Other congenital malformations (Q80-Q89) ICD-10-CM
The Q80–Q89 section covers other congenital malformations with 98 ICD-10-CM diagnosis codes, of which 81 are billable in fiscal year 2026. The section is organized into the 9 code ranges listed below.
Code Ranges in This Section 9 ranges · 98 codes
The info icon previews the code ranges inside each row and its instructional notations from the official Tabular List.
About the Q80–Q89 Code Range
ICD-10 codes Q80–Q89 categorize a wide range of congenital malformations affecting skin, integument, breast, phakomatoses, malformation syndromes, and other body systems. These codes are used to precisely document birth defects and hereditary syndromes involving structural and functional abnormalities present from birth.
This range includes codes for specific skin disorders like congenital ichthyosis (Q80) with types such as Ichthyosis vulgaris and Lamellar ichthyosis, and epidermolysis bullosa types (Q81), which cause skin fragility. It also covers hereditary lymphedema (Q82.0), xeroderma pigmentosum (Q82.1) characterized by UV sensitivity, and ectodermal dysplasias (Q82.4) involving abnormalities in hair, nails, teeth, and sweat glands. Congenital breast malformations appear under Q83, while Q84 addresses various integumentary system defects including alopecia and nail abnormalities. The phakomatoses category (Q85) includes neurofibromatosis types 1 and 2 and tuberous sclerosis, known for benign tumors affecting skin and nervous tissue. The syndromes subdivision (Q86-Q87) documents malformation syndromes caused by exogenous factors and genetic syndromes like Prader-Willi syndrome (Q87.11) and Marfan syndrome (Q87.4), including manifestations in cardiovascular, skeletal, and ocular systems. Finally, Q89 captures miscellaneous congenital malformations such as asplenia and situs inversus.
These codes assist medical professionals and coders in identifying and recording a spectrum of complex congenital conditions, connecting common terms like “fetal alcohol syndrome,” “accessory nipple,” and “congenital alopecia” to specific ICD-10 codes ensuring accurate diagnosis and data tracking.
Questions About This Page
How many codes are in the Q80-Q89 range?
The Q80-Q89 range contains 98 ICD-10-CM diagnosis codes in FY 2026. 81 of them are billable, and the rest are category headers that organize the section.
What conditions does Q80-Q89 cover?
The range covers other congenital malformations. The code ranges listed above break it into groups of related conditions, and each one links to its own page with the full code list.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
