2022 ICD-10-CM Code A50

Congenital syphilis

Version 2021

Not Valid for Submission

Short Description:Congenital syphilis
Long Description:Congenital syphilis

Code Classification

  • Certain infectious and parasitic diseases (A00–B99)
    • Infections with a predominantly sexual mode of transmission (A50-A64)
      • Congenital syphilis (A50)

A50 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of congenital syphilis. The code is not specific and is NOT valid for the year 2022 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding for Congenital syphilis

Non-specific codes like A50 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for congenital syphilis:

  • NON-BILLABLE CODE - A50.0 for Early congenital syphilis, symptomatic
  • BILLABLE CODE - Use A50.01 for Early congenital syphilitic oculopathy
  • BILLABLE CODE - Use A50.02 for Early congenital syphilitic osteochondropathy
  • BILLABLE CODE - Use A50.03 for Early congenital syphilitic pharyngitis
  • BILLABLE CODE - Use A50.04 for Early congenital syphilitic pneumonia
  • BILLABLE CODE - Use A50.05 for Early congenital syphilitic rhinitis
  • BILLABLE CODE - Use A50.06 for Early cutaneous congenital syphilis
  • BILLABLE CODE - Use A50.07 for Early mucocutaneous congenital syphilis
  • BILLABLE CODE - Use A50.08 for Early visceral congenital syphilis
  • BILLABLE CODE - Use A50.09 for Other early congenital syphilis, symptomatic
  • BILLABLE CODE - Use A50.1 for Early congenital syphilis, latent
  • BILLABLE CODE - Use A50.2 for Early congenital syphilis, unspecified
  • NON-BILLABLE CODE - A50.3 for Late congenital syphilitic oculopathy
  • BILLABLE CODE - Use A50.30 for Late congenital syphilitic oculopathy, unspecified
  • BILLABLE CODE - Use A50.31 for Late congenital syphilitic interstitial keratitis
  • BILLABLE CODE - Use A50.32 for Late congenital syphilitic chorioretinitis
  • BILLABLE CODE - Use A50.39 for Other late congenital syphilitic oculopathy
  • NON-BILLABLE CODE - A50.4 for Late congenital neurosyphilis [juvenile neurosyphilis]
  • BILLABLE CODE - Use A50.40 for Late congenital neurosyphilis, unspecified
  • BILLABLE CODE - Use A50.41 for Late congenital syphilitic meningitis
  • BILLABLE CODE - Use A50.42 for Late congenital syphilitic encephalitis
  • BILLABLE CODE - Use A50.43 for Late congenital syphilitic polyneuropathy
  • BILLABLE CODE - Use A50.44 for Late congenital syphilitic optic nerve atrophy
  • BILLABLE CODE - Use A50.45 for Juvenile general paresis
  • BILLABLE CODE - Use A50.49 for Other late congenital neurosyphilis
  • NON-BILLABLE CODE - A50.5 for Other late congenital syphilis, symptomatic
  • BILLABLE CODE - Use A50.51 for Clutton's joints
  • BILLABLE CODE - Use A50.52 for Hutchinson's teeth
  • BILLABLE CODE - Use A50.53 for Hutchinson's triad
  • BILLABLE CODE - Use A50.54 for Late congenital cardiovascular syphilis
  • BILLABLE CODE - Use A50.55 for Late congenital syphilitic arthropathy
  • BILLABLE CODE - Use A50.56 for Late congenital syphilitic osteochondropathy
  • BILLABLE CODE - Use A50.57 for Syphilitic saddle nose
  • BILLABLE CODE - Use A50.59 for Other late congenital syphilis, symptomatic
  • BILLABLE CODE - Use A50.6 for Late congenital syphilis, latent
  • BILLABLE CODE - Use A50.7 for Late congenital syphilis, unspecified
  • BILLABLE CODE - Use A50.9 for Congenital syphilis, unspecified

Clinical Information

Information for Patients


Syphilis is a sexually transmitted disease caused by bacteria. It infects the genital area, lips, mouth, or anus of both men and women. You usually get syphilis from sexual contact with someone who has it. It can also pass from mother to baby during pregnancy.

The early stage of syphilis usually causes a single, small, painless sore. Sometimes it causes swelling in nearby lymph nodes. If you do not treat it, syphilis usually causes a non-itchy skin rash, often on your hands and feet. Many people do not notice symptoms for years. Symptoms can go away and come back.

The sores caused by syphilis make it easier to get or give someone HIV during sex. If you are pregnant, syphilis can cause complications, or you could lose your baby. In rare cases, syphilis causes serious health problems and even death.

Syphilis is easy to cure with antibiotics if you catch it early. Correct usage of latex condoms greatly reduces, but does not completely eliminate, the risk of catching or spreading syphilis. If your or your partner is allergic to latex, you can use polyurethane condoms. The most reliable way to avoid infection is to not have anal, vaginal, or oral sex.

Centers for Disease Control and Prevention

[Learn More in MedlinePlus]

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)