Not Valid for Submission
A81.0 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of creutzfeldt-jakob disease. The code is not specific and is NOT valid for the year 2022 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.
Specific Coding for Creutzfeldt-Jakob disease
Non-specific codes like A81.0 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for creutzfeldt-jakob disease:
- PRION PROTEINS-. membrane glycosylphosphatidylinositol anchored glycoproteins that may aggregate into rod like structures. the prion protein prnp gene is characterized by five tandem repeat sequences that encode a highly unstable protein region of five octapeptide repeats. mutations in the repeat region and elsewhere in this gene are associated with creutzfeldt jakob disease; fatal familial insomnia; gerstmann straussler disease; huntington disease like 1 and kuru.
- CREUTZFELDT JAKOB SYNDROME-. a rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. affected individuals may present with sleep disturbances personality changes ataxia; aphasia visual loss weakness muscle atrophy myoclonus progressive dementia and death within one year of disease onset. a familial form exhibiting autosomal dominant inheritance and a new variant cjd potentially associated with encephalopathy bovine spongiform have been described. pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of prions. from n engl j med 1998 dec 31;33927
Information for Patients
Creutzfeldt-Jakob disease (CJD) is a rare, degenerative brain disorder. Symptoms usually start around age 60. Memory problems, behavior changes, vision problems, and poor muscle coordination progress quickly to dementia, coma, and death. Most patients die within a year.
The three main categories of CJD are
- Sporadic CJD, which occurs for no known reason
- Hereditary CJD, which runs in families
- Acquired CJD, which occurs from contact with infected tissue, usually during a medical procedure
Cattle can get a disease related to CJD called bovine spongiform encephalopathy (BSE) or "mad cow disease." There is concern that people can get a variant of CJD from eating beef from an infected animal, but there is no direct proof to support this.
NIH: National Institute of Neurological Disorders and Stroke
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Prion disease represents a group of conditions that affect the nervous system in humans and animals. In people, these conditions impair brain function, causing changes in memory, personality, and behavior; a decline in intellectual function (dementia); and abnormal movements, particularly difficulty with coordinating movements (ataxia). The signs and symptoms of prion disease typically begin in adulthood and worsen with time, leading to death within a few months to several years.
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