02
- G94 Other disorders of brain in diseases classified elsewhere
- G99 Other disorders of nervous system in diseases classified elsewhere Non-billable
- G99.0 Autonomic neuropathy in diseases classified elsewhere
- G99.2 Myelopathy in diseases classified elsewhere
- G99.8 Other specified disorders of nervous system in diseases classified elsewhere
Chapter 7: Diseases of the eye and adnexa (H00–H59)7 codes
- H22 Disorders of iris and ciliary body in diseases classified elsewhere
- H28 Cataract in diseases classified elsewhere
- H32 Chorioretinal disorders in diseases classified elsewhere Paired from B39
- H36 Retinal disorders in diseases classified elsewhere Non-billable
- H36.8 Other retinal disorders in diseases classified elsewhere Non-billable
- H36.89 Other retinal disorders in diseases classified elsewhere
- H42 Glaucoma in diseases classified elsewhere
Chapter 8: Diseases of the ear and mastoid process (H60–H95)44 codes
- H62 Disorders of external ear in diseases classified elsewhere Non-billable
- H62.4 Otitis externa in other diseases classified elsewhere Non-billable
- H62.40 Otitis externa in other diseases classified elsewhere, unspecified ear
- H62.41 Otitis externa in other diseases classified elsewhere, right ear
- H62.42 Otitis externa in other diseases classified elsewhere, left ear
- H62.43 Otitis externa in other diseases classified elsewhere, bilateral
- H62.8 Other disorders of external ear in diseases classified elsewhere Non-billable
- H62.8X Other disorders of external ear in diseases classified elsewhere Non-billable
- H62.8X1 Other disorders of right external ear in diseases classified elsewhere
- H62.8X2 Other disorders of left external ear in diseases classified elsewhere
- H62.8X3 Other disorders of external ear in diseases classified elsewhere, bilateral
- H62.8X9 Other disorders of external ear in diseases classified elsewhere, unspecified ear
- H67 Otitis media in diseases classified elsewhere Non-billablePaired from E88.02
- H67.1 Otitis media in diseases classified elsewhere, right ear
- H67.2 Otitis media in diseases classified elsewhere, left ear
- H67.3 Otitis media in diseases classified elsewhere, bilateral
- H67.9 Otitis media in diseases classified elsewhere, unspecified ear
- H75 Other disorders of middle ear and mastoid in diseases classified elsewhere Non-billable
- H75.0 Mastoiditis in infectious and parasitic diseases classified elsewhere Non-billable
- H75.00 Mastoiditis in infectious and parasitic diseases classified elsewhere, unspecified ear
- H75.01 Mastoiditis in infectious and parasitic diseases classified elsewhere, right ear
- H75.02 Mastoiditis in infectious and parasitic diseases classified elsewhere, left ear
- H75.03 Mastoiditis in infectious and parasitic diseases classified elsewhere, bilateral
- H75.8 Other specified disorders of middle ear and mastoid in diseases classified elsewhere Non-billable
- H75.80 Other specified disorders of middle ear and mastoid in diseases classified elsewhere, unspecified ear
- H75.81 Other specified disorders of right middle ear and mastoid in diseases classified elsewhere
- H75.82 Other specified disorders of left middle ear and mastoid in diseases classified elsewhere
- H75.83 Other specified disorders of middle ear and mastoid in diseases classified elsewhere, bilateral
- H82 Vertiginous syndromes in diseases classified elsewhere Non-billable
- H82.1 Vertiginous syndromes in diseases classified elsewhere, right ear
- H82.2 Vertiginous syndromes in diseases classified elsewhere, left ear
- H82.3 Vertiginous syndromes in diseases classified elsewhere, bilateral
- H82.9 Vertiginous syndromes in diseases classified elsewhere, unspecified ear
- H94 Other disorders of ear in diseases classified elsewhere Non-billable
- H94.0 Acoustic neuritis in infectious and parasitic diseases classified elsewhere Non-billable
- H94.00 Acoustic neuritis in infectious and parasitic diseases classified elsewhere, unspecified ear
- H94.01 Acoustic neuritis in infectious and parasitic diseases classified elsewhere, right ear
- H94.02 Acoustic neuritis in infectious and parasitic diseases classified elsewhere, left ear
- H94.03 Acoustic neuritis in infectious and parasitic diseases classified elsewhere, bilateral
- H94.8 Other specified disorders of ear in diseases classified elsewhere Non-billableCode first A50.0
