2027 ICD-10-CM Diagnosis Code Q89.1Congenital malformations of adrenal gland

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q89.1 is a billable ICD-10-CM diagnosis code for congenital malformations of adrenal gland. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 643 through 645. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.1
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformations of adrenal gland
Short Description
Congenital malformations of adrenal gland
Same as the full description in the CMS dataset.
Parent Code
Q89
Other congenital malformations, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.1Congenital malformations of adrenal gland

Present on Admission (POA)Billing

Q89.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal pituitary luteinizing hormone
  • Accessory adrenal cortex
  • Accessory adrenal gland
  • Adrenal cyst
  • Aplasia of adrenal gland
  • Congenital abnormal fusion of adrenal glands
  • Congenital abnormal shape of adrenal gland
  • Congenital absence of adrenal gland
  • Congenital anomaly of adrenal gland
  • Congenital cyst of adrenal gland
  • Congenital hypertrophy of adrenal gland
  • Congenital hypoplasia of adrenal gland
  • Congenital malposition of adrenal gland
  • Deficiency of glycerol kinase
  • Disorder of glycerol metabolism
  • Ectopic adrenal cortex
  • Ectopic adrenal gland
  • Enlarged adrenal gland
  • Extracapsular adrenal tissue
  • Familial adrenal hypoplasia with absent pituitary luteinizing hormone
  • Hypertrophy of adrenal gland
  • Hypoplasia of adrenal medulla
  • Intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomaly syndrome
  • Measurement procedure result absent
  • MIRAGE syndrome
  • SERKAL syndrome
  • Short stature co-occurrent and due to endocrine disorder
  • Xp21 deletion syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q89.1: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • adrenogenital disorders (E25.-)
  • congenital adrenal hyperplasia (E25.0)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.1 Adrenal gland anomaly
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q89.1Overview

What is the ICD-10 code for congenital malformations of adrenal gland?

The ICD-10-CM code for congenital malformations of adrenal gland is Q89.1 (sometimes written as Q891). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q89.1 (Other congenital malformations, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformations of adrenal gland on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q89.1 group to?

When congenital malformations of adrenal gland is the principal diagnosis on an inpatient stay, it groups to MS-DRG 644, 645, 643, with relative weights from 0.7461 to 1.6138 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformations of adrenal gland on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.

Can Q89.1 be reported with a code from E25?

Not as a rule. The Excludes1 note on Q89.1 lists "adrenogenital disorders (E25.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).