ICD-10-CM Code Q87.89

Other specified congenital malformation syndromes, not elsewhere classified

Version 2020 Replaced Code Billable Code POA Exempt

Valid for Submission

Q87.89 is a billable code used to specify a medical diagnosis of other specified congenital malformation syndromes, not elsewhere classified. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q87.89 might also be used to specify conditions or terms like ablepharon, absent eyebrow, acrodysplasia scoliosis, acrokeratosis, adrenal hyperfunction, allemann's syndrome, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Oth congenital malformation syndromes, NEC
Long Description:Other specified congenital malformation syndromes, not elsewhere classified

Replaced Code

This code was replaced in the 2020 ICD-10 code set with the code(s) listed below. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2019. This code was replaced for the FY 2020 (October 1, 2019 - September 30, 2020).

  • Q87.82 - Arterial tortuosity syndrome

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q87.89:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Laurence-Moon (-Bardet)-Biedl syndrome

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q87.89 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Ablepharon
  • Absent eyebrow
  • Acrodysplasia scoliosis
  • Acrokeratosis
  • Adrenal hyperfunction
  • Allemann's syndrome
  • Alstrom syndrome
  • Alveolar bone loss
  • Andersen Tawil syndrome
  • Aplasia cutis congenita secondary to malformation syndrome
  • Aplasia cutis in Johanson-Blizzard syndrome
  • Autosomal dominant dyskeratosis congenita
  • Autosomal dominant popliteal pterygium syndrome
  • Autosomal recessive popliteal pterygium syndrome
  • Axial mesodermal dysplasia spectrum
  • Bamforth Lazarus syndrome
  • Bardet-Biedl syndrome
  • Biemond syndrome type 2
  • Biemond's syndrome
  • Bohring Opitz syndrome
  • Bone age finding
  • Bosley Salih Alorainy syndrome
  • Bowen-Conradi syndrome
  • Braddock syndrome
  • Branchiootic syndrome
  • BSG syndrome
  • Cardiocranial syndrome Pfeiffer type
  • Carney complex
  • Carney complex, trismus, pseudocamptodactyly syndrome
  • Choroideremia
  • Christianson syndrome
  • Chudley McCullough syndrome
  • Cohen syndrome
  • Cohen syndrome
  • Cold-induced sweating syndrome
  • Congenital anomaly of choroid
  • Congenital atresia of external auditory canal
  • Congenital atrophy of optic nerve
  • Congenital blepharophimosis
  • Congenital blepharophimosis
  • Congenital coloboma of iris
  • Congenital intrauterine infection-like syndrome
  • Congenital long QT syndrome
  • Congenital long QT syndrome
  • Congenital malformation of the eyebrow
  • Congenital peripheral pulmonary artery stenosis
  • Constitutional aplastic anemia
  • Cooper Jabs syndrome
  • Costello syndrome
  • Craniofacial deafness hand syndrome
  • Craniofacial ulnar renal syndrome
  • Crisponi syndrome
  • Currarino triad
  • Cutis laxa-corneal clouding-oligophrenia syndrome
  • de Barsy syndrome
  • Delayed bone age
  • Developmental malformation of branchial arch
  • Developmental malformation, deafness, dystonia syndrome
  • Diabetes mellitus associated with genetic syndrome
  • DICER1 syndrome
  • Donnai-Barrow syndrome
  • Dyskeratosis congenita
  • Dystrophy of anterior cornea
  • Ear, patella, short stature syndrome
  • Ectodermal dysplasia with tooth-nail defects
  • Feingold syndrome
  • Floating-Harbor syndrome
  • Francois syndrome
  • Fried syndrome
  • Generalized dystonia
  • Genetic defect of hair shaft
  • German syndrome
  • Gomez Lopez Hernandez syndrome
  • Grubben, De Cock, Borghgraef syndrome
  • Haim Munk syndrome
  • Hecht syndrome
  • Hennekam lymphangiectasia-lymphedema syndrome
  • Heritable pulmonary arterial hypertension
  • Immotile cilia syndrome
  • Immotile cilia syndrome due to defective radial spokes
  • Intellectual disability, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth
  • Intellectual disability, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth
  • Jackson-Weiss syndrome
  • Johnson neuroectodermal syndrome
  • Juberg Hayward syndrome
  • Keutel syndrome
  • Kleefstra syndrome
  • Laurence-Moon syndrome
  • LIG4 syndrome
  • Loeys-Dietz syndrome
  • Long QT syndrome
  • Long QT syndrome
  • Long QT syndrome with genetic marker
  • Long QT syndrome with genetic marker
  • Lowry MacLean syndrome
  • Marden Walker syndrome
  • Marfanoid physique
  • Marfanoid syndrome De Silva type
