Congenital malformations of genital organs (Q50-Q56) ICD-10-CM
The Q50–Q56 section covers congenital malformations of genital organs with 115 ICD-10-CM diagnosis codes, of which 91 are billable in fiscal year 2026. The section is organized into the 7 code ranges listed below.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Code Ranges in This Section 7 ranges · 115 codes
The info icon previews the code ranges inside each row and its instructional notations from the official Tabular List.
About the Q50–Q56 Code Range
ICD-10 codes Q50-Q56 are dedicated to diagnosing and classifying congenital malformations of the genital organs in both females and males. These codes help healthcare providers identify specific structural anomalies present from birth, ensuring precise documentation and appropriate care.
This range covers a wide spectrum of birth defects affecting female reproductive organs such as the ovaries, fallopian tubes, uterus, cervix, vagina, and vulva—including conditions like congenital absence (e.g., Q50.01 for unilateral absence of ovary), uterine malformations (e.g., Q51.3 for bicornate uterus), vaginal anomalies like imperforate hymen (Q52.3), and vulvar abnormalities (Q52.5 for labial fusion). Male genital abnormalities are also included, such as undescended testicles (Q53), hypospadias subtypes (Q54.0 balanic, Q54.1 penile), and malformations of the penis (Q55.6). Additionally, this category incorporates complex conditions related to ambiguous genitalia and pseudohermaphroditism (Q56), addressing disorders of sex development. Synonyms like "agenesis of ovary," "Mayer Rokitansky Küster Hauser syndrome," or "cryptorchidism" correspond to their respective ICD-10 codes, aiding coders in linking clinical diagnosis terms to the correct codes within this specialized chapter.
Questions About This Page
How many codes are in the Q50-Q56 range?
The Q50-Q56 range contains 115 ICD-10-CM diagnosis codes in FY 2026. 91 of them are billable, and the rest are category headers that organize the section.
What conditions does Q50-Q56 cover?
The range covers congenital malformations of genital organs. The code ranges listed above break it into groups of related conditions, and each one links to its own page with the full code list.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
