2027 ICD-10-CM Diagnosis Code Q75.8Other specified congenital malformations of skull and face bones

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q75

ICD-10-CM Q75.8
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q75.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of skull and face bones. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q75.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of skull and face bones
Short Description
Oth congenital malformations of skull and face bones
Parent Code
Q75
Other congenital malformations of skull and face bones

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ75Other congenital malformations of skull and face bones
This CodeQ75.8Other specified congenital malformations of skull and face bones

Present on Admission (POA)Billing

Q75.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 3C syndrome
  • Absence of skull bone
  • Acalvaria
  • Acrocephalopolydactyly
  • Agenesis of nasal bone
  • Agenesis of neurocranium
  • Agenesis of premaxilla
  • Agenesis of vomer
  • Anterior perimaxillary faciosynostosis
  • Anterior pituitary hormone deficiency
  • Aplasia of bone of cranium
  • Aplasia of nasal bone
  • Aplasia of premaxilla
  • Basilar skull invagination
  • Bathrocephaly
  • Bilateral craniofacial microsomia
  • Bipartite ossification
  • Bipartite ossification of interparietal bone
  • Bipartite ossification of supraoccipital bone
  • Cheilognathoprosoposchisis
  • Choanal atresia
  • Choanal atresia, hearing loss, cardiac defect, craniofacial dysmorphism syndrome
  • Cleft mandible
  • Cloverleaf skull syndrome
  • Cloverleaf skull with multiple congenital anomalies syndrome
  • Complete perimaxillary faciosynostosis
  • Complex craniosynostosis
  • Congenital abnormal fusion of alisphenoid bone
  • Congenital abnormal fusion of basioccipital bone
  • Congenital abnormal fusion of basisphenoid bone
  • Congenital abnormal fusion of exoccipital bone
  • Congenital abnormal fusion of frontal bone
  • Congenital abnormal fusion of interparietal bone
  • Congenital abnormal fusion of parietal bone
  • Congenital abnormal fusion of premaxilla
  • Congenital abnormal fusion of presphenoid bone
  • Congenital abnormal fusion of squamosal bone
  • Congenital abnormal fusion of supraoccipital bone
  • Congenital abnormal fusion of tympanic anulus
  • Congenital abnormal fusion of vomer
  • Congenital abnormal fusion of zygomatic bone
  • Congenital abnormal shape of alisphenoid bone
  • Congenital abnormal shape of basioccipital bone
  • Congenital abnormal shape of basisphenoid bone
  • Congenital abnormal shape of exoccipital bone
  • Congenital abnormal shape of frontal bone
  • Congenital abnormal shape of interparietal bone
  • Congenital abnormal shape of nasal bone
  • Congenital abnormal shape of parietal bone
  • Congenital abnormal shape of premaxilla
  • Congenital abnormal shape of presphenoid bone
  • Congenital abnormal shape of squamosal bone
  • Congenital abnormal shape of supraoccipital bone
  • Congenital abnormal shape of tympanic anulus
  • Congenital abnormal shape of vomer
  • Congenital abnormal shape of zygomatic bone
  • Congenital abnormality of skull shape
  • Congenital absence of alisphenoid bone
  • Congenital absence of basioccipital bone
  • Congenital absence of basisphenoid bone
  • Congenital absence of cranial vault
  • Congenital absence of exoccipital bone
  • Congenital absence of frontal bone
  • Congenital absence of interparietal bone
  • Congenital absence of nasal bone
  • Congenital absence of nasal septum
  • Congenital absence of parietal bone
  • Congenital absence of premaxilla
  • Congenital absence of presphenoid bone
  • Congenital absence of skull bone
  • Congenital absence of squamosal bone
  • Congenital absence of supraoccipital bone
  • Congenital absence of tympanic anulus
  • Congenital absence of vomer
  • Congenital absence of zygomatic bone
  • Congenital anomaly of alisphenoid bone
  • Congenital anomaly of basioccipital bone
  • Congenital anomaly of basisphenoid bone
  • Congenital anomaly of craniovertebral junction
  • Congenital anomaly of exoccipital bone
  • Congenital anomaly of frontal bone
  • Congenital anomaly of interparietal bone
  • Congenital anomaly of lacrimal bone
  • Congenital anomaly of nasal bone
  • Congenital anomaly of palatine bone
  • Congenital anomaly of parietal bone
  • Congenital anomaly of premaxilla
  • Congenital anomaly of presphenoid bone
  • Congenital anomaly of squamosal bone
  • Congenital anomaly of supraoccipital bone
  • Congenital anomaly of tympanic anulus
  • Congenital anomaly of vomer
  • Congenital anomaly of zygomatic bone
  • Congenital asymmetry of forehead
  • Congenital deformity of forehead
  • Congenital dyserythropoietic anemia
  • Congenital enlargement of fontanel
  • Congenital facial asymmetry
  • Congenital fenestration of alisphenoid bone
  • Congenital fenestration of basioccipital bone
  • Congenital fenestration of basisphenoid bone
  • Congenital fenestration of exoccipital bone
  • Congenital fenestration of frontal bone
  • Congenital fenestration of interparietal bone
  • Congenital fenestration of nasal bone
  • Congenital fenestration of parietal bone
  • Congenital fenestration of premaxilla
  • Congenital fenestration of presphenoid bone
  • Congenital fenestration of squamosal bone
  • Congenital fenestration of supraoccipital bone
  • Congenital hypertrophy of sphenoid bone
  • Congenital hypoplasia of alisphenoid bone
  • Congenital hypoplasia of anterior pituitary
