2027 ICD-10-CM Diagnosis Code D68.023Von Willebrand disease, type 2N

ICD-10-CM Codes›D50–D89›D65-D69›D68

ICD-10-CM D68.023
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

D68.023 is a billable ICD-10-CM diagnosis code for von Willebrand disease, type 2N. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 813. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 50 closely related codes. Coders also document this condition as hereditary von Willebrand disease. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Coagulation and hemorrhagic disorders.

For Medicare Advantage risk adjustment, D68.023 maps to CMS-HCC Category 112 (Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions) under the V28 model, adding a risk factor of about 0.450 for a community, non-dual, aged beneficiary in payment year 2027.

Code Identity

ICD-10-CM Code
D68.023
Billable Status
Yes — Valid for Submission
Code Describes
Von Willebrand disease, type 2N
Short Description
Von Willebrand disease, type 2N
Same as the full description in the CMS dataset.
Parent Code
D68.02
Von Willebrand disease, type 2

Code Classification

ChapterD50–D89Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
SectionD65-D69Coagulation defects, purpura and other hemorrhagic conditions
CategoryD68Other coagulation defects
This CodeD68.023Von Willebrand disease, type 2N

Medicare Risk Adjustment (HCC)Billing

D68.023 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.

CMS-HCC V28 Category (Payment Model)
HCC 112— Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions
Payment HCC · PY 2027 one of 21 ICD-10-CM codes in this category
Risk Adjustment Factor (RAF) Weight
+0.450
community, non-dual, aged · ranges 0.450–0.708 across segments
Hierarchy
Superseded by HCC 111
a more severe related category takes the payment when both are reported
Prior Model (CMS-HCC V24)
HCC 48
V24 retired V28 pays 100% of MA risk scores since PY 2026
Other CMS Models
PACE (CMS-HCC V22): HCC 48 · ESRD (V21): HCC 48 · ESRD (V24): HCC 48
ESRD V21 weights: 0.059 dialysis, 0.173–0.234 functioning graft · ESRD V24 weights: 0.063 dialysis, 0.192–0.358 functioning graft
Part D (RxHCC)
Not mapped
D68.023 does not risk-adjust in the RxHCC prescription drug model

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Hereditary von Willebrand disease
  • Hereditary von Willebrand disease type 2
  • Hereditary von Willebrand disease type 2N

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to D68.023: its own notes plus those printed at D68.0, D68, and Chapter 3. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding
  • Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From D68.0 Von Willebrand disease applies to 10 codes
  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
From D68 Other coagulation defects applies to 25 codes
  • abnormal coagulation profile NOS (R79.1)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From D68 Other coagulation defects applies to 25 codes
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
From Chapter 3 (D50-D89) Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism applies to 324 codes
  • autoimmune disease (systemic) NOS (M35.9)
  • certain conditions originating in the perinatal period (P00-P96)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • human immunodeficiency virus [HIV] disease (B20)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name D68.023, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming D68.023: they are not reported together with it, unless the two conditions are unrelated.

  • D66 Hereditary factor VIII deficiency
    factor VIII deficiency with vascular defect (D68.0-) names D68.0-, which includes this code
  • R04.81 Acute idiopathic pulmonary hemorrhage in infants
    von Willebrand disease (D68.0-) names D68.0-, which includes this code
  • R79.1 Abnormal coagulation profile
    coagulation defects (D68.-) names D68.-, which includes this code

Excludes2 2

These codes carry an Excludes2 note naming D68.023: its condition is not part of those codes, and both may be reported when the patient has both.

  • D69.1 Qualitative platelet defects
    von Willebrand disease (D68.0-) names D68.0-, which includes this code
  • Block R70-R79 Abnormal findings on examination of blood, without diagnosis
    coagulation hemorrhagic disorders (D65-D68) names D65-D68, which includes this code

Code First 1

These codes say to code first a condition named in the note, and D68.023 is one of the conditions named.

  • M36.2 Hemophilic arthropathy
    with vascular defect (D68.0-) names D68.0-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR BLD006
Coagulation and hemorrhagic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • von Willebrand Diseases

    group of hemorrhagic disorders in which the von willebrand factor is either quantitatively or qualitatively abnormal. they are usually inherited as an autosomal dominant trait though rare kindreds are autosomal recessive. symptoms vary depending on severity and disease type but may include prolonged bleeding time, deficiency of factor viii, and impaired platelet adhesion.

Patient EducationClinical

Platelet Disorders

Platelets, also known as thrombocytes, are blood cells. They form in your bone marrow, a sponge-like tissue in your bones. Platelets play a major role in blood clotting. Normally, when one of your blood vessels is injured, you start to bleed.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement D68.023 replaces the following previously assigned code(s):

  • D68.0 - Von Willebrand disease
  • D68.0 - Von Willebrand's disease
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About D68.023Overview

What is the ICD-10 code for von Willebrand disease, type 2N?

The ICD-10-CM code for von Willebrand disease, type 2N is D68.023 (sometimes written as D68023). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is D68.023 (Von Willebrand disease, type 2) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report von Willebrand disease, type 2N on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does D68.023 group to?

When von Willebrand disease, type 2N is the principal diagnosis on an inpatient stay, it groups to MS-DRG 813 (coagulation Disorders), which carries a relative weight of 1.5279. Higher weights mean higher Medicare reimbursement.

Is D68.023 a CC or MCC?

CMS lists D68.023 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 50 closely related codes in its exclusion list.

Can D68.023 be reported with D69.8?

Not as a rule. The Excludes1 note at D68.0, which applies to D68.023, lists "capillary fragility (hereditary) (D69.8)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What HCC is D68.023?

D68.023 (von Willebrand disease, type 2N) maps to CMS-HCC Category 112 (Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions), commonly written as HCC 112, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 48 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.

Does D68.023 risk-adjust for Medicare Advantage payment?

Yes. When documented and reported on a Medicare Advantage encounter, D68.023 adds a risk adjustment factor of about 0.450 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.450 to 0.708 depending on the payment segment). A more severe related category (HCC 111) supersedes it when both are reported. See the full factor table on the HCC 112 category page.