Congenital malformations of the urinary system (Q60-Q64)

ICD-10 codes Q60 to Q64 cover congenital malformations of the urinary system, including abnormalities of the kidneys, ureters, bladder, and urethra present at birth. These codes are used to classify specific developmental defects such as renal agenesis, cystic kidney diseases, and obstructive urinary tract anomalies.

This range includes codes for renal agenesis and hypoplasia (Q60), which correspond to conditions where one or both kidneys are missing or underdeveloped, often referred to as "renal agenesis" or "hypoplastic kidney." Codes like Q61 categorize various congenital cystic kidney diseases, encompassing infantile and adult-type polycystic kidney disease. The segment Q62 addresses congenital obstructive defects including hydronephrosis, megaureter, and abnormalities like ureterocele or ureter malposition. For example, Q62.7 denotes congenital vesico-uretero-renal reflux, a backward flow of urine from bladder to kidneys. Additionally, Q63 describes other kidney malformations such as horseshoe kidney or ectopic kidney, while Q64 covers other congenital urinary tract malformations like epispadias, bladder exstrophy, and urethral anomalies. Recognizing specific synonyms, such as "Potter’s syndrome" for Q60.6 or "exstrophy epispadias complex" linked to Q64.0, helps ensure precise coding for congenital urinary disorders. These codes guide clinical documentation and epidemiologic tracking of urinary birth defects.