ICD-10-CM Code Q75.3


Version 2020 Billable Code POA Exempt

Valid for Submission

Q75.3 is a billable code used to specify a medical diagnosis of macrocephaly. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q75.3 might also be used to specify conditions or terms like bannayan syndrome, childhood obesity, congenital abnormal shape of rib, congenital anomaly of sclera, congenital deformity of chest wall, congenital pectus excavatum, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Macrocephaly
Long Description:Macrocephaly

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q75.3 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Bannayan syndrome
  • Childhood obesity
  • Congenital abnormal shape of rib
  • Congenital anomaly of sclera
  • Congenital deformity of chest wall
  • Congenital pectus excavatum
  • Corneal fragility keratoglobus, blue sclerae AND joint hypermobility
  • Cutis laxa, autosomal recessive
  • Dandy-Walker syndrome
  • Dandy-Walker syndrome
  • Ehlers-Danlos syndrome, hydroxylysine-deficient
  • Facial dysmorphism, macrocephaly, myopia, Dandy-Walker malformation syndrome
  • Fetal macrocephaly
  • Fryns macrocephaly
  • Heide syndrome
  • Intellectual disability, seizures, macrocephaly, obesity syndrome
  • Macrocephaly
  • Macrocephaly and developmental delay syndrome
  • Macrocephaly, short stature, paraplegia syndrome
  • Macrocephaly-capillary malformation
  • MACS syndrome
  • MOMO syndrome
  • Obesity by age of onset
  • Overgrowth, macrocephaly, facial dysmorphism syndrome
  • Pectus excavatum
  • Pectus excavatum, macrocephaly, dysplastic nails syndrome
  • PTEN hamartoma tumor syndrome
  • Relative macrocephaly
  • Scleral discoloration
  • X-linked intellectual disability, macrocephaly, macroorchidism syndrome
  • X-linked recessive intellectual disability and macrocephaly with ciliary dysfunction syndrome

Clinical Information

  • HAMARTOMA SYNDROME MULTIPLE-. a hereditary disease characterized by multiple ectodermal mesodermal and endodermal nevoid and neoplastic anomalies. facial trichilemmomas and papillomatous papules of the oral mucosa are the most characteristic lesions. individuals with this syndrome have a high risk of breast cancer; thyroid cancer; and endometrial cancer. this syndrome is associated with mutations in the gene for pten phosphatase.
  • MEGALENCEPHALY-. a congenital abnormality in which the occipitofrontal circumference is greater than two standard deviations above the mean for a given age. it is associated with hydrocephalus; subdural effusion; arachnoid cysts; or is part of a genetic condition e.g. alexander disease; sotos syndrome.
  • HEMIMEGALENCEPHALY-. rare malformations of cortical development group i characterized by the enlargement of one side of the brain. it is associated with seizures partial paralysis and mental retardation.

Diagnostic Related Groups

The ICD-10 code Q75.3 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q75.3 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q75.3 to ICD-9

  • 756.0 - Anomal skull/face bones (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations and deformations of the musculoskeletal system (Q65-Q79)
      • Other congenital malformations of skull and face bones (Q75)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks. These conditions may also affect other parts of the body.

Treatment depends on the type of problem. Plastic and reconstructive surgery may help the person's appearance.

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