2026 ICD-10-CM Diagnosis Code G10Huntington's disease

ICD-10-CM Codes›G00–G99›G10-G14›G10

ICD-10-CM G10
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G10 is a billable ICD-10-CM diagnosis code for Huntington's disease. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G10
Billable Status
Yes — Valid for Submission
Code Describes
Huntington's disease
Chapter
G10-G14
Systemic atrophies primarily affecting the central nervous system

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG10Huntington's disease
This CodeG10Huntington's disease

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Akinetic-rigid form of Huntington's disease
  • Altered behavior in Huntington's dementia
  • Atrophy of caudate nucleus
  • Chorea co-occurrent and due to Huntington disease-like condition
  • Dementia due to genetic disease
  • Dementia due to Huntington chorea
  • Huntington disease-like 2
  • Huntington disease-like syndrome
  • Huntington's chorea
  • Juvenile onset Huntington's disease
  • Late onset Huntington's disease
  • Progressive chorea

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Huntington's chorea
  • Huntington's dementia

Use Additional Code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Chorea(chronic) (gravis) (posthemiplegic) (senile) (spasmodic)
      • hereditary
    • Chorea(chronic) (gravis) (posthemiplegic) (senile) (spasmodic)
      • Huntington's
    • Chorea(chronic) (gravis) (posthemiplegic) (senile) (spasmodic)
      • progressive
        • hereditary
    • Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
      • in (due to)
        • Huntington's disease or chorea
    • Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
      • in (due to)
        • Huntington's disease or chorea
          • with behavioral disturbance
    • Disease, diseased
      • Huntington's
    • Disease, diseased
      • Huntington's
        • with dementia
    • Huntington's disease or chorea
    • Huntington's disease or chorea
      • with dementia
    • Huntington's disease or chorea
      • with dementia
        • with behavioral disturbance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Huntington's Disease

Huntington's disease (HD) is an inherited disease that causes certain nerve cells in the brain to waste away. People are born with the defective gene, but symptoms usually don't appear until middle age. Early symptoms of HD may include uncontrolled movements, clumsiness, and balance problems.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G10 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
333.4 Huntington's chorea
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G10Overview

Is G10 (Huntington's disease) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report Huntington's disease on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of G10?

Under the General Equivalence Mappings, Huntington's disease converts to ICD-9-CM 333.4 (Huntington's chorea). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.