2026 ICD-10-CM Diagnosis Code Q87Other specified congenital malformation syndromes affecting multiple systems

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87

ICD-10-CM Q87
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q87 is a non-billable ICD-10-CM category code for other specified congenital malformation syndromes affecting multiple systems, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q87.0, Q87.11, Q87.19, and Q87.2.

Code Identity

ICD-10-CM Code
Q87
Billable Status
No — Non-Billable Category
Code Describes
Other specified congenital malformation syndromes affecting multiple systems
Chapter
Q80-Q89
Other congenital malformations

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ87Other specified congenital malformation syndromes affecting multiple systems
This CodeQ87Other specified congenital malformation syndromes affecting multiple systems

Specific Coding for Oth congenital malform syndromes affecting multiple systemsOverview

Non-specific codes like Q87 require more characters. Use one of these billable codes instead:

  • Use Q87.0 for Congenital malformation syndromes predominantly affecting facial appearance

  • Q87.1 for Congenital malformation syndromes predominantly associated with short stature

  • Use Q87.11 for Prader-Willi syndrome

  • Use Q87.19 for Other congenital malformation syndromes predominantly associated with short stature

  • Use Q87.2 for Congenital malformation syndromes predominantly involving limbs

  • Use Q87.3 for Congenital malformation syndromes involving early overgrowth

  • Q87.4 for Marfan syndrome

  • Use Q87.40 for Marfan syndrome, unspecified

  • Q87.41 for Marfan syndrome with cardiovascular manifestations

  • Use Q87.42 for Marfan syndrome with ocular manifestations

  • Use Q87.43 for Marfan syndrome with skeletal manifestation

  • Use Q87.5 for Other congenital malformation syndromes with other skeletal changes

  • Q87.8 for Other specified congenital malformation syndromes, not elsewhere classified

  • Use Q87.81 for Alport syndrome

  • Use Q87.82 for Arterial tortuosity syndrome

  • Use Q87.83 for Bardet-Biedl syndrome

  • Use Q87.84 for Laurence-Moon syndrome

  • Use Q87.85 for MED13L syndrome

  • Use Q87.86 for Kleefstra syndrome

  • Use Q87.87 for Hao-Fountain Syndrome

  • Use Q87.88 for CTNNB1 syndrome

  • Use Q87.89 for Other specified congenital malformation syndromes, not elsewhere classified

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Use Additional Code

  • code(s) to identify all associated manifestations

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q87Overview

Is Q87 a billable code?

No. This is a category header that groups the codes for other specified congenital malformation syndromes affecting multiple systems, and headers cannot be submitted on claims. Claims for other specified congenital malformation syndromes affecting multiple systems need a more specific code from this category, such as Q87.0, Q87.11, and Q87.19.