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  6. 2026 ICD-10-CM Code Q89.89

2026 ICD-10-CM Diagnosis Code Q89.89

Other specified congenital malformations

ICD-10-CM Code:
Q89.89
ICD-10 Code for:
Other specified congenital malformations
Is Billable?
Yes - Valid for Submission
Code Navigator:

Q89.89 is a billable diagnosis code used to specify a medical diagnosis of other specified congenital malformations. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2025 through September 30, 2026. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    Q00-Q99
    • Other congenital malformations
      Q80-Q89
      • Other congenital malformations, not elsewhere classified
        Q89

Approximate Synonyms

The following list of clinical terms are approximate synonyms, alternative descriptions, or common phrases that might be used by patients, healthcare providers, or medical coders to describe the same condition. These synonyms and related diagnosis terms are often used when searching for an ICD-10 code, especially when the exact medical terminology is unclear. Whether you're looking for lay terms, similar diagnosis names, or common language alternatives, this list can help guide you to the correct ICD-10 classification.

  • Abnormal communication between pericardial sac and peritoneal cavity
  • Abnormal fetal duplication
  • Acardia
  • Acardia
  • Acephalobrachius
  • Acephalogaster
  • Aggressive fibromatosis of abdomen
  • Aggressive infantile fibromatosis
  • Aggressive systemic infantile myofibromatosis
  • Amniotic adhesion
  • Aplasia cutis congenita due to underlying malformation
  • Aplasia of lymphatic vessel
  • Borjeson-Forssman-Lehmann syndrome
  • Cardiac anomaly and heterotaxy syndrome
  • Celosomus
  • Cephalodiprosopus
  • CHARGE syndrome
  • Coffin-Lowry syndrome
  • Congenital absence of stomach
  • Congenital anomaly of body cavity
  • Congenital anomaly of body cavity
  • Congenital anomaly of body wall
  • Congenital anomaly of lower trunk
  • Congenital anomaly of lymphatic structure of trunk
  • Congenital anomaly of peritoneum
  • Congenital anomaly of trunk
  • Congenital anomaly of upper trunk
  • Congenital deformity of soft tissue
  • Congenital flat back deformity
  • Congenital hemihypertrophy
  • Congenital malformation of lymphatic system of cervicofacial region
  • Congenital malformation of lymphatic vessel of skin
  • Congenital pulmonary lymphatic dysplasia syndrome
  • Congenital short trunk
  • Derencephalus
  • Developmental malformation of branchial arch
  • Dicheirus
  • Diprosopus
  • Diprosopus tetrophthalmus
  • Disproportionate short stature
  • Duplication of upper limb
  • Dysplasia of lung
  • Embryological remnant
  • Hereditary disorder of lymphatic system
  • Hereditary hyperekplexia
  • Hereditary vitreoretinopathy
  • Hereditary vitreoretinopathy
  • Hereditary vitreoretinopathy
  • Hereditary vitreoretinopathy
  • Holoacardius acephalus
  • Holoacardius amorphus
  • Hyperekplexia epilepsy syndrome
  • Hyperexplexia
  • Hyperexplexia
  • Hyperexplexia
  • Infantile myofibromatosis
  • Lethal congenital disproportionate short trunk short stature
  • Lymphatic malformation
  • Marfanoid physique
  • Mixed cystic lymphatic malformation
  • Monocephalus
  • Monocephalus tetrapus dibrachius
  • Mullerian duct and limb anomalies syndrome
  • Mullerian remnant
  • Multicentric infantile myofibromatosis
  • Multifocal lymphangioendotheliomatosis, thrombocytopenia syndrome
  • Myofibromatosis
  • Myofibromatosis
  • Myofibromatosis
  • Myofibromatosis
  • Odontotrichomelic syndrome
  • Omphaloangiopagus
  • Parasitic twin of asymmetrical conjoined twins
  • Peripheral demyelinating neuropathy, central dysmyelinating leukodystrophy, Waardenburg syndrome, Hirschsprung disease
  • Persistent Müllerian duct syndrome
  • PTEN hamartoma tumor syndrome
  • Pygomelus
  • Segmental outgrowth, lipomatosis, arteriovenous malformation, epidermal nevus syndrome
  • Shprintzen Goldberg craniosynostosis syndrome
  • Simonart's band
  • Situs ambiguus
  • Situs ambiguus
  • Solitary infantile myofibromatosis
  • Stickler syndrome
  • Stickler syndrome type 1
  • Stickler syndrome type 2
  • Stickler syndrome type 3
  • Stickler syndrome type 4
  • Thoracodidymus
  • Waardenburg Shah syndrome
  • Waardenburg syndrome
  • Waardenburg syndrome
  • Waardenburg syndrome

Clinical Information

  • Myofibromatosis

    a condition characterized by multiple formations of myofibromas (leiomyoma).

