2022 ICD-10-CM Code E00

Congenital iodine-deficiency syndrome

Version 2021

Not Valid for Submission

ICD-10:E00
Short Description:Congenital iodine-deficiency syndrome
Long Description:Congenital iodine-deficiency syndrome

Code Classification

  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Disorders of thyroid gland (E00-E07)
      • Congenital iodine-deficiency syndrome (E00)

E00 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of congenital iodine-deficiency syndrome. The code is not specific and is NOT valid for the year 2022 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding for Congenital iodine-deficiency syndrome

Non-specific codes like E00 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for congenital iodine-deficiency syndrome:

  • BILLABLE CODE - Use E00.0 for Congenital iodine-deficiency syndrome, neurological type
  • BILLABLE CODE - Use E00.1 for Congenital iodine-deficiency syndrome, myxedematous type
  • BILLABLE CODE - Use E00.2 for Congenital iodine-deficiency syndrome, mixed type
  • BILLABLE CODE - Use E00.9 for Congenital iodine-deficiency syndrome, unspecified

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code E00:


Use Additional Code

Use Additional Code
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Information for Patients


Thyroid Diseases

Your thyroid is a butterfly-shaped gland in your neck, just above your collarbone. It is one of your endocrine glands, which make hormones. Thyroid hormones control the rate of many activities in your body. These include how fast you burn calories and how fast your heart beats. All of these activities are your body's metabolism.

Thyroid problems include

To diagnose thyroid diseases, doctors use a medical history, physical exam, and thyroid tests. They sometimes also use a biopsy. Treatment depends on the problem, but may include medicines, radioiodine therapy, or thyroid surgery.

Dept. of Health and Human Services Office on Women's Health


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Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)