Congenital malformations of musculoskeletal system, not elsewhere classified (Q79) ICD-10-CM
The Q79 code range covers congenital malformations of musculoskeletal system, not elsewhere classified with 17 ICD-10-CM diagnosis codes. 14 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- congenital sternomastoid torticollis Q68.0
Codes in the Q79 Range 17 codes · 14 billable
- Q79 Congenital malformations of musculoskeletal system, not elsewhere classifiedNon-billable
- Q79.0 Congenital diaphragmatic hernia
- Q79.1 Other congenital malformations of diaphragm
- Q79.2 Exomphalos
- Q79.3 Gastroschisis
- Q79.4 Prune belly syndrome
- Q79.5 Other congenital malformations of abdominal wallNon-billable
- Q79.51 Congenital hernia of bladder
- Q79.59 Other congenital malformations of abdominal wall
- Q79.6 Ehlers-Danlos syndromesNon-billable
- Q79.60 Ehlers-Danlos syndrome, unspecified
- Q79.61 Classical Ehlers-Danlos syndrome
- Q79.62 Hypermobile Ehlers-Danlos syndrome
- Q79.63 Vascular Ehlers-Danlos syndrome
- Q79.69 Other Ehlers-Danlos syndromes
- Q79.8 Other congenital malformations of musculoskeletal system
- Q79.9 Congenital malformation of musculoskeletal system, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q79 range.
Arthrogryposis
Persistent flexure or contracture of a joint.
Ehlers-Danlos Syndrome
A heterogeneous group of autosomally inherited COLLAGEN DISEASES caused by defects in the synthesis or structure of FIBRILLAR COLLAGEN. There are numerous subtypes: classical, hypermobility, vascular, and others. Common clinical features include hyperextensible skin and joints, skin fragility and reduced wound healing capability.
Ehlers-Danlos Syndrome, Type IV
A subtype of Ehlers-Danlos syndrome (EDS) characterized by vascular pathologies, e.g., AORTIC DISSECTION in addition to common EDS findings, e.g., hyperextensible skin and joints, skin fragility and reduced wound healing capability. It is associated with mutations in collagen type III alpha 1 chain gene (COLLAGEN TYPE III).
Gastroschisis
A congenital defect with major fissure in the ABDOMINAL WALL lateral to, but not at, the UMBILICUS. This results in the extrusion of VISCERA. Unlike OMPHALOCELE, herniated structures in gastroschisis are not covered by a sac or PERITONEUM.
Hernias, Diaphragmatic, Congenital
Protrusion of abdominal structures into the THORAX as a result of embryologic defects in the DIAPHRAGM often present in the neonatal period. It can be isolated, syndromic, non-syndromic or be a part of chromosome abnormality. Associated pulmonary hypoplasia and PULMONARY HYPERTENSION can further complicate stabilization and surgical intervention.
Omphalocele
A congenital defect with major fissure in the ABDOMINAL WALL at the UMBILICUS resulting in the extrusion of VISCERA through the UMBILICUS. Unlike GASTROSCHISIS, omphalocele is covered with PERITONEUM but without overlying SKIN.
Poland Syndrome
A syndrome which is characterized by symbrachydactyly and aplasia of the sternal head of pectoralis major.
Prune Belly Syndrome
A syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. The syndrome derives its name from its characteristic distended abdomen with wrinkled skin.
About the Q79 Code Range
These conditions are present at birth and involve the diaphragm, abdominal wall, or musculoskeletal system. The category also includes Ehlers-Danlos syndromes.
Q79.0 identifies a diaphragmatic hernia, while Q79.1 identifies other diaphragm malformations. Separate subdivisions identify exomphalos, gastroschisis, and prune belly syndrome. Under Q79.5, the codes distinguish a bladder hernia from other abdominal wall malformations.
Q79.6 groups Ehlers-Danlos syndromes by named type, other type, or unspecified type. The final subdivisions identify other or unspecified musculoskeletal malformations.
Questions About This Page
How many billable codes are in the Q79 range?
Of the 17 codes in this range, 14 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q79 range classify?
The range classifies congenital malformations of musculoskeletal system, not elsewhere classified. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
