Cystic fibrosis (E84) ICD-10-CM
The E84 code range covers cystic fibrosis with 7 ICD-10-CM diagnosis codes. 5 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- mucoviscidosis
Code Also
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
- exocrine pancreatic insufficiency K86.81
Codes in the E84 Range 7 codes · 5 billable
- E84 Cystic fibrosisNon-billable
- E84.0 Cystic fibrosis with pulmonary manifestations
- E84.1 Cystic fibrosis with intestinal manifestationsNon-billable
- E84.11 Meconium ileus in cystic fibrosis
- E84.19 Cystic fibrosis with other intestinal manifestations
- E84.8 Cystic fibrosis with other manifestations
- E84.9 Cystic fibrosis, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the E84 range.
Cystic Fibrosis
An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION.
About the E84 Code Range
Cystic fibrosis is an inherited metabolic disorder that disrupts gland secretions in organs including the lungs and pancreas.
The subdivisions distinguish where the condition has manifestations. E84.0 identifies lung manifestations. E84.1 identifies intestinal manifestations, divided into meconium ileus under E84.11 and other intestinal manifestations under E84.19. E84.8 identifies other manifestations, while E84.9 leaves them unspecified.
Questions About This Page
How many billable codes are in the E84 range?
Of the 7 codes in this range, 5 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the E84 range classify?
The range classifies cystic fibrosis. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