- H94.80 Other specified disorders of ear in diseases classified elsewhere, unspecified ear
- H94.81 Other specified disorders of right ear in diseases classified elsewhere
- H94.82 Other specified disorders of left ear in diseases classified elsewhere
- H94.83 Other specified disorders of ear in diseases classified elsewhere, bilateral
Chapter 9: Diseases of the circulatory system (I00–I99)13 codes
- I31.31 Malignant pericardial effusion in diseases classified elsewhere
- I32 Pericarditis in diseases classified elsewhere Paired from B39
- I39 Endocarditis and heart valve disorders in diseases classified elsewhere Code first A78Paired from B39
- I41 Myocarditis in diseases classified elsewhere
- I43 Cardiomyopathy in diseases classified elsewhere
- I52 Other heart disorders in diseases classified elsewhere
- I68 Cerebrovascular disorders in diseases classified elsewhere Non-billable
- I68.2 Cerebral arteritis in other diseases classified elsewhere
- I68.8 Other cerebrovascular disorders in diseases classified elsewhere
- I79 Disorders of arteries, arterioles and capillaries in diseases classified elsewhere Non-billable
- I79.0 Aneurysm of aorta in diseases classified elsewhere
- I79.1 Aortitis in diseases classified elsewhere
- I79.8 Other disorders of arteries, arterioles and capillaries in diseases classified elsewhere Code first E85.-
Chapter 10: Diseases of the respiratory system (J00–J99)7 codes
- J17 Pneumonia in diseases classified elsewhere
- J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere Non-billable
- J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
- J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J91 Pleural effusion in conditions classified elsewhere Non-billable
- J91.8 Pleural effusion in other conditions classified elsewhere
- J99 Respiratory disorders in diseases classified elsewhere Paired from E88.02
Chapter 11: Diseases of the digestive system (K00–K95)5 codes
- K23 Disorders of esophagus in diseases classified elsewhere Code first A50.5
- K67 Disorders of peritoneum in infectious diseases classified elsewhere
- K77 Liver disorders in diseases classified elsewhere
- K82.A Disorders of gallbladder in diseases classified elsewhere Non-billable
- K87 Disorders of gallbladder, biliary tract and pancreas in diseases classified elsewhere
Chapter 12: Diseases of the skin and subcutaneous tissue (L00–L99)6 codes
- L14 Bullous disorders in diseases classified elsewhere
- L45 Papulosquamous disorders in diseases classified elsewhere
- L54 Erythema in diseases classified elsewhere
- L62 Nail disorders in diseases classified elsewhere Code first M89.4-
- L86 Keratoderma in diseases classified elsewhere Code first M02.3-
- L99 Other disorders of skin and subcutaneous tissue in diseases classified elsewhere Code first E85.-
Chapter 13: Diseases of the musculoskeletal system and connective tissue (M00–M99)179 codes
- M01 Direct infections of joint in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X Direct infection of joint in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X0 Direct infection of unspecified joint in infectious and parasitic diseases classified elsewhere
- M01.X1 Direct infection of shoulder joint in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X11 Direct infection of right shoulder in infectious and parasitic diseases classified elsewhere
- M01.X12 Direct infection of left shoulder in infectious and parasitic diseases classified elsewhere
- M01.X19 Direct infection of unspecified shoulder in infectious and parasitic diseases classified elsewhere
- M01.X2 Direct infection of elbow in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X21 Direct infection of right elbow in infectious and parasitic diseases classified elsewhere
- M01.X22 Direct infection of left elbow in infectious and parasitic diseases classified elsewhere
- M01.X29 Direct infection of unspecified elbow in infectious and parasitic diseases classified elsewhere
- M01.X3 Direct infection of wrist in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X31 Direct infection of right wrist in infectious and parasitic diseases classified elsewhere
- M01.X32 Direct infection of left wrist in infectious and parasitic diseases classified elsewhere
- M01.X39 Direct infection of unspecified wrist in infectious and parasitic diseases classified elsewhere
