2027 ICD-10-CM Diagnosis Code Q89Other congenital malformations, not elsewhere classified

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q89 is a non-billable ICD-10-CM category code for other congenital malformations, not elsewhere classified, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q89.01, Q89.09, Q89.1, and Q89.2.

Code Identity

ICD-10-CM Code
Q89
Billable Status
No — Non-Billable Category
Code Describes
Other congenital malformations, not elsewhere classified
Short Description
Other congenital malformations, not elsewhere classified
Same as the full description in the CMS dataset.
Chapter
Q80-Q89
Other congenital malformations

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89Other congenital malformations, not elsewhere classified

Specific Coding for Other congenital malformations, not elsewhere classifiedOverview

Non-specific codes like Q89 require more characters. Use one of these billable codes instead:

  • Q89.0 for Congenital absence and malformations of spleen

  • Use Q89.01 for Asplenia (congenital)

  • Use Q89.09 for Congenital malformations of spleen

  • Use Q89.1 for Congenital malformations of adrenal gland

  • Use Q89.2 for Congenital malformations of other endocrine glands

  • Use Q89.3 for Situs inversus

  • Use Q89.4 for Conjoined twins

  • Use Q89.7 for Multiple congenital malformations, not elsewhere classified

  • Q89.8 for Other specified congenital malformations

  • Use Q89.81 for Kabuki syndrome

  • Use Q89.89 for Other specified congenital malformations

  • Use Q89.9 for Congenital malformation, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q89: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q89Overview

What is the ICD-10 code for other congenital malformations, not elsewhere classified?

Q89 is the ICD-10-CM category for other congenital malformations, not elsewhere classified, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is Q89 (Other congenital malformations, not elsewhere classified) a billable code?

No. This is a category header that groups the codes for other congenital malformations, not elsewhere classified, and headers cannot be submitted on claims. Claims for other congenital malformations, not elsewhere classified need a more specific code from this category, such as Q89.01, Q89.09, and Q89.1.