Hereditary factor IX deficiency (D67)

The ICD-10 code D67 is designated for diagnosing hereditary factor IX deficiency, a genetic bleeding disorder affecting blood clotting.

This code covers various severities of the condition, including mild, moderate, and severe forms, and whether or not an inhibitor (an antibody that interferes with treatment) is present. Common synonyms like "congenital factor IX deficiency" and "factor IX deficiency" help clarify that D67 applies to a range of inherited forms of this coagulation disorder. Medical coders use this specific ICD-10 code for patients with a hereditary shortage or malfunction of factor IX, a crucial protein for blood clotting. It is essential for accurately documenting types such as "hereditary factor IX deficiency disease with inhibitor" or "without inhibitor," to distinguish treatment challenges and patient management needs. In summary, the ICD-10 code for hereditary factor IX deficiency helps healthcare professionals and coders precisely identify this inherited blood clotting disorder and its variations for clinical and billing purposes.

Instructional Notations

Inclusion Terms

These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.

  • Christmas disease
  • Factor IX deficiency (with functional defect)
  • Hemophilia B
  • Plasma thromboplastin component [PTC] deficiency