  • Congenital hypoplasia of basioccipital bone
  • Congenital hypoplasia of basisphenoid bone
  • Congenital hypoplasia of bilateral zygomatic bones
  • Congenital hypoplasia of bone of cranium
  • Congenital hypoplasia of carotid canal
  • Congenital hypoplasia of clavicle
  • Congenital hypoplasia of exoccipital bone
  • Congenital hypoplasia of frontal bone
  • Congenital hypoplasia of interparietal bone
  • Congenital hypoplasia of lacrimal bone
  • Congenital hypoplasia of left zygomatic bone
  • Congenital hypoplasia of nasal septum
  • Congenital hypoplasia of parietal bone
  • Congenital hypoplasia of premaxilla
  • Congenital hypoplasia of presphenoid bone
  • Congenital hypoplasia of right zygomatic bone
  • Congenital hypoplasia of squamosal bone
  • Congenital hypoplasia of supraoccipital bone
  • Congenital hypoplasia of tympanic anulus
  • Congenital hypoplasia of vomer
  • Congenital hypoplasia of zygomatic bone
  • Congenital J shaped sella turcica
  • Congenital malformation of anterior pituitary
  • Congenital malformation of sphenoid wing
  • Craniofacial cleft
  • Craniofacial conodysplasia syndrome
  • Craniofacial dysplasia osteopenia syndrome
  • Craniofacial microsomia
  • Craniofaciofrontodigital syndrome
  • Craniolacunia
  • Craniolenticulosutural dysplasia
  • Cranioosteoarthropathy
  • Cranioschisis
  • Cytochrome-c oxidase deficiency
  • Defect of skull ossification
  • Delayed membranous cranial ossification
  • Disorder of lacrimal bone
  • Domed head
  • Doughnut lesion of calvaria and bone fragility syndrome
  • Endosteal hyperostoses
  • Enlarged parietal foramina
  • Exocrine pancreatic insufficiency
  • Frontal bossing
  • Frontal dysostosis
  • Frontonasal dysplasia sequence
  • Frontonasal dysplasia, bifid nose, upper limb anomalies syndrome
  • Frontorhiny
  • Hyperostosis cranialis interna
  • Hypertelorism
  • Incomplete ossification of alisphenoid bone
  • Incomplete ossification of basioccipital bone
  • Incomplete ossification of basisphenoid bone
  • Incomplete ossification of exoccipital bone
  • Incomplete ossification of frontal bone
  • Incomplete ossification of interparietal bone
  • Incomplete ossification of nasal bone
  • Incomplete ossification of palatine bone
  • Incomplete ossification of parietal bone
  • Incomplete ossification of premaxilla
  • Incomplete ossification of presphenoid bone
  • Incomplete ossification of skull
  • Incomplete ossification of squamosal bone
  • Incomplete ossification of supraoccipital bone
  • Incomplete ossification of tympanic anulus
  • Incomplete ossification of zygomatic bone
  • Infraorbital facial cleft - Tessier cleft 4
  • Infraorbital facial cleft - Tessier cleft 5
  • Infraorbital facial cleft - Tessier cleft 6
  • Infraorbital facial cleft - Tessier cleft 7
  • Intellectual disability, craniofacial dysmorphism, cryptorchidism syndrome
  • Lack of ossification of alisphenoid bone
  • Lack of ossification of basioccipital bone
  • Lack of ossification of basisphenoid bone
  • Lack of ossification of exoccipital bone
  • Lack of ossification of frontal bone
  • Lack of ossification of interparietal bone
  • Lack of ossification of nasal bone
  • Lack of ossification of palatine bone
  • Lack of ossification of parietal bone
  • Lack of ossification of premaxilla
  • Lack of ossification of presphenoid bone
  • Lack of ossification of squamosal bone
  • Lack of ossification of supraoccipital bone
  • Lack of ossification of tympanic anulus
  • Lack of ossification of zygomatic bone
  • Leptocephaly
  • Localized congenital skull defect
  • MacDermot Winter syndrome
  • Metopic ridging, ptosis, facial dysmorphism syndrome
  • Microbrachycephaly, ptosis, cleft lip syndrome
  • Midline facial cleft - Tessier cleft 0
  • Midline facial cleft - Tessier cleft 14
  • Midline facial cleft - Tessier cleft 30
  • Occipital dysplasia
  • Osteochondrodysplasia with osteopetrosis
  • Osteosclerosis
  • Overgrowth, macrocephaly, facial dysmorphism syndrome
  • Overriding skull bones
  • Pancreatic insufficiency
  • Pancreatic insufficiency, dyserythropoietic anemia, calvarial hyperostosis syndrome
  • Paramedian facial cleft - Tessier cleft 1
  • Paramedian facial cleft - Tessier cleft 2
  • Paramedian facial cleft - Tessier cleft 3
  • Parietal foramina with clavicular hypoplasia
  • Parieto-occipital craniosynostosis
  • Platybasia
  • Posterior perimaxillary faciosynostosis
  • Progressive sclerosis of base of skull
  • Robin sequence
  • Sagittal craniosynostosis
  • Sclerosis of base of skull
  • Short stature, Pierre Robin sequence, cleft mandible, hand anomalies, clubfoot syndrome
  • Short stature, pituitary and cerebellar defect and small sella turcica syndrome
  • Short stature, wormian bones, dextrocardia syndrome
  • SIX2-related frontonasal dysplasia
  • Spheno-fronto-parietal craniofaciosynostosis
  • Supraorbital facial cleft - Tessier cleft 10
  • Supraorbital facial cleft - Tessier cleft 11
  • Supraorbital facial cleft - Tessier cleft 12
  • Supraorbital facial cleft - Tessier cleft 13
  • Supraorbital facial cleft - Tessier cleft 8
  • Supraorbital facial cleft - Tessier cleft 9
  • Vomero-premaxillary faciosynostosis
  • Wormian bone of cranium
  • Wormian bones, micrognathia, abnormal dentition, progeroid syndrome
  • X-linked intellectual disability, craniofacioskeletal syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q75.8: its own notes plus those printed at Q75 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Absence of skull bone, congenital
  • Congenital deformity of forehead
  • Platybasia

