2024 ICD-10-CM Diagnosis Code Q89.8

Other specified congenital malformations

ICD-10-CM Code:
ICD-10 Code for:
Other specified congenital malformations
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    • Other congenital malformations
      • Other congenital malformations, not elsewhere classified

Q89.8 is a billable diagnosis code used to specify a medical diagnosis of other specified congenital malformations. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abdominal fibromatosis
  • Abnormal communication between pericardial sac and peritoneal cavity
  • Abnormal fetal duplication
  • Acardia
  • Acardia
  • Acephalobrachius
  • Acephalogaster
  • Aggressive fibromatosis
  • Aggressive fibromatosis
  • Aggressive infantile fibromatosis
  • Aggressive systemic infantile myofibromatosis
  • Amniotic adhesion
  • Aplasia cutis congenita due to underlying malformation
  • Borjeson-Forssman-Lehmann syndrome
  • Cardiac anomaly and heterotaxy syndrome
  • Celosomus
  • Cephalodiprosopus
  • CHARGE syndrome
  • Coffin-Lowry syndrome
  • Congenital absence of stomach
  • Congenital anomaly of body cavity
  • Congenital anomaly of body cavity
  • Congenital anomaly of body wall
  • Congenital anomaly of lower trunk
  • Congenital anomaly of lymphatic structure of trunk
  • Congenital anomaly of peritoneum
  • Congenital anomaly of trunk
  • Congenital anomaly of upper trunk
  • Congenital deformity of soft tissue
  • Congenital flat back deformity
  • Congenital hemihypertrophy
  • Congenital malformation of lymphatic system of cervicofacial region
  • Congenital malformation of lymphatic vessel of skin
  • Congenital malformation of vitreous humor
  • Congenital malformation of vitreous humor
  • Congenital malformation of vitreous humor
  • Congenital malformation of vitreous humor
  • Congenital pulmonary lymphatic dysplasia syndrome
  • Congenital short trunk
  • Derencephalus
  • Developmental malformation of branchial arch
  • Dicheirus
  • Diprosopus
  • Diprosopus tetrophthalmus
  • Duplication of upper limb
  • Dysplasia of lung
  • Embryological remnant
  • Hereditary disorder of lymphatic system
  • Hereditary hyperekplexia
  • Hereditary vitreoretinopathy
  • Hereditary vitreoretinopathy
  • Hereditary vitreoretinopathy
  • Hereditary vitreoretinopathy
  • Holoacardius acephalus
  • Holoacardius amorphus
  • Hyperekplexia epilepsy syndrome
  • Hyperexplexia
  • Hyperexplexia
  • Hyperexplexia
  • Infantile myofibromatosis
  • Kabuki make-up syndrome
  • Lymphatic malformation
  • Marfanoid physique
  • Mixed cystic lymphatic malformation
  • Monocephalus
  • Monocephalus tetrapus dibrachius
  • Mullerian duct and limb anomalies syndrome
  • Mullerian remnant
  • Multicentric infantile myofibromatosis
  • Multifocal lymphangioendotheliomatosis, thrombocytopenia syndrome
  • Odontotrichomelic syndrome
  • Omphaloangiopagus
  • Parasitic twin of asymmetrical conjoined twins
  • Peripheral demyelinating neuropathy, central dysmyelinating leukodystrophy, Waardenburg syndrome, Hirschsprung disease
  • Persistent Müllerian duct syndrome
  • PTEN hamartoma tumor syndrome
  • Pygomelus
  • Segmental outgrowth, lipomatosis, arteriovenous malformation, epidermal nevus syndrome
  • Shprintzen Goldberg craniosynostosis syndrome
  • Simonart's band
  • Situs ambiguus
  • Situs ambiguus
  • Solitary infantile myofibromatosis
  • Stickler syndrome
  • Stickler syndrome type 1
  • Stickler syndrome type 2
  • Stickler syndrome type 3
  • Stickler syndrome type 4
  • Thoracodidymus
  • Waardenburg Shah syndrome
  • Waardenburg syndrome
  • Waardenburg syndrome
  • Waardenburg syndrome

Clinical Classification

Clinical Information

  • Waardenburg Syndrome

    rare, autosomal dominant disease with variable penetrance and several known clinical types. characteristics may include depigmentation of the hair and skin, congenital deafness, heterochromia iridis, medial eyebrow hyperplasia, hypertrophy of the nasal root, and especially dystopia canthorum. the underlying cause may be defective development of the neural crest (neurocristopathy). waardenburg's syndrome may be closely related to piebaldism. klein-waardenburg syndrome refers to a disorder that also includes upper limb abnormalities.
  • CHARGE Syndrome

    rare disease characterized by coloboma; choanal atresia; and abnormal semicircular canals. mutations in chd7 protein resulting in disturbed neural crest development are associated with charge syndrome.
  • Stickler Syndrome

    a rare autosomal dominant syndrome caused by mutations in the col11a1, col11a2, and col2a1 genes which affect the production of type ii and xi collagen. it is characterized by a range of signs and symptoms including cleft palate, large tongue, small lower jaw, hearing loss, myopia, glaucoma, retinal detachment, skeletal, and joint abnormalities.
  • Stickler Syndrome Type 1|STL1

    stickler syndrome inherited in an autosomal dominant pattern, caused by mutation(s) in the col2a1 gene, encoding collagen alpha-1(ii) chain.
  • Stickler Syndrome Type 2|Stickler Syndrome Type II

    a rare autosomal dominant syndrome caused by mutations in the col11a1 gene. it is characterized by an abnormal ocular vitreous architecture (beaded vitreous phenotype). other signs and symptoms include retinal detachment, joint hypermobility, hearing loss, and midline clefting.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.

Use Additional Code

Use Additional Code
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
  • code(s) to identify all associated manifestations

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q89.8 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q89.8 to ICD-9-CM

  • ICD-9-CM Code: 759.89 - Specfied cong anomal NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.


[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.