E85.4 - Organ-limited amyloidosis

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Acquired abnormality of atrium
• Age-related amyloidosis
• Age-related amyloidosis
• Age-related amyloidosis
• Amyloid disease of the urethra
• Amyloid nephropathy
• Amyloid of bladder
• Amyloid of cornea
• Amyloid of prostate
• Amyloid of testes
• Amyloid of ureter
• Amyloid of vitreous
• Amyloidosis cutis dyschromia
• Amyloidosis limited to skin
• Amyloidosis of skin
• Amyloidosis of small intestine
• Amyloidosis of spleen
• Arthritis secondary to amyloidosis
• Autonomic neuropathy due to amyloidosis
• Beta-2 microglobulin arthropathy
• Bullous cutaneous amyloidosis
• Cardiac familial non-neuropathic amyloidosis
• Cerebral amyloid angiopathy
• Conjunctival amyloidosis
• Danish type familial amyloid cardiomyopathy
• Dominant primary localized cutaneous amyloidosis
• Enlargement of tongue
• Familial amyloid polyneuropathy
• Familial amyloid polyneuropathy with cutaneous amyloidosis
• Familial cardiomyopathy
• Familial non-neuropathic amyloidosis
• Gingival amyloidosis
• Glomerular disorder due to amyloidosis
• Glomerular disorder due to organ-limited amyloidosis
• Hepatic amyloidosis
• Hereditary cerebral amyloid angiopathy, Dutch type
• Hereditary cerebral hemorrhage with amyloidosis
• Hereditary cerebrovascular amyloidosis
• Hereditary oculoleptomeningeal amyloid angiopathy
• Heredofamilial systemic amyloidosis affecting skin
• Infiltrative cardiomyopathy
• Isolated atrial amyloid
• Isolated corneal amyloidosis
• Laryngeal amyloidosis
• Lichen amyloidosis
• Localized amyloidosis
• Localized hereditary amyloidosis
• Localized hereditary amyloidosis
• Localized non-hereditary amyloidosis
• Macroglossia due to amyloidosis
• Macular cutaneous amyloidosis
• Macule of skin
• Myocardial degeneration
• Neuropathy associated with dysproteinemias
• Ocular amyloid deposit
• Poikilodermal cutaneous amyloid
• Primary localized cutaneous amyloidosis
• Primary localized cutaneous nodular amyloidosis
• Pulmonary amyloidosis
• Secondary localized cutaneous amyloidosis
• Senile brain amyloidosis
• Senile cardiac amyloidosis
• Sporadic cerebral amyloid angiopathy
• Systemic amyloidosis affecting skin

Clinical Information

• Amyloid Neuropathies, Familial-. inherited disorders of the peripheral nervous system associated with the deposition of amyloid in nerve tissue. the different clinical types based on symptoms correspond to the presence of a variety of mutations in several different proteins including transthyretin (prealbumin); apolipoprotein a-i; and gelsolin.
• Cerebral Amyloid Angiopathy-. a heterogeneous group of sporadic or familial disorders characterized by amyloid deposits in the walls of small and medium sized blood vessels of cerebral cortex and meninges. clinical features include multiple, small lobar cerebral hemorrhage; cerebral ischemia (brain ischemia); and cerebral infarction. cerebral amyloid angiopathy is unrelated to generalized amyloidosis. amyloidogenic peptides in this condition are nearly always the same ones found in alzheimer disease. (from kumar: robbins and cotran: pathologic basis of disease, 7th ed., 2005)
• Cerebral Amyloid Angiopathy, Familial-. a familial disorder marked by amyloid deposits in the walls of small and medium sized blood vessels of cerebral cortex and meninges.
• Cerebral Amyloid Angiopathy-. a disorder characterized by the deposition of amyloid in the wall of the vessels in the brain.
• Cerebral Amyloid Angiopathy, APP-Related|HCHWAD|Hereditary Cerebral Hemorrhage with Amyloidosis-Dutch Type-. an autosomal dominant form of cerebral amyloid angiopathy caused by mutation(s) in the app gene, encoding amyloid-beta a4 protein. the deposition of amyloid in cerebral blood vessels wall may lead to degenerative vascular changes that may result in cerebral hemorrhage. mutation(s) in the app gene may also cause autosomal dominant alzheimer disease 1.
• Myocardial Degeneration-. degeneration of myocardial tissue.

Diagnostic Related Groups - MS-DRG Mapping

The is diagnosis code is grouped in the following groups for version MS-DRG V40.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC). applicable from 10/01/2022 through 09/30/2023.

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Patient Education

Amyloidosis

Amyloidosis occurs when abnormal proteins called amyloids build up and form deposits. The deposits can collect in organs such as the kidney and heart. This can cause the organs to become stiff and unable to work the way they should.

There are three main types of amyloidosis:

• Primary - with no known cause
• Secondary - caused by another disease, including some types of cancer
• Familial - passed down through genes

Symptoms can vary, depending upon which organs are affected. Treatment depends on the type of amyloidosis you have. The goal is to help with symptoms and limit the production of proteins. If another disease is the cause, it needs to be treated.

Amyloidosis & Kidney Disease

Code History

• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)