Disorders of glycosaminoglycan metabolism (E76)

• ICD-10 Index

  • Endocrine, nutritional and metabolic diseases (E00–E90)

    • Metabolic disorders (E70-E88)

      • Disorders of glycosaminoglycan metabolism (E76)

        • E76 - Disorders of glycosaminoglycan metabolism NON-BILLABLE CODE
        • E76.0 - Mucopolysaccharidosis, type I NON-BILLABLE CODE
        • E76.01 - Hurler's syndrome BILLABLE CODE
        • E76.02 - Hurler-Scheie syndrome BILLABLE CODE
        • E76.03 - Scheie's syndrome BILLABLE CODE
        • E76.1 - Mucopolysaccharidosis, type II BILLABLE CODE
        • E76.2 - Other mucopolysaccharidoses NON-BILLABLE CODE
        • E76.21 - Morquio mucopolysaccharidoses NON-BILLABLE CODE
        • E76.210 - Morquio A mucopolysaccharidoses BILLABLE CODE
        • E76.211 - Morquio B mucopolysaccharidoses BILLABLE CODE
        • E76.219 - Morquio mucopolysaccharidoses, unspecified BILLABLE CODE
        • E76.22 - Sanfilippo mucopolysaccharidoses BILLABLE CODE
        • E76.29 - Other mucopolysaccharidoses BILLABLE CODE
        • E76.3 - Mucopolysaccharidosis, unspecified BILLABLE CODE
        • E76.8 - Other disorders of glucosaminoglycan metabolism BILLABLE CODE
        • E76.9 - Glucosaminoglycan metabolism disorder, unspecified BILLABLE CODE

Clinical Information for Disorders of glycosaminoglycan metabolism (E76)

Mucopolysaccharidoses - Group of lysosomal storage diseases each caused by an inherited deficiency of an enzyme involved in the degradation of glycosaminoglycans (mucopolysaccharides). The diseases are progressive and often display a wide spectrum of clinical severity within one enzyme deficiency.

Mucopolysaccharidoses - Group of lysosomal storage diseases each caused by an inherited deficiency of an enzyme involved in the degradation of glycosaminoglycans (mucopolysaccharides). The diseases are progressive and often display a wide spectrum of clinical severity within one enzyme deficiency.