2026 ICD-10-CM Diagnosis Code E00Congenital iodine-deficiency syndrome

ICD-10-CM Codes›E00–E89›E00-E07›E00

ICD-10-CM E00
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E00 is a non-billable ICD-10-CM category code for congenital iodine-deficiency syndrome, so it cannot be submitted on claims. Use a more specific code from this category instead, such as E00.0, E00.1, E00.2, and E00.9.

Code Identity

ICD-10-CM Code
E00
Billable Status
No — Non-Billable Category
Code Describes
Congenital iodine-deficiency syndrome
Chapter
E00-E07
Disorders of thyroid gland

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE00-E07Disorders of thyroid gland
CategoryE00Congenital iodine-deficiency syndrome
This CodeE00Congenital iodine-deficiency syndrome

Specific Coding for Congenital iodine-deficiency syndromeOverview

Non-specific codes like E00 require more characters. Use one of these billable codes instead:

  • Use E00.0 for Congenital iodine-deficiency syndrome, neurological type

  • Use E00.1 for Congenital iodine-deficiency syndrome, myxedematous type

  • Use E00.2 for Congenital iodine-deficiency syndrome, mixed type

  • Use E00.9 for Congenital iodine-deficiency syndrome, unspecified

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Use Additional Code

Type 1 Excludes

  • subclinical iodine-deficiency hypothyroidism E02

Patient EducationClinical

Thyroid Diseases

Your thyroid is a small, butterfly-shaped gland in the front of your neck. It makes hormones that control the way the body uses energy. These hormones affect nearly every organ in your body and control many of your body's most important functions. For example, they affect your breathing, heart rate, weight, digestion, and moods.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E00Overview

Is E00 (Congenital iodine-deficiency syndrome) a billable code?

No. This is a category header that groups the codes for congenital iodine-deficiency syndrome, and headers cannot be submitted on claims. Claims for congenital iodine-deficiency syndrome need a more specific code from this category, such as E00.0, E00.1, and E00.2.