Congenital malformations of the nervous system (Q00-Q07) ICD-10-CM
The Q00–Q07 section covers congenital malformations of the nervous system with 53 ICD-10-CM diagnosis codes, of which 45 are billable in fiscal year 2027. The section is organized into the 8 code ranges listed below.
Code Ranges in This Section 8 ranges · 53 codes
The info icon previews the code ranges inside each row and its instructional notations from the official Tabular List.
About the Q00–Q07 Code Range
These conditions are malformations of the brain, spinal cord and other parts of the nervous system that are present at birth. An encephalocele is brain tissue protruding through a defect in the skull. Microcephaly involves an underdeveloped cerebrum and a small head.
Q00 separates named malformations, while Q01 separates encephaloceles by location. Q02 identifies microcephaly. Q03 distinguishes named conditions from other or unspecified congenital hydrocephalus. Q04 groups other brain malformations by named structure or condition.
Spina bifida involves a defect in closure of the bony arches of the spine. Q05 separates it by spinal region and whether hydrocephalus is present. Q06 lists other spinal cord malformations, while Q07 groups other nervous system malformations.
Questions About This Page
How many codes are in the Q00-Q07 range?
The Q00-Q07 range contains 53 ICD-10-CM diagnosis codes in FY 2027. 45 of them are billable, and the rest are category headers that organize the section.
What conditions does Q00-Q07 cover?
The range covers congenital malformations of the nervous system. The code ranges listed above break it into groups of related conditions, and each one links to its own page with the full code list.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