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q75 Other congenital malformations of skull and face bones applies to 22 codes
  • congenital malformation of face NOS (Q18.-)
  • congenital malformation syndromes classified to Q87.-
  • dentofacial anomalies [including malocclusion] (M26.-)
  • musculoskeletal deformities of head and face (Q67.0-Q67.4)
  • skull defects associated with congenital anomalies of brain such as:
  • anencephaly (Q00.0)
  • encephalocele (Q01.-)
  • hydrocephalus (Q03.-)
  • microcephaly (Q02)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q75.8, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q75.8: they are not reported together with it, unless the two conditions are unrelated.

  • Q18 Other congenital malformations of face and neck
    congenital malformations of skull and face bones (Q75.-) names Q75.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Platybasia

    a developmental deformity of the occipital bone and upper end of the cervical spine, in which the latter appears to have pushed the floor of the occipital bone upward. (dorland, 27th ed)

Patient EducationClinical

Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q75.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.0 Anomal skull/face bones
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q75.8Overview

What is the ICD-10 code for other specified congenital malformations of skull and face bones?

The ICD-10-CM code for other specified congenital malformations of skull and face bones is Q75.8 (sometimes written as Q758). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q75.8 (Other congenital malformations of skull and face bones) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of skull and face bones on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q75.8 group to?

When other specified congenital malformations of skull and face bones is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q75.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of skull and face bones on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.

Can Q75.8 be reported with a code from Q18?

Not as a rule. The Excludes1 note at Q75, which applies to Q75.8, lists "congenital malformation of face NOS (Q18.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).