1. Home
  2. ICD-10-CM Codes
  3. Q00-Q99
  4. Q80-Q89
  5. Q87
  6. 2025 ICD-10-CM Code Q87
Version 2025
Non-Billable Code

2025 ICD-10-CM Diagnosis Code Q87

Other specified congenital malformation syndromes affecting multiple systems

ICD-10-CM Code:
Q87
ICD-10 Code for:
Oth congenital malform syndromes affecting multiple systems
Is Billable?
Not Valid for Submission
Code Navigator:

Q87 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of other specified congenital malformation syndromes affecting multiple systems. The code is not specific and is NOT valid for the year 2025 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Oth congenital malform syndromes affecting multiple systems

Non-specific codes like Q87 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for oth congenital malform syndromes affecting multiple systems:

  • Use Q87.0 for Congenital malformation syndromes predominantly affecting facial appearance - BILLABLE CODE

  • Q87.1 for Congenital malformation syndromes predominantly associated with short stature - NON-BILLABLE CODE

  • Use Q87.11 for Prader-Willi syndrome - BILLABLE CODE

  • Use Q87.19 for Other congenital malformation syndromes predominantly associated with short stature - BILLABLE CODE

  • Use Q87.2 for Congenital malformation syndromes predominantly involving limbs - BILLABLE CODE

  • Use Q87.3 for Congenital malformation syndromes involving early overgrowth - BILLABLE CODE

  • Q87.4 for Marfan syndrome - NON-BILLABLE CODE

  • Use Q87.40 for Marfan syndrome, unspecified - BILLABLE CODE

  • Q87.41 for Marfan syndrome with cardiovascular manifestations - NON-BILLABLE CODE

  • Use Q87.42 for Marfan syndrome with ocular manifestations - BILLABLE CODE

  • Use Q87.43 for Marfan syndrome with skeletal manifestation - BILLABLE CODE

  • Use Q87.5 for Other congenital malformation syndromes with other skeletal changes - BILLABLE CODE

  • Q87.8 for Other specified congenital malformation syndromes, not elsewhere classified - NON-BILLABLE CODE

  • Use Q87.81 for Alport syndrome - BILLABLE CODE

  • Use Q87.82 for Arterial tortuosity syndrome - BILLABLE CODE

  • Use Q87.83 for Bardet-Biedl syndrome - BILLABLE CODE

  • Use Q87.84 for Laurence-Moon syndrome - BILLABLE CODE

  • Use Q87.85 for MED13L syndrome - BILLABLE CODE

  • Use Q87.86 for Kleefstra syndrome - BILLABLE CODE

  • Use Q87.89 for Other specified congenital malformation syndromes, not elsewhere classified - BILLABLE CODE

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Other congenital malformations
      (Q80-Q89)
      • Other specified congenital malformation syndromes affecting multiple systems
        (Q87)

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Use Additional Code

Use Additional Code
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
  • code(s) to identify all associated manifestations

Patient Education


Birth Defects

What are birth defects?

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works, or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. Others, like heart disease, are found using special tests. Birth defects can range from mild to severe. How a birth defect affects a child's life depends mostly on which organ or body part is involved and how severe the defect is.

What causes birth defects?

For some birth defects, researchers know the cause. But for many birth defects, the exact cause is unknown. Researchers think that most birth defects are caused by a complex mix of factors, which can include:

  • Genetics. One or more genes might have a change or mutation that prevents them from working properly. For example, this happens in Fragile X syndrome. With some defects, a gene or part of the gene might be missing.
  • Chromosomal problems. In some cases, a chromosome or part of a chromosome might be missing. This is what happens in Turner syndrome. In other cases, such as with Down syndrome, the child has an extra chromosome.
  • Exposures to medicines, chemicals, or other toxic substances. For example, alcohol misuse can cause fetal alcohol spectrum disorders.
  • Infections during pregnancy. For example, infection with Zika virus during pregnancy can cause a serious defect in the brain.
  • Lack of certain nutrients. Not getting enough folic acid before and during pregnancy is a key factor in causing neural tube defects.

Who is at risk of having a baby with birth defects?

Certain factors may increase the chances of having a baby with a birth defect, such as:

  • Smoking, drinking alcohol, or taking certain "street" drugs during pregnancy
  • Having certain medical conditions, such as obesity or uncontrolled diabetes, before and during pregnancy
  • Taking certain medicines
  • Having someone in your family with a birth defect. To learn more about your risk of having a baby with a birth defect, you can talk with a genetic counselor,
  • Being an older mother, typically over the age of 34 years

How are birth defects diagnosed?

Health care providers can diagnose some birth defects during pregnancy, using prenatal testing. That's why it important to get regular prenatal care.

Other birth defects may not be found until after the baby is born. Providers may find them through newborn screening. Some defects, such as club foot, are obvious right away. Other times, the health care provider may not discover a defect until later in life, when the child has symptoms.

What are the treatments for birth defects?

Children with birth defects often need special care and treatments. Because the symptoms and problems caused by birth defects vary, the treatments also vary. Possible treatments may include surgery, medicines, assistive devices, physical therapy, and speech therapy.

Often, children with birth defects need a variety of services and may need to see several specialists. The primary health care provider can coordinate the special care that the child needs.

Can birth defects be prevented?

Not all birth defects can be prevented. But there are things you can do before and during pregnancy to increase your chance of having a healthy baby:

  • Start prenatal care as soon as you think you might be pregnant, and see your health care provider regularly during pregnancy
  • Get 400 micrograms (mcg) of folic acid every day. If possible, you should start taking it at least one month before you get pregnant.
  • Don't drink alcohol, smoke, or use "street" drugs
  • Talk to your health care provider about any medicines you are taking or thinking about taking. This includes prescription and over-the-counter medicines, as well as dietary or herbal supplements.
  • Learn how to prevent infections during pregnancy
  • If you have any medical conditions, try to get them under control before you get pregnant

Centers for Disease Control and Prevention


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.