- M01.X4 Direct infection of hand in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X41 Direct infection of right hand in infectious and parasitic diseases classified elsewhere
- M01.X42 Direct infection of left hand in infectious and parasitic diseases classified elsewhere
- M01.X49 Direct infection of unspecified hand in infectious and parasitic diseases classified elsewhere
- M01.X5 Direct infection of hip in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X51 Direct infection of right hip in infectious and parasitic diseases classified elsewhere
- M01.X52 Direct infection of left hip in infectious and parasitic diseases classified elsewhere
- M01.X59 Direct infection of unspecified hip in infectious and parasitic diseases classified elsewhere
- M01.X6 Direct infection of knee in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X61 Direct infection of right knee in infectious and parasitic diseases classified elsewhere
- M01.X62 Direct infection of left knee in infectious and parasitic diseases classified elsewhere
- M01.X69 Direct infection of unspecified knee in infectious and parasitic diseases classified elsewhere
- M01.X7 Direct infection of ankle and foot in infectious and parasitic diseases classified elsewhere Non-billable
- M01.X71 Direct infection of right ankle and foot in infectious and parasitic diseases classified elsewhere
- M01.X72 Direct infection of left ankle and foot in infectious and parasitic diseases classified elsewhere
- M01.X79 Direct infection of unspecified ankle and foot in infectious and parasitic diseases classified elsewhere
- M01.X8 Direct infection of vertebrae in infectious and parasitic diseases classified elsewhere
- M01.X9 Direct infection of multiple joints in infectious and parasitic diseases classified elsewhere
- M14 Arthropathies in other diseases classified elsewhere Non-billable
- M14.8 Arthropathies in other specified diseases classified elsewhere Non-billablePaired from L51
- M14.80 Arthropathies in other specified diseases classified elsewhere, unspecified site
- M14.81 Arthropathies in other specified diseases classified elsewhere, shoulder Non-billable
- M14.811 Arthropathies in other specified diseases classified elsewhere, right shoulder
- M14.812 Arthropathies in other specified diseases classified elsewhere, left shoulder
- M14.819 Arthropathies in other specified diseases classified elsewhere, unspecified shoulder
- M14.82 Arthropathies in other specified diseases classified elsewhere, elbow Non-billable
- M14.821 Arthropathies in other specified diseases classified elsewhere, right elbow
- M14.822 Arthropathies in other specified diseases classified elsewhere, left elbow
- M14.829 Arthropathies in other specified diseases classified elsewhere, unspecified elbow
- M14.83 Arthropathies in other specified diseases classified elsewhere, wrist Non-billable
- M14.831 Arthropathies in other specified diseases classified elsewhere, right wrist
- M14.832 Arthropathies in other specified diseases classified elsewhere, left wrist
- M14.839 Arthropathies in other specified diseases classified elsewhere, unspecified wrist
- M14.84 Arthropathies in other specified diseases classified elsewhere, hand Non-billable
- M14.841 Arthropathies in other specified diseases classified elsewhere, right hand
- M14.842 Arthropathies in other specified diseases classified elsewhere, left hand
- M14.849 Arthropathies in other specified diseases classified elsewhere, unspecified hand
- M14.85 Arthropathies in other specified diseases classified elsewhere, hip Non-billable
- M14.851 Arthropathies in other specified diseases classified elsewhere, right hip
- M14.852 Arthropathies in other specified diseases classified elsewhere, left hip
- M14.859 Arthropathies in other specified diseases classified elsewhere, unspecified hip
- M14.86 Arthropathies in other specified diseases classified elsewhere, knee Non-billable
- M14.861 Arthropathies in other specified diseases classified elsewhere, right knee
- M14.862 Arthropathies in other specified diseases classified elsewhere, left knee
- M14.869 Arthropathies in other specified diseases classified elsewhere, unspecified knee
- M14.87 Arthropathies in other specified diseases classified elsewhere, ankle and foot Non-billable
