ICD-10-CM Code E70

Disorders of aromatic amino-acid metabolism

Version 2021 Non-Billable Code

Not Valid for Submission

E70 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of disorders of aromatic amino-acid metabolism. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions.

ICD-10:E70
Short Description:Disorders of aromatic amino-acid metabolism
Long Description:Disorders of aromatic amino-acid metabolism

Consider the following ICD-10 codes with a higher level of specificity:

  • E70.0 - Classical phenylketonuria
  • E70.1 - Other hyperphenylalaninemias
  • E70.2 - Disorders of tyrosine metabolism
  • E70.20 - Disorder of tyrosine metabolism, unspecified
  • E70.21 - Tyrosinemia
  • E70.29 - Other disorders of tyrosine metabolism
  • E70.3 - Albinism
  • E70.30 - Albinism, unspecified
  • E70.31 - Ocular albinism
  • E70.310 - X-linked ocular albinism
  • E70.311 - Autosomal recessive ocular albinism
  • E70.318 - Other ocular albinism
  • E70.319 - Ocular albinism, unspecified
  • E70.32 - Oculocutaneous albinism
  • E70.320 - Tyrosinase negative oculocutaneous albinism
  • E70.321 - Tyrosinase positive oculocutaneous albinism
  • E70.328 - Other oculocutaneous albinism
  • E70.329 - Oculocutaneous albinism, unspecified
  • E70.33 - Albinism with hematologic abnormality
  • E70.330 - Chediak-Higashi syndrome
  • E70.331 - Hermansky-Pudlak syndrome
  • E70.338 - Other albinism with hematologic abnormality
  • E70.339 - Albinism with hematologic abnormality, unspecified
  • E70.39 - Other specified albinism
  • E70.4 - Disorders of histidine metabolism
  • E70.40 - Disorders of histidine metabolism, unspecified
  • E70.41 - Histidinemia
  • E70.49 - Other disorders of histidine metabolism
  • E70.5 - Disorders of tryptophan metabolism
  • E70.8 - Other disorders of aromatic amino-acid metabolism
  • E70.81 - Aromatic L-amino acid decarboxylase deficiency
  • E70.89 - Other disorders of aromatic amino-acid metabolism
  • E70.9 - Disorder of aromatic amino-acid metabolism, unspecified

Code Classification

  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Metabolic disorders (E70-E88)
      • Disorders of aromatic amino-acid metabolism (E70)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients


Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues, such as your liver, muscles, and body fat.

A metabolic disorder occurs when abnormal chemical reactions in your body disrupt this process. When this happens, you might have too much of some substances or too little of other ones that you need to stay healthy. There are different groups of disorders. Some affect the breakdown of amino acids, carbohydrates, or lipids. Another group, mitochondrial diseases, affects the parts of the cells that produce the energy.

You can develop a metabolic disorder when some organs, such as your liver or pancreas, become diseased or do not function normally. Diabetes is an example.

  • Acidosis (Medical Encyclopedia)
  • Alkalosis (Medical Encyclopedia)
  • Lactic acid test (Medical Encyclopedia)
  • Metabolic acidosis (Medical Encyclopedia)
  • Metabolic neuropathies (Medical Encyclopedia)
  • Pseudohypoparathyroidism (Medical Encyclopedia)

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