2027 ICD-10-CM Diagnosis Code E70Disorders of aromatic amino-acid metabolism

ICD-10-CM Codes›E00–E89›E70-E88›E70

ICD-10-CM E70
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

E70 is a non-billable ICD-10-CM category code for disorders of aromatic amino-acid metabolism, so it cannot be submitted on claims. Use a more specific code from this category instead, such as E70.0, E70.1, E70.20, and E70.21.

Code Identity

ICD-10-CM Code
E70
Billable Status
No — Non-Billable Category
Code Describes
Disorders of aromatic amino-acid metabolism
Short Description
Disorders of aromatic amino-acid metabolism
Same as the full description in the CMS dataset.
Chapter
E70-E88
Metabolic disorders

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE70Disorders of aromatic amino-acid metabolism
This CodeE70Disorders of aromatic amino-acid metabolism

Specific Coding for Disorders of aromatic amino-acid metabolismOverview

Non-specific codes like E70 require more characters. Use one of these billable codes instead:

  • Use E70.0 for Classical phenylketonuria

  • Use E70.1 for Other hyperphenylalaninemias

  • E70.2 for Disorders of tyrosine metabolism

  • Use E70.20 for Disorder of tyrosine metabolism, unspecified

  • Use E70.21 for Tyrosinemia

  • Use E70.29 for Other disorders of tyrosine metabolism

  • E70.3 for Albinism

  • Use E70.30 for Albinism, unspecified

  • E70.31 for Ocular albinism

  • E70.32 for Oculocutaneous albinism

  • E70.33 for Albinism with hematologic abnormality

  • Use E70.39 for Other specified albinism

  • E70.4 for Disorders of histidine metabolism

  • Use E70.40 for Disorders of histidine metabolism, unspecified

  • Use E70.41 for Histidinemia

  • Use E70.49 for Other disorders of histidine metabolism

  • Use E70.5 for Disorders of tryptophan metabolism

  • E70.8 for Other disorders of aromatic amino-acid metabolism

  • Use E70.81 for Aromatic L-amino acid decarboxylase deficiency

  • Use E70.89 for Other disorders of aromatic amino-acid metabolism

  • Use E70.9 for Disorder of aromatic amino-acid metabolism, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to E70: its own notes plus those printed at block E70-E88 and Chapter 4. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Block E70-E88 Metabolic disorders applies to 286 codes
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseases applies to 973 codes
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Block E70-E88 Metabolic disorders applies to 286 codes
  • Ehlers-Danlos syndromes (Q79.6-)

Notes

General instructions on how these codes are used.

From Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseases applies to 973 codes
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name E70, its category, or a range that includes it.

Excludes1 4

These codes carry an Excludes1 note naming E70: they are not reported together with it, unless the two conditions are unrelated.

  • E72 Other disorders of amino-acid metabolism
    aromatic amino-acid metabolism (E70.-)
  • R79 Other abnormal findings of blood chemistry
    specific findings indicating disorder of amino-acid metabolism (E70-E72)
  • R79.83 Abnormal findings of blood amino-acid level
    disorders of amino-acid metabolism (E70-E72)
  • Block R80-R82 Abnormal findings on examination of urine, without diagnosis
    specific findings indicating disorder of amino-acid metabolism (E70-E72)

Patient EducationClinical

Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About E70Overview

What is the ICD-10 code for disorders of aromatic amino-acid metabolism?

E70 is the ICD-10-CM category for disorders of aromatic amino-acid metabolism, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is E70 (Disorders of aromatic amino-acid metabolism) a billable code?

No. This is a category header that groups the codes for disorders of aromatic amino-acid metabolism, and headers cannot be submitted on claims. Claims for disorders of aromatic amino-acid metabolism need a more specific code from this category, such as E70.0, E70.1, and E70.20.

Can E70 be reported with a code from E34.5?

Not as a rule. The Excludes1 note at block E70-E88, which applies to E70, lists "androgen insensitivity syndrome (E34.5-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).