Other congenital malformations of skin (Q82) ICD-10-CM
The Q82 code range covers other congenital malformations of skin with 10 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the Q82 Range 10 codes · 9 billable
- Q82 Other congenital malformations of skinNon-billable
- Q82.0 Hereditary lymphedema
- Q82.1 Xeroderma pigmentosum
- Q82.2 Congenital cutaneous mastocytosis
- Q82.3 Incontinentia pigmenti
- Q82.4 Ectodermal dysplasia (anhidrotic)
- Q82.5 Congenital non-neoplastic nevus
- Q82.6 Congenital sacral dimple
- Q82.8 Other specified congenital malformations of skin
- Q82.9 Congenital malformation of skin, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q82 range.
Ectodermal Dysplasia
A group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, FOCAL DERMAL HYPOPLASIA, and aplasia cutis congenita.
Incontinentia Pigmenti
A genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Meige Syndrome
A syndrome characterized by orofacial DYSTONIA; including BLEPHAROSPASM; forceful jaw opening; lip retraction; platysma muscle spasm; and tongue protrusion. It primarily affects older adults, with an incidence peak in the seventh decade of life. (From Adams et al., Principles of Neurology, 6th ed, p108)
Xeroderma Pigmentosum
A rare, pigmentary, and atrophic autosomal recessive disease. It is manifested as an extreme photosensitivity to ULTRAVIOLET RAYS as the result of a deficiency in the enzyme that permits excisional repair of ultraviolet-damaged DNA.
About the Q82 Code Range
These skin malformations are present at birth. The subdivisions separate named conditions from specific skin findings and other skin malformations.
Named conditions include hereditary lymphedema (Q82.0), xeroderma pigmentosum (Q82.1), congenital cutaneous mastocytosis (Q82.2), incontinentia pigmenti (Q82.3), and anhidrotic ectodermal dysplasia (Q82.4). Separate subdivisions identify a congenital non-neoplastic nevus (Q82.5) and a congenital sacral dimple (Q82.6). The remaining subdivisions distinguish other specified skin malformations (Q82.8) from unspecified ones (Q82.9).
Questions About This Page
How many billable codes are in the Q82 range?
Of the 10 codes in this range, 9 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q82 range classify?
The range classifies other congenital malformations of skin. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
