Hereditary factor VIII deficiency (D66) ICD-10-CM
The D66 code range covers hereditary factor viii deficiency with 1 ICD-10-CM diagnosis codes. 1 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Classical hemophilia
- Deficiency factor VIII (with functional defect)
- Hemophilia NOS
- Hemophilia A
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- factor VIII deficiency with vascular defect D68.0
Codes in the D66 Range 1 codes · 1 billable
- D66 Hereditary factor VIII deficiency
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the D66 range.
Factor V Deficiency
A deficiency of blood coagulation factor V (known as proaccelerin or accelerator globulin or labile factor) leading to a rare hemorrhagic tendency known as Owren's disease or parahemophilia. It varies greatly in severity. Factor V deficiency is an autosomal recessive trait. (Dorland, 27th ed)
About the D66 Code Range
ICD-10 code D66 is used to identify hereditary factor VIII deficiency, a genetic bleeding disorder commonly known as Hemophilia A. This condition affects blood clotting due to low or absent factor VIII, leading to prolonged bleeding.
This specific ICD-10 code covers various presentations of the disorder, including mild, moderate, or severe hereditary factor VIII deficiency, with or without the presence of inhibitors that affect treatment response. Synonyms such as Factor VIII deficiency, Hemophilia, and Hereditary factor VIII deficiency disease help medical coders recognize when to apply code D66. It also includes cases complicated by joint issues (hemophilic arthropathy) and combined deficiencies of related clotting factors. Understanding these synonyms and variations supports accurate coding for coagulation and hemorrhagic disorders and facilitates proper diagnosis and management documentation.
Questions About This Page
How many billable codes are in the D66 range?
Of the 1 codes in this range, 1 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the D66 range classify?
The range classifies hereditary factor viii deficiency. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