  • Matthew Wood syndrome
  • McKusick Kaufman syndrome
  • Meacham syndrome
  • Morquio syndrome
  • Multiple malformation syndrome with senile-like appearance
  • Multiple system malformation syndrome
  • Myhre syndrome
  • Myxoma of heart
  • Myxoma of heart
  • N syndrome
  • Nance-Horan syndrome
  • Neu-Laxova syndrome
  • Neuroectodermal endocrine syndrome
  • Neuroectodermal melanolysosomal disease
  • Nicolaides-Baraitser syndrome
  • Oculodental syndrome
  • Oculodentodigital syndrome
  • Oculodento-osseous dysplasia
  • Oculodento-osseous dysplasia
  • Oculodento-osseous dysplasia - mild type
  • Oculodento-osseous dysplasia - severe type
  • Oculofaciocardiodental syndrome
  • Oculotrichodysplasia
  • Ohdo syndrome, Maat-Kievit-Brunner type
  • Ohdo syndrome, Say-Barber-Biesecker-Young-Simpson variant
  • Oto-onycho-peroneal syndrome
  • Pallister-Hall syndrome
  • Papillon-Lefèvre syndrome
  • Pena-Shokeir phenotype
  • Pena-Shokeir syndrome type I
  • Periodontitis co-occurrent with Cohen syndrome
  • Periodontitis co-occurrent with genetic disorder
  • Periodontitis due to Papillon-Lefèvre syndrome
  • Peripheral pulmonary artery stenosis
  • Photosensitivity with ichthyosis, brittle hair, impaired intelligence, decreased fertility and short stature syndrome
  • Polyglandular hyperfunction
  • Popliteal pterygium syndrome
  • Posterior fossa brain malformation, haemaniogma, arterial anomaly, cardiac defect and aortic coarctation, eye abnormality synodrome and sternal anomaly syndrome
  • Posterior fossa brain malformation, hemangioma, arterial anomaly, cardiac defect and aortic coarctation, and eye abnormality syndrome
  • Primary ciliary dyskinesia and retinitis pigmentosa syndrome
  • Primary ciliary dyskinesia due to transposition of ciliary microtubules
  • Pseudoleprechaunism syndrome Patterson type
  • Pseudoprogeria syndrome
  • PURA syndrome
  • Pure gonadal dysgenesis
  • Pure gonadal dysgenesis 46,XY
  • RAB18 deficiency
  • Renpenning syndrome
  • Revesz syndrome
  • Rhombencephalosynapsis
  • Rutland ciliary disorientation syndrome
  • Scholte syndrome
  • Schöpf-Schulz-Passarge syndrome
  • Sensory hearing loss
  • Severe combined immunodeficiency with low T- and B-cell numbers
  • Severe combined immunodeficiency, microcephaly, growth retardation, sensitivity to ionizing radiation syndrome
  • Siegler Brewer Carey syndrome
  • Singleton-Merten syndrome
  • Snyder-Robinson syndrome
  • Speech delay
  • Stern Lubinsky Durrie syndrome
  • Stimmler syndrome
  • Timothy syndrome type 1
  • Trichothiodystrophy
  • VACTEL syndrome
  • Van den Bosch syndrome
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome
  • Vici syndrome
  • Warburg micro syndrome
  • Warburg syndrome
  • Weaver Williams syndrome
  • Wolfram-like syndrome
  • XY type gonadal dysgenesis with associated anomalies syndrome
  • Young's syndrome
  • Zimmermann-Laband syndrome

Diagnostic Related Groups

The ICD-10 code Q87.89 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2020 through 09/30/2020.


Present on Admission (POA)

Q87.89 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q87.89 to ICD-9

  • 759.89 - Specfied cong anomal NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Oth congenital malform syndromes affecting multiple systems (Q87)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. To find others, like heart defects, doctors use special tests. Birth defects can range from mild to severe. Causes can include

  • Genetics
  • Exposures to medicines or chemicals. For example, alcohol abuse can cause fetal alcohol syndrome.
  • Infections during pregnancy
  • Certain medicines. Before you get pregnant, talk to your health care provider about any medicines you take.
  • Not getting enough of certain nutrients. For example, not getting enough folic acid before and during pregnancy is a key factor in causing neural tube defects.

For most birth defects, the cause is unknown.

Health care providers can diagnose certain birth defects during pregnancy, with prenatal tests. That's why it important to get regular prenatal care. Other birth defects may not be found until after the baby is born. Sometimes the defect is obvious right away. Other times, the health care provider may not discover it until later in life.

Babies with birth defects often need special care and treatments. The treatments may include surgery, medicines, assistive devices, and therapies.

Centers for Disease Control and Prevention

[Learn More]