2027 ICD-10-CM Diagnosis Code Q41Congenital absence, atresia and stenosis of small intestine

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q41

ICD-10-CM Q41
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q41 is a non-billable ICD-10-CM category code for congenital absence, atresia and stenosis of small intestine, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q41.0, Q41.1, Q41.2, and Q41.8.

Code Identity

ICD-10-CM Code
Q41
Billable Status
No — Non-Billable Category
Code Describes
Congenital absence, atresia and stenosis of small intestine
Short Description
Congenital absence, atresia and stenosis of small intestine
Same as the full description in the CMS dataset.
Chapter
Q38-Q45
Other congenital malformations of the digestive system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ41Congenital absence, atresia and stenosis of small intestine
This CodeQ41Congenital absence, atresia and stenosis of small intestine

Specific Coding for Congenital absence, atresia and stenosis of small intestineOverview

Non-specific codes like Q41 require more characters. Use one of these billable codes instead:

  • Use Q41.0 for Congenital absence, atresia and stenosis of duodenum

  • Use Q41.1 for Congenital absence, atresia and stenosis of jejunum

  • Use Q41.2 for Congenital absence, atresia and stenosis of ileum

  • Use Q41.8 for Congenital absence, atresia and stenosis of other specified parts of small intestine

  • Use Q41.9 for Congenital absence, atresia and stenosis of small intestine, part unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q41: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Includes

Further defines, or gives examples of, the content of the category.

  • congenital obstruction, occlusion or stricture of small intestine or intestine NOS

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • cystic fibrosis with intestinal manifestation (E84.11)
  • meconium ileus NOS (without cystic fibrosis) (P76.0)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q41, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q41: they are not reported together with it, unless the two conditions are unrelated.

  • K56 Paralytic ileus and intestinal obstruction without hernia
    congenital stricture or stenosis of intestine (Q41-Q42)

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q41Overview

What is the ICD-10 code for congenital absence, atresia and stenosis of small intestine?

Q41 is the ICD-10-CM category for congenital absence, atresia and stenosis of small intestine, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is Q41 (Congenital absence, atresia and stenosis of small intestine) a billable code?

No. This is a category header that groups the codes for congenital absence, atresia and stenosis of small intestine, and headers cannot be submitted on claims. Claims for congenital absence, atresia and stenosis of small intestine need a more specific code from this category, such as Q41.0, Q41.1, and Q41.2.

Can Q41 be reported with E84.11?

Not as a rule. The Excludes1 note on Q41 lists "cystic fibrosis with intestinal manifestation (E84.11)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).