  • Waardenburg Syndrome

    rare, autosomal dominant disease with variable penetrance and several known clinical types. characteristics may include depigmentation of the hair and skin, congenital deafness, heterochromia iridis, medial eyebrow hyperplasia, hypertrophy of the nasal root, and especially dystopia canthorum. the underlying cause may be defective development of the neural crest (neurocristopathy). waardenburg's syndrome may be closely related to piebaldism. klein-waardenburg syndrome refers to a disorder that also includes upper limb abnormalities.

  • CHARGE Syndrome

    rare disease characterized by coloboma; choanal atresia; and abnormal semicircular canals. mutations in chd7 protein resulting in disturbed neural crest development are associated with charge syndrome.

  • Leiomyoma

    a benign tumor derived from smooth muscle tissue, also known as a fibroid tumor. they rarely occur outside of the uterus and the gastrointestinal tract but can occur in the skin and subcutaneous tissue, probably arising from the smooth muscle of small blood vessels in these tissues.

  • Thoracodidymus

    conjoined twins united at the thorax.

  • Stickler Syndrome

    a rare autosomal dominant syndrome caused by mutations in the col11a1, col11a2, and col2a1 genes which affect the production of type ii and xi collagen. it is characterized by a range of signs and symptoms including cleft palate, large tongue, small lower jaw, hearing loss, myopia, glaucoma, retinal detachment, skeletal, and joint abnormalities.

  • Stickler Syndrome Type 1|STL1

    stickler syndrome inherited in an autosomal dominant pattern, caused by mutation(s) in the col2a1 gene, encoding collagen alpha-1(ii) chain.

  • Stickler Syndrome Type 2|Stickler Syndrome Type II

    a rare autosomal dominant syndrome caused by mutations in the col11a1 gene. it is characterized by an abnormal ocular vitreous architecture (beaded vitreous phenotype). other signs and symptoms include retinal detachment, joint hypermobility, hearing loss, and midline clefting.

New 2026 ICD-10-CM Code

Q89.89 is new to ICD-10-CM code set for the FY 2026, effective October 1, 2025. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2025. This is a new and revised code for the FY 2026 (October 1, 2025 - September 30, 2026).

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Index of External Cause of Injuries

References found for this diagnosis code in the External Cause of Injuries Index:

    • Absence(of) (organ or part) (complete or partial)
      • organ
        • or site, congenital NEC
    • Acardia, acardius
    • Acardiacus amorphus
    • Accessory(congenital)
      • genitourinary organs NEC
    • Acephalobrachia monster
    • Acephalochirus monster
    • Acephalogaster
    • Acephalostomus monster
    • Acephalothorax
    • Anomaly, anomalous(congenital) (unspecified type)
      • specified organ or site NEC
    • Atresia, atretic
      • organ or site NEC
    • CHARGE association
    • Cyst(colloid) (mucous) (simple) (retention)
      • congenital NEC
    • Disease, diseased
      • Kok
    • Disease, diseased
      • Startle
    • Goldberg syndrome
    • Hyperekplexia
    • Hyperexplexia
    • Malformation(congenital)
      • specified NEC
    • Myofibromatosis
      • infantile
    • Nephrosis, nephrotic(Epstein's) (syndrome) (congenital)
      • Finnish type (congenital)
    • Syndrome
      • Borjeson Forssman Lehmann
    • Syndrome
      • CHARGE
    • Syndrome
      • Coffin-Lowry
    • Syndrome
      • Goldberg
    • Syndrome
      • Stickler
    • Syndrome
      • stiff baby
    • Teratencephalus

Present on Admission (POA)

Q89.89 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA Indicator: Y

Reason: Diagnosis was present at time of inpatient admission.

CMS Pays CC/MCC DRG? YES

POA Indicator: N

Reason: Diagnosis was not present at time of inpatient admission.

CMS Pays CC/MCC DRG? NO

POA Indicator: U

Reason: Documentation insufficient to determine if the condition was present at the time of inpatient admission.

CMS Pays CC/MCC DRG? NO

POA Indicator: W

Reason: Clinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.

CMS Pays CC/MCC DRG? YES

POA Indicator: 1

Reason: Unreported/Not used - Exempt from POA reporting.

CMS Pays CC/MCC DRG? NO

Replacement Code

Q8989 replaces the following previously assigned ICD-10-CM code(s):

  • Q89.8 - Other specified congenital malformations

Code History

  • FY 2026 - Code Added, effective from 10/1/2025 through 9/30/2026