2022 ICD-10-CM Code E70

Disorders of aromatic amino-acid metabolism

Version 2021

Not Valid for Submission

ICD-10:E70
Short Description:Disorders of aromatic amino-acid metabolism
Long Description:Disorders of aromatic amino-acid metabolism

Code Classification

  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Metabolic disorders (E70-E88)
      • Disorders of aromatic amino-acid metabolism (E70)

E70 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of disorders of aromatic amino-acid metabolism. The code is not specific and is NOT valid for the year 2022 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding for Disorders of aromatic amino-acid metabolism

Non-specific codes like E70 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for disorders of aromatic amino-acid metabolism:

  • BILLABLE CODE - Use E70.0 for Classical phenylketonuria
  • BILLABLE CODE - Use E70.1 for Other hyperphenylalaninemias
  • NON-BILLABLE CODE - E70.2 for Disorders of tyrosine metabolism
  • BILLABLE CODE - Use E70.20 for Disorder of tyrosine metabolism, unspecified
  • BILLABLE CODE - Use E70.21 for Tyrosinemia
  • BILLABLE CODE - Use E70.29 for Other disorders of tyrosine metabolism
  • NON-BILLABLE CODE - E70.3 for Albinism
  • BILLABLE CODE - Use E70.30 for Albinism, unspecified
  • NON-BILLABLE CODE - E70.31 for Ocular albinism
  • NON-BILLABLE CODE - E70.32 for Oculocutaneous albinism
  • NON-BILLABLE CODE - E70.33 for Albinism with hematologic abnormality
  • BILLABLE CODE - Use E70.39 for Other specified albinism
  • NON-BILLABLE CODE - E70.4 for Disorders of histidine metabolism
  • BILLABLE CODE - Use E70.40 for Disorders of histidine metabolism, unspecified
  • BILLABLE CODE - Use E70.41 for Histidinemia
  • BILLABLE CODE - Use E70.49 for Other disorders of histidine metabolism
  • BILLABLE CODE - Use E70.5 for Disorders of tryptophan metabolism
  • NON-BILLABLE CODE - E70.8 for Other disorders of aromatic amino-acid metabolism
  • BILLABLE CODE - Use E70.81 for Aromatic L-amino acid decarboxylase deficiency
  • BILLABLE CODE - Use E70.89 for Other disorders of aromatic amino-acid metabolism
  • BILLABLE CODE - Use E70.9 for Disorder of aromatic amino-acid metabolism, unspecified

Information for Patients


Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.

A metabolic disorder occurs when abnormal chemical reactions in your body disrupt this process. When this happens, you might have too much of some substances or too little of other ones that you need to stay healthy. There are different groups of disorders. Some affect the breakdown of amino acids, carbohydrates, or lipids. Another group, mitochondrial diseases, affects the parts of the cells that produce the energy.

You can develop a metabolic disorder when some organs, such as your liver or pancreas, become diseased or do not function normally. Diabetes is an example.


[Learn More in MedlinePlus]

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)