Hereditary factor VIII deficiency (D66)
ICD-10 code D66 is used to identify hereditary factor VIII deficiency, a genetic bleeding disorder commonly known as Hemophilia A. This condition affects blood clotting due to low or absent factor VIII, leading to prolonged bleeding.
This specific ICD-10 code covers various presentations of the disorder, including mild, moderate, or severe hereditary factor VIII deficiency, with or without the presence of inhibitors that affect treatment response. Synonyms such as Factor VIII deficiency, Hemophilia, and Hereditary factor VIII deficiency disease help medical coders recognize when to apply code D66. It also includes cases complicated by joint issues (hemophilic arthropathy) and combined deficiencies of related clotting factors. Understanding these synonyms and variations supports accurate coding for coagulation and hemorrhagic disorders and facilitates proper diagnosis and management documentation.
Instructional Notations
Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Classical hemophilia
- Deficiency factor VIII (with functional defect)
- Hemophilia NOS
- Hemophilia A
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- factor VIII deficiency with vascular defect D68.0
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Factor V Deficiency
A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed)
