2024 ICD-10-CM Diagnosis Code Q00.0
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Anencephaly without rachischisis
- Congenital absence of left hand
- Congenital absence of right hand
- Congenital brain aplasia
- Holoacardius acephalus
- Incomplete anencephaly
Clinical Category is Nervous system congenital anomalies
- CCSR Category Code: MAL004
- Inpatient Default CCSR: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.
- Outpatient Default CCSR: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.
Anencephalya malformation of the nervous system caused by failure of the anterior neuropore to close. infants are born with intact spinal cords, cerebellums, and brainstems, but lack formation of neural structures above this level. the skull is only partially formed but the eyes are usually normal. this condition may be associated with folate deficiency. affected infants are only capable of primitive (brain stem) reflexes and usually do not survive for more than two weeks. (from menkes, textbook of child neurology, 5th ed, p247)
Tabular List of Diseases and Injuries
The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.
Inclusion TermsInclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and Injuries References
The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).
- - Absence (of) (organ or part) (complete or partial)
- - Acrania - Q00.0
- - Amyelencephalus, amyelencephaly - Q00.0
- - Anencephalus, anencephaly - Q00.0
- - Anomaly, anomalous (congenital) (unspecified type) - Q89.9
- - Hemianencephaly - Q00.0
- - Hemicephalus, hemicephaly - Q00.0
Present on Admission (POA)
CMS POA Indicator Options and Definitions
|Reason for Code
|CMS will pay the CC/MCC DRG?
|Diagnosis was present at time of inpatient admission.
|Diagnosis was not present at time of inpatient admission.
|Documentation insufficient to determine if the condition was present at the time of inpatient admission.
|Clinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.
|Unreported/Not used - Exempt from POA reporting.
Neural Tube Defects
Neural tube defects are birth defects of the brain, spine, or spinal cord. They happen in the first month of pregnancy, often before a woman even knows that she is pregnant. The two most common neural tube defects are spina bifida and anencephaly. In spina bifida, the fetal spinal column doesn't close completely. There is usually nerve damage that causes at least some paralysis of the legs. In anencephaly, most of the brain and skull do not develop. Babies with anencephaly are usually either stillborn or die shortly after birth. Another type of defect, Chiari malformation, causes the brain tissue to extend into the spinal canal.
The exact causes of neural tube defects aren't known. You're at greater risk of having an infant with a neural tube defect if you:
- Have obesity
- Have poorly controlled diabetes
- Take certain antiseizure medicines
Getting enough folic acid, a type of B vitamin, before and during pregnancy prevents most neural tube defects.
Neural tube defects are usually diagnosed before the infant is born, through lab or imaging tests. There is no cure for neural tube defects. The nerve damage and loss of function that are present at birth are usually permanent. However, a variety of treatments can sometimes prevent further damage and help with complications.
NIH: National Institute of Child Health and Human Development
[Learn More in MedlinePlus]
Anencephaly is a condition that prevents the normal development of the brain and the bones of the skull. This condition results when a structure called the neural tube fails to close during the first few weeks of embryonic development. The neural tube is a layer of cells that ultimately develops into the brain and spinal cord. Because anencephaly is caused by abnormalities of the neural tube, it is classified as a neural tube defect.
Because the neural tube fails to close properly, the developing brain and spinal cord are exposed to the amniotic fluid that surrounds the fetus in the womb. This exposure causes the nervous system tissue to break down (degenerate). As a result, people with anencephaly are missing large parts of the brain called the cerebrum and cerebellum. These brain regions are necessary for thinking, hearing, vision, emotion, and coordinating movement. The bones of the skull are also missing or incompletely formed.
Because these nervous system abnormalities are so severe, almost all babies with anencephaly die before birth or within a few hours or days after birth.
[Learn More in MedlinePlus]
- FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
- FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
- FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.
 Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.