2027 ICD-10-CM Diagnosis Code E84.11Meconium ileus in cystic fibrosis

ICD-10-CM Codes›E00–E89›E70-E88›E84

ICD-10-CM E84.11
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

E84.11 is a billable ICD-10-CM diagnosis code for meconium ileus in cystic fibrosis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 791, 793. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 5 closely related codes. The code is restricted by the Medicare Code Editor to newborn patients (age 0). Coders also document this condition as cystic fibrosis with meconium ileus. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cystic fibrosis.

For Medicare Advantage risk adjustment, E84.11 maps to CMS-HCC Category 277 (Cystic Fibrosis) under the V28 model, adding a risk factor of about 0.998 for a community, non-dual, aged beneficiary in payment year 2027.

Code Identity

ICD-10-CM Code
E84.11
Billable Status
Yes — Valid for Submission
Code Describes
Meconium ileus in cystic fibrosis
Short Description
Meconium ileus in cystic fibrosis
Same as the full description in the CMS dataset.
Parent Code
E84.1
Cystic fibrosis with intestinal manifestations

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE84Cystic fibrosis
This CodeE84.11Meconium ileus in cystic fibrosis

Code EditsBilling

Medicare Code Editor checks that affect claim validity for E84.11.

Perinatal / Newborn diagnoses
The Medicare Code Editor detects inconsistencies in perinatal / newborn cases by checking a patient's age and any diagnosis on the patient's record. The newborn code edits apply to patients age 0 years only; a subset of diagnoses which will only occur during the perinatal or newborn period of age 0 (e.g., tetanus neonatorum, health examination for newborn under 8 days old).

Medicare Risk Adjustment (HCC)Billing

E84.11 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.

CMS-HCC V28 Category (Payment Model)
HCC 277— Cystic Fibrosis
Payment HCC · PY 2027 one of 5 ICD-10-CM codes in this category
Risk Adjustment Factor (RAF) Weight
+0.998
community, non-dual, aged · ranges 0.650–3.829 across segments
Hierarchy
Superseded by HCC 276
a more severe related category takes the payment when both are reported
Prior Model (CMS-HCC V24)
HCC 110
V24 retired V28 pays 100% of MA risk scores since PY 2026
Other CMS Models
PACE (CMS-HCC V22): HCC 110 · ESRD (V21): HCC 110 · ESRD (V24): HCC 110
ESRD V21 weights: 0.072 dialysis, 0.435–0.494 functioning graft · ESRD V24 weights: 0.125 dialysis, 0.329–3.090 functioning graft
Part D (RxHCC)
RxHCC 225 — Cystic Fibrosis
also risk-adjusts in the Part D prescription drug model (V08)

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cystic fibrosis with meconium ileus
  • Meconium ileus
  • Neonatal obstruction of intestine
  • Perforation of intestine due to cystic fibrosis with meconium ileus
  • Perinatal intestinal obstruction
  • Perinatal intestinal perforation

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to E84.11: its own notes plus those printed at E84, block E70-E88, and Chapter 4. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

From E84 Cystic fibrosis applies to 5 codes
  • mucoviscidosis

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

On E84.11 itself
  • meconium ileus not due to cystic fibrosis (P76.0)
From Block E70-E88 Metabolic disorders applies to 286 codes
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseases applies to 973 codes
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Block E70-E88 Metabolic disorders applies to 286 codes
  • Ehlers-Danlos syndromes (Q79.6-)

Code Also

A second code may be needed to fully describe the condition; the note gives no sequencing direction.

From E84 Cystic fibrosis applies to 5 codes
  • exocrine pancreatic insufficiency (K86.81)

Notes

General instructions on how these codes are used.

From Chapter 4 (E00-E89) Endocrine, nutritional and metabolic diseases applies to 973 codes
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name E84.11, its category, or a range that includes it.

Excludes1 6

These codes carry an Excludes1 note naming E84.11: they are not reported together with it, unless the two conditions are unrelated.

