Congenital malformations of the circulatory system (Q20-Q28)

ICD-10 codes Q20-Q28 are used to classify congenital malformations of the circulatory system, encompassing a wide range of heart and blood vessel abnormalities present from birth. These codes cover specific defects in cardiac chambers, septa, valves, great arteries and veins, peripheral vascular system, and miscellaneous circulatory malformations.

This group includes well-known conditions such as common arterial trunk (Q20.0, also called truncus arteriosus), double outlet right ventricle (Q20.1), ventricular septal defects (Q21.0), atrial septal defects (Q21.1), and tetralogy of Fallot (Q21.3). Synonymous terms such as Ebstein’s anomaly (Q22.5), patent ductus arteriosus (Q25.0), and bicuspid aortic valve (Q23.81) are mapped clearly to their respective codes to aid accurate coding. Valve malformations include stenosis and insufficiency of pulmonary, tricuspid, aortic, and mitral valves. The range also covers anomalies of great arteries like coarctation of aorta (Q25.1), interruption of aortic arch (Q25.21), and double aortic arch (Q25.45). Additionally, it includes malformations of great veins such as persistent left superior vena cava (Q26.1) and complex peripheral vascular anomalies like congenital absence or hypoplasia of umbilical artery (Q27.0) and arteriovenous malformations at various sites (Q27.3, Q28.0, Q28.2). Specified and unspecified forms allow for detailed or general coding, facilitating precise documentation of congenital cardiovascular conditions for both clinical understanding and medical coding purposes.