2027 ICD-10-CM Diagnosis Code Q87Other specified congenital malformation syndromes affecting multiple systems

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87

ICD-10-CM Q87
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q87 is a non-billable ICD-10-CM category code for other specified congenital malformation syndromes affecting multiple systems, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q87.0, Q87.11, Q87.19, and Q87.2.

Code Identity

ICD-10-CM Code
Q87
Billable Status
No — Non-Billable Category
Code Describes
Other specified congenital malformation syndromes affecting multiple systems
Short Description
Oth congenital malform syndromes affecting multiple systems
Chapter
Q80-Q89
Other congenital malformations

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ87Other specified congenital malformation syndromes affecting multiple systems
This CodeQ87Other specified congenital malformation syndromes affecting multiple systems

Specific Coding for Oth congenital malform syndromes affecting multiple systemsOverview

Non-specific codes like Q87 require more characters. Use one of these billable codes instead:

  • Use Q87.0 for Congenital malformation syndromes predominantly affecting facial appearance

  • Q87.1 for Congenital malformation syndromes predominantly associated with short stature

  • Use Q87.11 for Prader-Willi syndrome

  • Use Q87.19 for Other congenital malformation syndromes predominantly associated with short stature

  • Use Q87.2 for Congenital malformation syndromes predominantly involving limbs

  • Use Q87.3 for Congenital malformation syndromes involving early overgrowth

  • Q87.4 for Marfan syndrome

  • Use Q87.40 for Marfan syndrome, unspecified

  • Q87.41 for Marfan syndrome with cardiovascular manifestations

  • Use Q87.42 for Marfan syndrome with ocular manifestations

  • Use Q87.43 for Marfan syndrome with skeletal manifestation

  • Use Q87.5 for Other congenital malformation syndromes with other skeletal changes

  • Q87.8 for Other specified congenital malformation syndromes, not elsewhere classified

  • Use Q87.81 for Alport syndrome

  • Use Q87.82 for Arterial tortuosity syndrome

  • Use Q87.83 for Bardet-Biedl syndrome

  • Use Q87.84 for Laurence-Moon syndrome

  • Use Q87.85 for MED13L syndrome

  • Use Q87.86 for Kleefstra syndrome

  • Use Q87.87 for Hao-Fountain Syndrome

  • Use Q87.88 for CTNNB1 syndrome

  • Use Q87.89 for Other specified congenital malformation syndromes, not elsewhere classified

  • Use Q87.A for Loeys-Dietz syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q87: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Use Additional Code

Add a second code, after this one, to fully describe the condition.

  • code(s) to identify all associated manifestations

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q87, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming Q87: they are not reported together with it, unless the two conditions are unrelated.

  • Q67 Congenital musculoskeletal deformities of head, face, spine and chest
    congenital malformation syndromes classified to Q87.-
  • Q75 Other congenital malformations of skull and face bones
    congenital malformation syndromes classified to Q87.-
  • Q89.7 Multiple congenital malformations, not elsewhere classified
    congenital malformation syndromes affecting multiple systems (Q87.-)

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q87Overview

Is Q87 a billable code?

No. This is a category header that groups the codes for other specified congenital malformation syndromes affecting multiple systems, and headers cannot be submitted on claims. Claims for other specified congenital malformation syndromes affecting multiple systems need a more specific code from this category, such as Q87.0, Q87.11, and Q87.19.

Does Q87 need an additional code?

When the condition applies, yes. The Use Additional Code note reads: code(s) to identify all associated manifestations. The additional code is reported after Q87.