2026 ICD-10-CM Diagnosis Code L86Keratoderma in diseases classified elsewhere
ICD-10-CM Codes›L00–L99›L80-L99›L86
- Billable — Valid for Submission
- Not Chronic
L86 is a billable ICD-10-CM diagnosis code for keratoderma in diseases classified elsewhere. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. The code is a manifestation code that cannot be reported as the principal diagnosis. Coders also document this condition as keratoderma due to Dowling-Meara type epidermolysis bullosa simplex. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified skin disorders.
Code Identity
Code Classification
Code EditsBilling
Medicare Code Editor checks that affect claim validity for L86.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Keratoderma due to Dowling-Meara type epidermolysis bullosa simplex
- Palmoplantar keratoderma with leukoplakia
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Code First
- underlying disease, such as:
- Reiter's disease M02.3
Type 1 Excludes
- gonococcal keratoderma A54.89
- gonococcal keratosis A54.89
- keratoderma due to vitamin A deficiency E50.8
- keratosis due to vitamin A deficiency E50.8
- xeroderma due to vitamin A deficiency E50.8
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Keratoderma, keratodermia(congenital) (palmaris et plantaris) (symmetrical)
- acquired
- in diseases classified elsewhere
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Palmoplantar Keratoderma with Leukoplakia
a hereditary syndrome this is characterized by palmoplantar keratoderma accompanied by leukoplakia and may be associated with a high lifetime risk of esophageal cancer, as seen in howel-evans syndrome.
Patient EducationClinical
Skin Conditions
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
The full article covers:
- What does your skin do?
- What problems and conditions can affect your skin?
- How can I keep my skin healthy?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert L86 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About L86Overview
Is L86 (Keratoderma in diseases classified elsewhere) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report keratoderma in diseases classified elsewhere on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does L86 group to?
On inpatient claims, keratoderma in diseases classified elsewhere maps to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.
Can L86 be a principal diagnosis?
No. This is a manifestation code: keratoderma in diseases classified elsewhere describes the manifestation of an underlying disease rather than the disease itself, so the underlying condition is sequenced first.
What is the ICD-9 equivalent of L86?
Under the General Equivalence Mappings, keratoderma in diseases classified elsewhere converts to ICD-9-CM 701.1 (keratoderma, acquired). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.
