2026 ICD-10-CM Diagnosis Code E83.822

ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

ICD-10-CM Code:
E83.822
ICD-10 Code for:
ENPP1 def cause autosom recess hypophosphate rickets type 2
Is Billable?
Yes - Valid for Submission
Code Navigator:

E83.822 is a billable diagnosis code used to specify a medical diagnosis of enpp1 deficiency causing autosomal recessive hypophosphatemic rickets type 2. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2025 through September 30, 2026.

Code Classification

  • Endocrine, nutritional and metabolic diseases
    E00–E89
    • Metabolic disorders
      E70-E88
      • Disorders of mineral metabolism
        E83

New 2026 ICD-10-CM Code

E83.822 is new to ICD-10-CM code set for the FY 2026, effective October 1, 2025. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2025. This is a new and revised code for the FY 2026 (October 1, 2025 - September 30, 2026).

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Index of External Cause of Injuries

References found for this diagnosis code in the External Cause of Injuries Index:

    • Deficiency, deficient
      • ENPP1
        • causing
          • autosomal recessive hypophosphatemic rickets type 2

Replacement Code

E83822 replaces the following previously assigned ICD-10-CM code(s):

  • E83.89 - Other disorders of mineral metabolism

Code History

  • FY 2026 - Code Added, effective from 10/1/2025 through 9/30/2026