2026 ICD-10-CM Diagnosis Code Q89.1Congenital malformations of adrenal gland

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q89.1 is a billable ICD-10-CM diagnosis code for congenital malformations of adrenal gland. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 643 through 645. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.1
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformations of adrenal gland
Short Description
Congenital malformations of adrenal gland
Same as the full description in the CMS dataset.
Parent Code
Q89
Other congenital malformations, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.1Congenital malformations of adrenal gland

Present on Admission (POA)Billing

Q89.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal pituitary luteinizing hormone
  • Accessory adrenal cortex
  • Accessory adrenal gland
  • Adrenal cyst
  • Aplasia of adrenal gland
  • Congenital abnormal fusion of adrenal glands
  • Congenital abnormal shape of adrenal gland
  • Congenital absence of adrenal gland
  • Congenital anomaly of adrenal gland
  • Congenital cyst of adrenal gland
  • Congenital hypertrophy of adrenal gland
  • Congenital hypoplasia of adrenal gland
  • Congenital malposition of adrenal gland
  • Deficiency of glycerol kinase
  • Disorder of glycerol metabolism
  • Ectopic adrenal cortex
  • Ectopic adrenal gland
  • Enlarged adrenal gland
  • Extracapsular adrenal tissue
  • Familial adrenal hypoplasia with absent pituitary luteinizing hormone
  • Hypertrophy of adrenal gland
  • Hypoplasia of adrenal medulla
  • Intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomaly syndrome
  • Measurement procedure result absent
  • MIRAGE syndrome
  • SERKAL syndrome
  • Short stature co-occurrent and due to endocrine disorder
  • Xp21 deletion syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • adrenogenital disorders E25
  • congenital adrenal hyperplasia E25.0

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aberrant(congenital)
      • adrenal gland
    • Absence(of) (organ or part) (complete or partial)
      • adrenal (gland) (congenital)
    • Accessory(congenital)
      • adrenal gland
    • Agenesis
      • adrenal (gland)
    • Anomaly, anomalous(congenital) (unspecified type)
      • adrenal (gland)
    • Cyst(colloid) (mucous) (simple) (retention)
      • adrenal gland
        • congenital
    • Cyst(colloid) (mucous) (simple) (retention)
      • congenital NEC
        • adrenal gland
    • Deformity
      • adrenal gland
    • Displacement, displaced
      • adrenal gland (congenital)
    • Distortion(s) (congenital)
      • adrenal (gland)
    • Ectopic, ectopia(congenital)
      • adrenal gland
    • Hypoplasia, hypoplastic
      • adrenal (gland), congenital
    • Malformation(congenital)
      • adrenal gland
    • Malposition
      • congenital
        • adrenal (gland)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Adrenal Cyst

    a cyst located in the adrenal gland.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.1 Adrenal gland anomaly
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q89.1Overview

Is Q89.1 (Other congenital malformations, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformations of adrenal gland on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q89.1 group to?

When congenital malformations of adrenal gland is the principal diagnosis on an inpatient stay, it groups to MS-DRG 643, 644, 645, with relative weights from 0.7683 to 1.6461 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformations of adrenal gland on inpatient claims.

What is the ICD-9 equivalent of Q89.1?

Under the General Equivalence Mappings, congenital malformations of adrenal gland converts to ICD-9-CM 759.1 (adrenal gland anomaly). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.