ICD-10-CM Code Q89.8

Other specified congenital malformations

Version 2020 Billable Code POA Exempt

Valid for Submission

Q89.8 is a billable code used to specify a medical diagnosis of other specified congenital malformations. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q89.8 might also be used to specify conditions or terms like abdominal fibromatosis, abnormal communication between pericardial sac and peritoneal cavity, abnormal fetal duplication, acardia, acephalobrachius, acephalogaster, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Other specified congenital malformations
Long Description:Other specified congenital malformations

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q89.8:

Use Additional Code

Use Additional Code
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
  • code(s) to identify all associated manifestations

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q89.8 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abdominal fibromatosis
  • Abnormal communication between pericardial sac and peritoneal cavity
  • Abnormal fetal duplication
  • Acardia
  • Acephalobrachius
  • Acephalogaster
  • Acephalothorax
  • Aggressive fibromatosis
  • Aggressive fibromatosis
  • Aggressive infantile fibromatosis
  • Aggressive systemic infantile myofibromatosis
  • Amniotic adhesion
  • Aplasia cutis congenita due to underlying malformation
  • Atretocephalus
  • Borjeson-Forssman-Lehmann syndrome
  • Cardiac anomaly and heterotaxy syndrome
  • Celosomus
  • Cephalodiprosopus
  • Choanal atresia
  • Choanal atresia with CHARGE association
  • Coffin-Lowry syndrome
  • Coloboma, heart malformation, choanal atresia, retardation of growth and development, genital abnormalities, and ear malformations association
  • Congenital anomaly of body cavity
  • Congenital anomaly of body cavity
  • Congenital anomaly of body wall
  • Congenital anomaly of lower trunk
  • Congenital anomaly of lymphatic structure of trunk
  • Congenital anomaly of peritoneum
  • Congenital anomaly of trunk
  • Congenital anomaly of upper trunk
  • Congenital atresia of nares
  • Congenital atresia of nasopharynx
  • Congenital atresia of pharynx
  • Congenital flat back deformity
  • Congenital hemihypertrophy
  • Congenital malformation of cutaneous lymphatics
  • Congenital pulmonary lymphatic dysplasia syndrome
  • Congenital short trunk
  • Cryptodidymus
  • Derencephalus
  • Developmental malformation of branchial arch
  • Dicheirus
  • Diprosopus
  • Diprosopus tetrophthalmus
  • Duplication of upper limb
  • Embryological remnant
  • Hereditary disorder of lymphatic system
  • Hereditary hyperekplexia
  • Hereditary vitreoretinopathy
  • Holoacardius acephalus
  • Holoacardius amorphus
  • Hyperexplexia
  • Infantile myofibromatosis
  • Kabuki make-up syndrome
  • Kniest-Stickler dysplasia group
  • Malformation association
  • Malformation association
  • Monocephalus
  • Monocephalus tetrapus dibrachius
  • Mullerian duct and limb anomalies syndrome
  • Mullerian remnant
  • Multicentric infantile myofibromatosis
  • MVRCS association
  • Myoclonus
  • Nodular embryo
  • Odontotrichomelic syndrome
  • Omphaloangiopagus
  • Parasitic twin of asymmetrical conjoined twins
  • Peripheral demyelinating neuropathy, central dysmyelinating leukodystrophy, Waardenburg syndrome, Hirschsprung disease
  • Persistent Müllerian duct syndrome
  • PTEN hamartoma tumor syndrome
  • Pygomelus
  • Regional congenital anomaly
  • Regional congenital anomaly
  • Segmental outgrowth, lipomatosis, arteriovenous malformation, epidermal nevus syndrome
  • Shortened trunk
  • Simonart's band
  • Situs ambiguus
  • Situs ambiguus
  • Solitary infantile myofibromatosis
  • Stickler syndrome
  • Stunted embryo
  • Thoracodidymus
  • Variation of umbilical cord
  • Waardenburg Shah syndrome
  • Waardenburg's syndrome
  • Waardenburg's syndrome

Diagnostic Related Groups

The ICD-10 code Q89.8 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q89.8 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q89.8 to ICD-9

  • 759.89 - Specfied cong anomal NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations, not elsewhere classified (Q89)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. To find others, like heart defects, doctors use special tests. Birth defects can range from mild to severe. Causes can include

  • Genetics
  • Exposures to medicines or chemicals. For example, alcohol abuse can cause fetal alcohol syndrome.
  • Infections during pregnancy
  • Certain medicines. Before you get pregnant, talk to your health care provider about any medicines you take.
  • Not getting enough of certain nutrients. For example, not getting enough folic acid before and during pregnancy is a key factor in causing neural tube defects.

For most birth defects, the cause is unknown.

Health care providers can diagnose certain birth defects during pregnancy, with prenatal tests. That's why it important to get regular prenatal care. Other birth defects may not be found until after the baby is born. Sometimes the defect is obvious right away. Other times, the health care provider may not discover it until later in life.

Babies with birth defects often need special care and treatments. The treatments may include surgery, medicines, assistive devices, and therapies.

Centers for Disease Control and Prevention

[Learn More]