- M14.871 Arthropathies in other specified diseases classified elsewhere, right ankle and foot
- M14.872 Arthropathies in other specified diseases classified elsewhere, left ankle and foot
- M14.879 Arthropathies in other specified diseases classified elsewhere, unspecified ankle and foot
- M14.88 Arthropathies in other specified diseases classified elsewhere, vertebrae
- M14.89 Arthropathies in other specified diseases classified elsewhere, multiple sites
- M36 Systemic disorders of connective tissue in diseases classified elsewhere Non-billable
- M36.4 Arthropathy in hypersensitivity reactions classified elsewhere
- M36.8 Systemic disorders of connective tissue in other diseases classified elsewhere
- M49 Spondylopathies in diseases classified elsewhere Non-billable
- M49.8 Spondylopathy in diseases classified elsewhere Non-billable
- M49.80 Spondylopathy in diseases classified elsewhere, site unspecified
- M49.81 Spondylopathy in diseases classified elsewhere, occipito-atlanto-axial region
- M49.82 Spondylopathy in diseases classified elsewhere, cervical region
- M49.83 Spondylopathy in diseases classified elsewhere, cervicothoracic region
- M49.84 Spondylopathy in diseases classified elsewhere, thoracic region
- M49.85 Spondylopathy in diseases classified elsewhere, thoracolumbar region
- M49.86 Spondylopathy in diseases classified elsewhere, lumbar region
- M49.87 Spondylopathy in diseases classified elsewhere, lumbosacral region
- M49.88 Spondylopathy in diseases classified elsewhere, sacral and sacrococcygeal region
- M49.89 Spondylopathy in diseases classified elsewhere, multiple sites in spine
- M63 Disorders of muscle in diseases classified elsewhere Non-billable
- M63.8 Disorders of muscle in diseases classified elsewhere Non-billable
- M63.80 Disorders of muscle in diseases classified elsewhere, unspecified site
- M63.81 Disorders of muscle in diseases classified elsewhere, shoulder Non-billable
- M63.811 Disorders of muscle in diseases classified elsewhere, right shoulder
- M63.812 Disorders of muscle in diseases classified elsewhere, left shoulder
- M63.819 Disorders of muscle in diseases classified elsewhere, unspecified shoulder
- M63.82 Disorders of muscle in diseases classified elsewhere, upper arm Non-billable
- M63.821 Disorders of muscle in diseases classified elsewhere, right upper arm
- M63.822 Disorders of muscle in diseases classified elsewhere, left upper arm
- M63.829 Disorders of muscle in diseases classified elsewhere, unspecified upper arm
- M63.83 Disorders of muscle in diseases classified elsewhere, forearm Non-billable
- M63.831 Disorders of muscle in diseases classified elsewhere, right forearm
- M63.832 Disorders of muscle in diseases classified elsewhere, left forearm
- M63.839 Disorders of muscle in diseases classified elsewhere, unspecified forearm
- M63.84 Disorders of muscle in diseases classified elsewhere, hand Non-billable
- M63.841 Disorders of muscle in diseases classified elsewhere, right hand
- M63.842 Disorders of muscle in diseases classified elsewhere, left hand
- M63.849 Disorders of muscle in diseases classified elsewhere, unspecified hand
- M63.85 Disorders of muscle in diseases classified elsewhere, thigh Non-billable
- M63.851 Disorders of muscle in diseases classified elsewhere, right thigh
- M63.852 Disorders of muscle in diseases classified elsewhere, left thigh
- M63.859 Disorders of muscle in diseases classified elsewhere, unspecified thigh
- M63.86 Disorders of muscle in diseases classified elsewhere, lower leg Non-billable
- M63.861 Disorders of muscle in diseases classified elsewhere, right lower leg
- M63.862 Disorders of muscle in diseases classified elsewhere, left lower leg
- M63.869 Disorders of muscle in diseases classified elsewhere, unspecified lower leg
- M63.87 Disorders of muscle in diseases classified elsewhere, ankle and foot Non-billable
- M63.871 Disorders of muscle in diseases classified elsewhere, right ankle and foot
- M63.872 Disorders of muscle in diseases classified elsewhere, left ankle and foot
- M63.879 Disorders of muscle in diseases classified elsewhere, unspecified ankle and foot
- M63.88 Disorders of muscle in diseases classified elsewhere, other site
- M63.89 Disorders of muscle in diseases classified elsewhere, multiple sites
- M90 Osteopathies in diseases classified elsewhere Non-billable