  • K56 Paralytic ileus and intestinal obstruction without hernia
    cystic fibrosis with meconium ileus (E84.11)
  • P76.0 Meconium plug syndrome
    meconium ileus in cystic fibrosis (E84.11)
  • Q41 Congenital absence, atresia and stenosis of small intestine
    cystic fibrosis with intestinal manifestation (E84.11)
  • Q45.3 Other congenital malformations of pancreas and pancreatic duct
    fibrocystic disease of pancreas (E84.-) names E84.-, which includes this code
  • P78 Other perinatal digestive system disorders
    cystic fibrosis (E84.0-E84.9) names E84.0-E84.9, which includes this code
  • Q45.3 Other congenital malformations of pancreas and pancreatic duct
    cystic fibrosis (E84.0-E84.9) names E84.0-E84.9, which includes this code

Excludes2 2

These codes carry an Excludes2 note naming E84.11: its condition is not part of those codes, and both may be reported when the patient has both.

  • Block J40-J4B Chronic lower respiratory diseases
    cystic fibrosis (E84.-) names E84.-, which includes this code
  • K86 Other diseases of pancreas
    fibrocystic disease of pancreas (E84.-) names E84.-, which includes this code

Code First 3

These codes say to code first a condition named in the note, and E84.11 is one of the conditions named.

  • E08 Diabetes mellitus due to underlying condition
    cystic fibrosis (E84.-) names E84.-, which includes this code
  • J93.12 Secondary spontaneous pneumothorax
    cystic fibrosis (E84.-) names E84.-, which includes this code
  • Q55.3 Atresia of vas deferens
    any associated cystic fibrosis (E84.-) names E84.-, which includes this code

Code Also 1

These codes say E84.11 may also be needed to fully describe the condition. The note gives no sequencing direction.

  • Z71.87 Encounter for pediatric-to-adult transition counseling
    cystic fibrosis (E84.-) names E84.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END012
Cystic fibrosis
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cystic Fibrosis

    an autosomal recessive genetic disease of the exocrine glands. it is caused by mutations in the gene encoding the cystic fibrosis transmembrane conductance regulator expressed in several organs including the lung, the pancreas, the biliary system, and the sweat glands. cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in airway obstruction; chronic respiratory infections; pancreatic insufficiency; maldigestion; salt depletion; and heat prostration.

Patient EducationClinical

Cystic Fibrosis

Cystic fibrosis (CF) is an inherited disease of the mucus and sweat glands. It affects mostly your lungs, pancreas, liver, intestines, sinuses, and sex organs. CF causes your mucus to be thick and sticky. The mucus clogs the lungs, causing breathing problems and making it easy for bacteria to grow.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert E84.11 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
277.01 Cystic fibrosis w ileus
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About E84.11Overview

What is the ICD-10 code for meconium ileus in cystic fibrosis?

The ICD-10-CM code for meconium ileus in cystic fibrosis is E84.11 (sometimes written as E8411). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is E84.11 (Cystic fibrosis with intestinal manifestations) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report meconium ileus in cystic fibrosis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does E84.11 group to?

When meconium ileus in cystic fibrosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 793, 791, with relative weights from 4.1073 to 4.2192 depending on complications. Higher weights mean higher Medicare reimbursement.

Is E84.11 a CC or MCC?

CMS lists E84.11 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 5 closely related codes in its exclusion list.

Who can E84.11 be reported for?

The Medicare Code Editor checks meconium ileus in cystic fibrosis against patient demographics: this code is intended for newborn patients (age 0). Claims outside these limits are flagged as inconsistent.

What HCC is E84.11?

E84.11 (meconium ileus in cystic fibrosis) maps to CMS-HCC Category 277 (Cystic Fibrosis), commonly written as HCC 277, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 110 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. In the Part D prescription drug model it maps to RxHCC 225.

Does E84.11 risk-adjust for Medicare Advantage payment?

Yes. When documented and reported on a Medicare Advantage encounter, E84.11 adds a risk adjustment factor of about 0.998 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.650 to 3.829 depending on the payment segment). A more severe related category (HCC 276) supersedes it when both are reported. See the full factor table on the HCC 277 category page.