2027 ICD-10-CM Diagnosis Code I00Rheumatic fever without heart involvement

ICD-10-CM Codes›I00–I99›I00-I02›I00

ICD-10-CM I00
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

I00 is a billable ICD-10-CM diagnosis code for rheumatic fever without heart involvement. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 545 through 547. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Acute rheumatic heart disease and Bacterial infections.

Code Identity

ICD-10-CM Code
I00
Billable Status
Yes — Valid for Submission
Code Describes
Rheumatic fever without heart involvement
Short Description
Rheumatic fever without heart involvement
Same as the full description in the CMS dataset.
Chapter
I00-I02
Acute rheumatic fever

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI00-I02Acute rheumatic fever
CategoryI00Rheumatic fever without heart involvement
This CodeI00Rheumatic fever without heart involvement

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acute rheumatic fever
  • Annular erythema
  • Erythema marginatum in acute rheumatic fever
  • Migratory polyarthritis
  • Recurrent rheumatic fever
  • Rheumatic arthritis
  • Rheumatic fever
  • Rheumatic fever without heart involvement
  • Rheumatic pneumonitis
  • Subacute arthritis
  • Subacute arthropathy
  • Subacute rheumatic arthritis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to I00: its own notes plus those printed at Chapter 9. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

  • arthritis, rheumatic, acute or subacute

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • rheumatic fever with heart involvement (I01.0 -I01.9)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 9 (I00-I99) Diseases of the circulatory system applies to 1,433 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • transient cerebral ischemic attacks and related syndromes (G45.-)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name I00, its category, or a range that includes it.

Applicable To 5

These notes mention I00.

  • I01.0 Acute rheumatic pericarditis
    Any condition in I00 with pericarditis
  • I01.1 Acute rheumatic endocarditis
    Any condition in I00 with endocarditis or valvulitis
  • I01.2 Acute rheumatic myocarditis
    Any condition in I00 with myocarditis
  • I01.8 Other acute rheumatic heart disease
    Any condition in I00 with other or multiple types of heart involvement
  • I01.9 Acute rheumatic heart disease, unspecified
    Any condition in I00 with unspecified type of heart involvement

Excludes1 2

These codes carry an Excludes1 note naming I00: they are not reported together with it, unless the two conditions are unrelated.

  • M02 Postinfective and reactive arthropathies
    rheumatic fever (I00)
  • M05 Rheumatoid arthritis with rheumatoid factor
    rheumatic fever (I00)

Excludes2 2

These codes carry an Excludes2 note naming I00: its condition is not part of those codes, and both may be reported when the patient has both.

  • I51 Complications and ill-defined descriptions of heart disease
    heart disease specified as rheumatic (I00-I09)
  • Block J09-J18 Influenza and pneumonia
    rheumatic pneumonia (I00)

Code First 1

These codes say to code first a condition named in the note, and I00 is one of the conditions named.

  • J17 Pneumonia in diseases classified elsewhere
    rheumatic fever (I00)

Index to Diseases and InjuriesGuidance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR002
Acute rheumatic heart disease
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR INF003
Bacterial infections
Default principal diagnosis: inpatient No · outpatient No

Patient EducationClinical

Streptococcal Infections

Strep is short for Streptococcus, a type of bacteria that often lives in your nose and throat. Most strep infections are mild, but some may become serious depending on your overall health.

The full article covers:

  • What are streptococcal infections?
  • How do streptococcal infections spread?
  • Who is more likely to get a streptococcal infection?
  • What are the symptoms of streptococcal infections?
  • How are streptococcal infections diagnosed?
  • What are the treatments for streptococcal infections?
  • Can streptococcal infections be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert I00 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
390 Rheum fev w/o hrt involv
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About I00Overview

What is the ICD-10 code for rheumatic fever without heart involvement?

The ICD-10-CM code for rheumatic fever without heart involvement is I00. It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is I00 (Rheumatic fever without heart involvement) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report rheumatic fever without heart involvement on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does I00 group to?

When rheumatic fever without heart involvement is the principal diagnosis on an inpatient stay, it groups to MS-DRG 546, 545, 547, with relative weights from 0.7160 to 2.3903 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of I00?

Under the General Equivalence Mappings, rheumatic fever without heart involvement converts to ICD-9-CM 390 (rheum fev w/o hrt involv). The mapping is a direct match.