Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
ICD-10 codes D65-D69 cover disorders related to blood clotting problems and bleeding conditions, including coagulation defects, purpura, and other hemorrhagic states. These codes are used to classify a wide range of bleeding disorders from rare genetic deficiencies to acquired clotting abnormalities.
This range begins with D65, which codes for disseminated intravascular coagulation (also known as systemic fibrinogenolysis or purpura fulminans), a serious condition where clotting and bleeding happen simultaneously. Codes D66 and D67 specify hereditary deficiencies of clotting factors VIII and IX, commonly called hemophilia A and B. D68 captures other coagulation defects, including von Willebrand disease (types 1, 2, and 3), acquired coagulation factor deficiencies, and thrombophilia such as activated protein C resistance (Factor V Leiden mutation) and prothrombin gene mutations. The D69 series identifies purpura and platelet-related bleeding conditions, including immune thrombocytopenic purpura (ITP), allergic purpura (immunoglobulin A vasculitis), and other primary or secondary thrombocytopenias. These codes help healthcare providers and coders document specific bleeding disorders like Evans syndrome, posttransfusion purpura, and hereditary platelet function defects, ensuring precise diagnosis and management.
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
- D65 Disseminated intravascular coagulation [defibrination syndrome]
Disseminated intravascular coagulation [defibrination syndrome] (D65)
- D66 Hereditary factor VIII deficiency
Hereditary factor VIII deficiency (D66)
- D67 Hereditary factor IX deficiency
Hereditary factor IX deficiency (D67)
D68 Other coagulation defects
D68.0 Von Willebrand disease
- D68.00 Von Willebrand disease, unspecified
- D68.01 Von Willebrand disease, type 1
D68.02 Von Willebrand disease, type 2
- D68.020 Von Willebrand disease, type 2A
- D68.021 Von Willebrand disease, type 2B
- D68.022 Von Willebrand disease, type 2M
- D68.023 Von Willebrand disease, type 2N
- D68.029 Von Willebrand disease, type 2, unspecified
- D68.03 Von Willebrand disease, type 3
- D68.04 Acquired von Willebrand disease
- D68.09 Other von Willebrand disease
- D68.1 Hereditary factor XI deficiency
- D68.2 Hereditary deficiency of other clotting factors
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
- D68.311 Acquired hemophilia
- D68.312 Antiphospholipid antibody with hemorrhagic disorder
- D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
- D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants
- D68.4 Acquired coagulation factor deficiency
D68.5 Primary thrombophilia
- D68.51 Activated protein C resistance
- D68.52 Prothrombin gene mutation
- D68.59 Other primary thrombophilia
D68.6 Other thrombophilia
- D68.61 Antiphospholipid syndrome
- D68.62 Lupus anticoagulant syndrome
- D68.69 Other thrombophilia
- D68.8 Other specified coagulation defects
- D68.9 Coagulation defect, unspecified
Other coagulation defects (D68)
D69 Purpura and other hemorrhagic conditions
- D69.0 Allergic purpura
- D69.1 Qualitative platelet defects
- D69.2 Other nonthrombocytopenic purpura
- D69.3 Immune thrombocytopenic purpura
D69.4 Other primary thrombocytopenia
- D69.41 Evans syndrome
- D69.42 Congenital and hereditary thrombocytopenia purpura
- D69.49 Other primary thrombocytopenia
D69.5 Secondary thrombocytopenia
- D69.51 Posttransfusion purpura
- D69.59 Other secondary thrombocytopenia
- D69.6 Thrombocytopenia, unspecified
- D69.8 Other specified hemorrhagic conditions
- D69.9 Hemorrhagic condition, unspecified
Purpura and other hemorrhagic conditions (D69)