2026 ICD-10-CM Diagnosis Code D67Hereditary factor IX deficiency

ICD-10-CM Codes›D50–D89›D65-D69›D67

ICD-10-CM D67
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D67 is a billable ICD-10-CM diagnosis code for hereditary factor IX deficiency. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Coagulation and hemorrhagic disorders.

Code Identity

ICD-10-CM Code
D67
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary factor IX deficiency
Chapter
D65-D69
Coagulation defects, purpura and other hemorrhagic conditions

Code Classification

ChapterD50–D89Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
SectionD65-D69Coagulation defects, purpura and other hemorrhagic conditions
CategoryD67Hereditary factor IX deficiency
This CodeD67Hereditary factor IX deficiency

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Congenital factor IX deficiency variant
  • Congenital factor IX deficiency with inhibitor
  • Congenital factor IX deficiency without inhibitor
  • Factor IX deficiency
  • Hemophilia B Leyden
  • Hereditary factor IX deficiency disease
  • Hereditary factor IX deficiency disease with inhibitor
  • Hereditary factor IX deficiency disease without inhibitor
  • Mild hereditary factor IX deficiency disease
  • Mild hereditary factor IX deficiency disease with high response inhibitor
  • Mild hereditary factor IX deficiency disease with inhibitor
  • Mild hereditary factor IX deficiency disease with low response inhibitor
  • Mild hereditary factor IX deficiency disease without inhibitor
  • Moderate hereditary factor IX deficiency disease
  • Moderate hereditary factor IX deficiency disease with high response inhibitor
  • Moderate hereditary factor IX deficiency disease with inhibitor
  • Moderate hereditary factor IX deficiency disease with low response inhibitor
  • Moderate hereditary factor IX deficiency disease without inhibitor
  • Severe hereditary factor IX deficiency disease
  • Severe hereditary factor IX deficiency disease with high response inhibitor
  • Severe hereditary factor IX deficiency disease with inhibitor
  • Severe hereditary factor IX deficiency disease with low response inhibitor
  • Severe hereditary factor IX deficiency disease without inhibitor

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Christmas disease
  • Factor IX deficiency (with functional defect)
  • Hemophilia B
  • Plasma thromboplastin component PTC deficiency

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Christmas disease
    • Deficiency, deficient
      • anti-hemophilic
        • factor (A)
          • B
    • Deficiency, deficient
      • autoprothrombin
        • II
    • Deficiency, deficient
      • Christmas factor
    • Deficiency, deficient
      • factor
        • IX (congenital) (functional) (hereditary) (with functional defect)
    • Deficiency, deficient
      • plasma thromboplastin
        • component (PTC)
    • Deficiency, deficient
      • PTC (plasma thromboplastin component)
    • Disease, diseased
      • Christmas
    • Hemophilia(classical) (familial) (hereditary)
      • B

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR BLD006
Coagulation and hemorrhagic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Hemophilia

Hemophilia is a rare bleeding disorder in which the blood does not clot properly. This can lead to problems with bleeding too much after an injury or surgery. You can also have sudden bleeding inside your body, such as in your joints, muscles, and organs.

The full article covers:

  • What is hemophilia?
  • What are the types of hemophilia?
  • What causes hemophilia?
  • Who is at risk for hemophilia?
  • What are the symptoms of hemophilia?
  • How is hemophilia diagnosed?
  • What are the treatments for hemophilia?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D67 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
286.1 Cong factor IX disorder
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D67Overview

Is D67 (Hereditary factor IX deficiency) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary factor IX deficiency on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of D67?

Under the General Equivalence Mappings, hereditary factor IX deficiency converts to ICD-9-CM 286.1 (cong factor IX disorder). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.