2026 ICD-10-CM Diagnosis Code E70Disorders of aromatic amino-acid metabolism
E70 is a non-billable ICD-10-CM category code for disorders of aromatic amino-acid metabolism, so it cannot be submitted on claims. Use a more specific code from this category instead, such as E70.0, E70.1, E70.20, and E70.21.
Code Identity
Code Classification
Specific Coding for Disorders of aromatic amino-acid metabolismOverview
Non-specific codes like E70 require more characters. Use one of these billable codes instead:
Use E70.0 for Classical phenylketonuria
Use E70.1 for Other hyperphenylalaninemias
E70.2 for Disorders of tyrosine metabolism
Use E70.20 for Disorder of tyrosine metabolism, unspecified
Use E70.21 for Tyrosinemia
Use E70.29 for Other disorders of tyrosine metabolism
E70.3 for Albinism
Use E70.30 for Albinism, unspecified
E70.31 for Ocular albinism
E70.32 for Oculocutaneous albinism
E70.33 for Albinism with hematologic abnormality
Use E70.39 for Other specified albinism
E70.4 for Disorders of histidine metabolism
Use E70.40 for Disorders of histidine metabolism, unspecified
Use E70.41 for Histidinemia
Use E70.49 for Other disorders of histidine metabolism
Use E70.5 for Disorders of tryptophan metabolism
E70.8 for Other disorders of aromatic amino-acid metabolism
Use E70.81 for Aromatic L-amino acid decarboxylase deficiency
Use E70.89 for Other disorders of aromatic amino-acid metabolism
Use E70.9 for Disorder of aromatic amino-acid metabolism, unspecified
Patient EducationClinical
Metabolic Disorders
Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel.
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Code HistoryHistory
Questions About E70Overview
Is E70 (Disorders of aromatic amino-acid metabolism) a billable code?
No. This is a category header that groups the codes for disorders of aromatic amino-acid metabolism, and headers cannot be submitted on claims. Claims for disorders of aromatic amino-acid metabolism need a more specific code from this category, such as E70.0, E70.1, and E70.20.