- M90.5 Osteonecrosis in diseases classified elsewhere Non-billable
- M90.50 Osteonecrosis in diseases classified elsewhere, unspecified site
- M90.51 Osteonecrosis in diseases classified elsewhere, shoulder Non-billable
- M90.511 Osteonecrosis in diseases classified elsewhere, right shoulder
- M90.512 Osteonecrosis in diseases classified elsewhere, left shoulder
- M90.519 Osteonecrosis in diseases classified elsewhere, unspecified shoulder
- M90.52 Osteonecrosis in diseases classified elsewhere, upper arm Non-billable
- M90.521 Osteonecrosis in diseases classified elsewhere, right upper arm
- M90.522 Osteonecrosis in diseases classified elsewhere, left upper arm
- M90.529 Osteonecrosis in diseases classified elsewhere, unspecified upper arm
- M90.53 Osteonecrosis in diseases classified elsewhere, forearm Non-billable
- M90.531 Osteonecrosis in diseases classified elsewhere, right forearm
- M90.532 Osteonecrosis in diseases classified elsewhere, left forearm
- M90.539 Osteonecrosis in diseases classified elsewhere, unspecified forearm
- M90.54 Osteonecrosis in diseases classified elsewhere, hand Non-billable
- M90.541 Osteonecrosis in diseases classified elsewhere, right hand
- M90.542 Osteonecrosis in diseases classified elsewhere, left hand
- M90.549 Osteonecrosis in diseases classified elsewhere, unspecified hand
- M90.55 Osteonecrosis in diseases classified elsewhere, thigh Non-billable
- M90.551 Osteonecrosis in diseases classified elsewhere, right thigh
- M90.552 Osteonecrosis in diseases classified elsewhere, left thigh
- M90.559 Osteonecrosis in diseases classified elsewhere, unspecified thigh
- M90.56 Osteonecrosis in diseases classified elsewhere, lower leg Non-billable
- M90.561 Osteonecrosis in diseases classified elsewhere, right lower leg
- M90.562 Osteonecrosis in diseases classified elsewhere, left lower leg
- M90.569 Osteonecrosis in diseases classified elsewhere, unspecified lower leg
- M90.57 Osteonecrosis in diseases classified elsewhere, ankle and foot Non-billable
- M90.571 Osteonecrosis in diseases classified elsewhere, right ankle and foot
- M90.572 Osteonecrosis in diseases classified elsewhere, left ankle and foot
- M90.579 Osteonecrosis in diseases classified elsewhere, unspecified ankle and foot
- M90.58 Osteonecrosis in diseases classified elsewhere, other site
- M90.59 Osteonecrosis in diseases classified elsewhere, multiple sites
- M90.8 Osteopathy in diseases classified elsewhere Non-billable
- M90.80 Osteopathy in diseases classified elsewhere, unspecified site
- M90.81 Osteopathy in diseases classified elsewhere, shoulder Non-billable
- M90.811 Osteopathy in diseases classified elsewhere, right shoulder
- M90.812 Osteopathy in diseases classified elsewhere, left shoulder
- M90.819 Osteopathy in diseases classified elsewhere, unspecified shoulder
- M90.82 Osteopathy in diseases classified elsewhere, upper arm Non-billable
- M90.821 Osteopathy in diseases classified elsewhere, right upper arm
- M90.822 Osteopathy in diseases classified elsewhere, left upper arm
- M90.829 Osteopathy in diseases classified elsewhere, unspecified upper arm
- M90.83 Osteopathy in diseases classified elsewhere, forearm Non-billable
- M90.831 Osteopathy in diseases classified elsewhere, right forearm
- M90.832 Osteopathy in diseases classified elsewhere, left forearm
- M90.839 Osteopathy in diseases classified elsewhere, unspecified forearm
- M90.84 Osteopathy in diseases classified elsewhere, hand Non-billable
- M90.841 Osteopathy in diseases classified elsewhere, right hand
- M90.842 Osteopathy in diseases classified elsewhere, left hand
- M90.849 Osteopathy in diseases classified elsewhere, unspecified hand
- M90.85 Osteopathy in diseases classified elsewhere, thigh Non-billable
- M90.851 Osteopathy in diseases classified elsewhere, right thigh
- M90.852 Osteopathy in diseases classified elsewhere, left thigh
- M90.859 Osteopathy in diseases classified elsewhere, unspecified thigh
- M90.86 Osteopathy in diseases classified elsewhere, lower leg Non-billable
- M90.861 Osteopathy in diseases classified elsewhere, right lower leg
- M90.862 Osteopathy in diseases classified elsewhere, left lower leg
- M90.869 Osteopathy in diseases classified elsewhere, unspecified lower leg
- M90.87 Osteopathy in diseases classified elsewhere, ankle and foot Non-billable
