Other congenital malformations of limb(s) (Q74) ICD-10-CM
The Q74 code range covers other congenital malformations of limb(s) with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the Q74 Range 7 codes · 6 billable
- Q74 Other congenital malformations of limb(s)Non-billable
- Q74.0 Other congenital malformations of upper limb(s), including shoulder girdle
- Q74.1 Congenital malformation of knee
- Q74.2 Other congenital malformations of lower limb(s), including pelvic girdle
- Q74.3 Arthrogryposis multiplex congenita
- Q74.8 Other specified congenital malformations of limb(s)
- Q74.9 Unspecified congenital malformation of limb(s)
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q74 range.
Acrocallosal Syndrome
Autosomal recessive syndrome characterized by hypogenesis or agenesis of CORPUS CALLOSUM. Clinical features include MENTAL RETARDATION; CRANIOFACIAL ABNORMALITIES; digital malformations, and growth retardation.
Arachnodactyly
An abnormal bone development that is characterized by extra long and slender hands and fingers, such that the clenched thumb extends beyond the ulnar side of the hand. Arachnodactyly can include feet and toes. Arachnodactyly has been associated with several gene mutations and syndromes.
Arthrogryposis
Persistent flexure or contracture of a joint.
Dentinogenesis Imperfecta
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
Hepatorenal Syndrome
Functional KIDNEY FAILURE in patients with liver disease, usually LIVER CIRRHOSIS or portal hypertension (HYPERTENSION, PORTAL), and in the absence of intrinsic renal disease or kidney abnormality. It is characterized by intense renal vasculature constriction, reduced renal blood flow, OLIGURIA, and sodium retention.
Hypertelorism
Abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid.
Malignant Hyperthermia
Rapid and excessive rise of temperature accompanied by muscular rigidity following general anesthesia.
Pectus Carinatum
A developmental anomaly characterized by abnormal anterior protrusion of the STERNUM and adjacent COSTAL CARTILAGE.
Thrombocythemia, Essential
A clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.
Thrombocytosis
Increased numbers of platelets in the peripheral blood. (Dorland, 27th ed)
About the Q74 Code Range
The ICD-10 code Q74 covers a range of other congenital malformations of limbs, detailing specific malformations of upper limbs, knees, lower limbs, and unspecified limb defects. These codes are specifically used to classify diverse, often complex congenital conditions affecting bones, joints, and surrounding structures of the limbs and pelvic girdle.
The ICD-10 code for other congenital malformations of upper limb(s) (Q74.0) includes a broad spectrum of conditions such as bilateral humero-ulnar synostosis, congenital deformities of the scapula, radius, and ulna, polydactyly, and congenital dislocations of shoulder joints. Coders encountering terms like congenital trigger finger, Steel syndrome, or radial ray defect syndrome will find these appropriately categorized under Q74.0. Q74.1 is used for congenital malformations of the knee, covering conditions such as congenital genu varum or valgum, dislocation of patella, and congenital dysplasia of knee joints. For the lower limbs and pelvic girdle, Q74.2 applies to malformations like tibiofibular synostosis, agenesis of pelvic bones, congenital torsions, or macrodactyly of the toes. Q74.3 is dedicated to arthrogryposis multiplex congenita, a syndrome characterized by multiple joint contractures present at birth, also referenced by synonymous terms like distal arthrogryposis or inherited arthrogryposis. The section also includes Q74.8 for other specified congenital limb malformations, capturing rare syndromes and anomalies such as camptodactyly syndrome, multiple pterygium syndromes, or phocomelia. Lastly, Q74.9 addresses unspecified congenital malformations of limb(s) where precise diagnosis is unavailable but congenital anomalies exist. This classification helps medical coders link clinical terms and syndromic descriptors to the correct ICD-10 code for congenital limb malformations, facilitating accurate documentation and medical record clarity.
Questions About This Page
How many billable codes are in the Q74 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q74 range classify?
The range classifies other congenital malformations of limb(s). Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