- M90.871 Osteopathy in diseases classified elsewhere, right ankle and foot
- M90.872 Osteopathy in diseases classified elsewhere, left ankle and foot
- M90.879 Osteopathy in diseases classified elsewhere, unspecified ankle and foot
- M90.88 Osteopathy in diseases classified elsewhere, other site
- M90.89 Osteopathy in diseases classified elsewhere, multiple sites
Chapter 14: Diseases of the genitourinary system (N00–N99)13 codes
- N08 Glomerular disorders in diseases classified elsewhere
- N16 Renal tubulo-interstitial disorders in diseases classified elsewhere
- N22 Calculus of urinary tract in diseases classified elsewhere
- N29 Other disorders of kidney and ureter in diseases classified elsewhere
- N33 Bladder disorders in diseases classified elsewhere
- N37 Urethral disorders in diseases classified elsewhere
- N48.32 Priapism due to disease classified elsewhere
- N51 Disorders of male genital organs in diseases classified elsewhere
- N52.1 Erectile dysfunction due to diseases classified elsewhere
- N74 Female pelvic inflammatory disorders in diseases classified elsewhere
- N77 Vulvovaginal ulceration and inflammation in diseases classified elsewhere Non-billable
- N77.0 Ulceration of vulva in diseases classified elsewhere Code first M35.2
- N77.1 Vaginitis, vulvitis and vulvovaginitis in diseases classified elsewhere Code first B80
“Code first” shows the codes named in the code’s Code First note; a note printed on a category is shown once, on the category, and applies to every code under it. Some notes name only “the underlying condition” without a code. “Paired from” shows etiology codes whose Use Additional Code note points to this code or its category.
ICD-10-CM
Etiology Codes That Point to a Manifestation 38 codes and categories
Codes whose Use Additional Code note names a manifestation code. The code below is reported first; the manifestation it names follows.
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- code for any associated fever (R50.81)
- D57.09 Hb-SS disease with crisis with other specified complication
- priapism (N48.32)
- D57.218 Sickle-cell/Hb-C disease with crisis with other specified complication
- priapism (N48.32)
- D57.418 Sickle-cell thalassemia, unspecified, with crisis with other specified complication
- priapism (N48.32)
- D57.438 Sickle-cell thalassemia beta zero with crisis with other specified complication
- priapism (N48.32)
- D57.458 Sickle-cell thalassemia beta plus with crisis with other specified complication
- priapism (N48.32)
- D57.818 Other sickle-cell disorders with crisis with other specified complication
- priapism (N48.32)
- fever (R50.81)
- E72.03 Lowe's syndrome
- code for associated glaucoma (H42)
- E88.02 Plasminogen deficiency
- F01.518 Vascular dementia, unspecified severity, with other behavioral disturbance
- code, if applicable, to identify wandering in vascular dementia (Z91.83)
- F01.A18 Vascular dementia, mild, with other behavioral disturbance
- code, if applicable, to identify wandering in vascular dementia (Z91.83)
- F01.B18 Vascular dementia, moderate, with other behavioral disturbance
- code, if applicable, to identify wandering in vascular dementia (Z91.83)
- F01.C18 Vascular dementia, severe, with other behavioral disturbance
- code, if applicable, to identify wandering in vascular dementia (Z91.83)
- F02.818 Dementia in other diseases classified elsewhere, unspecified severity, with other behavioral disturbance
- code, if applicable, to identify wandering in dementia in conditions classified elsewhere (Z91.83)
- F02.A18 Dementia in other diseases classified elsewhere, mild, with other behavioral disturbance
- code, if applicable, to identify wandering in dementia in conditions classified elsewhere (Z91.83)
- F02.B18 Dementia in other diseases classified elsewhere, moderate, with other behavioral disturbance
- code, if applicable, to identify wandering in dementia in conditions classified elsewhere (Z91.83)
- F02.C18 Dementia in other diseases classified elsewhere, severe, with other behavioral disturbance
- code, if applicable, to identify wandering in dementia in conditions classified elsewhere (Z91.83)
- F03.918 Unspecified dementia, unspecified severity, with other behavioral disturbance
- code, if applicable, to identify wandering in unspecified dementia (Z91.83)
- F03.A18 Unspecified dementia, mild, with other behavioral disturbance
- code, if applicable, to identify wandering in unspecified dementia (Z91.83)
- F03.B18 Unspecified dementia, moderate, with other behavioral disturbance
- code, if applicable, to identify wandering in unspecified dementia (Z91.83)
- F03.C18 Unspecified dementia, severe, with other behavioral disturbance
- code, if applicable, to identify wandering in unspecified dementia (Z91.83)
- G10 Huntington's disease
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
- J09.X2 Influenza due to identified novel influenza A virus with other respiratory manifestations
- pleural effusion (J91.8)
- J10.1 Influenza due to other identified influenza virus with other respiratory manifestations
- code for associated pleural effusion, if applicable (J91.8)
- J11.1 Influenza due to unidentified influenza virus with other respiratory manifestations
- code for associated pleural effusion, if applicable (J91.8)
- K90.0 Celiac disease
- gluten ataxia (G32.81)
- arthropathy associated with dermatological disorders (M14.8-)
- Autonomic neuropathy in diseases classified elsewhere (G99.0)
- Calculus of urinary tract in diseases classified elsewhere (N22)
- Cardiomyopathy in diseases classified elsewhere (I43)
- Disorders of external ear in diseases classified elsewhere (H61.1-, H62.8-)
- Disorders of iris and ciliary body in diseases classified elsewhere (H22)
- Glomerular disorders in diseases classified elsewhere (N08)
- Autonomic neuropathy in diseases classified elsewhere (G99.0)
- Calculus of urinary tract in diseases classified elsewhere (N22)
- Cardiomyopathy in diseases classified elsewhere (I43)
- Disorders of external ear in diseases classified elsewhere (H61.1-, H62.8-)
- Disorders of iris and ciliary body in diseases classified elsewhere (H22)
- Glomerular disorders in diseases classified elsewhere (N08)
- M32.19 Other organ or system involvement in systemic lupus erythematosus
- code(s) to identify organ or system involvement, such as encephalitis (G05.3)
- Q13.1 Absence of iris
- code for associated glaucoma (H42)
- Q13.81 Rieger anomaly
- code for associated glaucoma (H42)
Questions About Etiology and Manifestation Codes
Can a manifestation code be the principal diagnosis?
No. “In diseases classified elsewhere” codes are never permitted to be used as first-listed or principal diagnosis codes. They must be used together with a code for the underlying condition and listed after it (Section I.A.13).
What does “in diseases classified elsewhere” mean?
It marks a manifestation code: the condition is caused by a disease coded in another part of the classification. The title itself tells you the code is part of the etiology/manifestation convention and needs the underlying condition coded first.
Are there manifestation codes without “in diseases classified elsewhere” in the title?
Yes. For those codes there is still a “use additional code” note at the etiology code and a “code first” note at the manifestation code, and the same sequencing rule applies. The Code First notes page lists every one.
How do I find the manifestation code in the Alphabetic Index?
Both conditions are listed together, the etiology code first and the manifestation code in brackets, for example Dementia, in Parkinson’s disease: G20.- [F02.80]. The code in brackets is always sequenced second.
Official Sources & Methodology
Every note on these pages is loaded verbatim from the FY 2027 ICD-10-CM Tabular List. Code references inside the notes are matched against the FY 2027 code set, so every link opens a valid code; scope counts (“applies to N codes”) count the billable codes under the note’s chapter, block or category.
- CMS ICD-10-CM FilesThe Tabular List (XML) that every note, note type and code reference on ICD List comes from.
- ICD-10-CM Official Guidelines for Coding and Reporting FY 2027Section I.A, Conventions for the ICD-10-CM, defines each note type; the definitions on these pages follow its wording.
ICD List is not affiliated with CMS or NCHS. These pages are a coding reference; the Tabular List and the Official Guidelines remain the authority.
Related References
Source: FY 2027 ICD-10-CM Tabular List (CMS and NCHS) and the ICD-10-CM Official Guidelines for Coding and Reporting FY 2027, Section I.A. ICD List is not affiliated with CMS or NCHS.
