Other congenital malformations of skull and face bones (Q75) ICD-10-CM
The Q75 code range covers other congenital malformations of skull and face bones with 28 ICD-10-CM diagnosis codes. 22 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- congenital malformation of face NOS Q18
- congenital malformation syndromes classified to Q87
- dentofacial anomalies [including malocclusion] M26
- musculoskeletal deformities of head and face Q67.0 Q67.4
- skull defects associated with congenital anomalies of brain such as:
- anencephaly Q00.0
- encephalocele Q01
- hydrocephalus Q03
- microcephaly Q02
Codes in the Q75 Range 28 codes · 22 billable
- Q75 Other congenital malformations of skull and face bonesNon-billable
- Q75.0 CraniosynostosisNon-billable
- Q75.00 Craniosynostosis, unspecifiedNon-billable
- Q75.001 Craniosynostosis, unspecified type, unilateral Updated
- Q75.002 Craniosynostosis, unspecified type, bilateral Updated
- Q75.009 Craniosynostosis, unspecified Updated
- Q75.01 Sagittal craniosynostosis
- Q75.02 Coronal craniosynostosisNon-billable
- Q75.021 Coronal craniosynostosis, unilateral Updated
- Q75.022 Coronal craniosynostosis, bilateral Updated
- Q75.029 Coronal craniosynostosis, unspecified Updated
- Q75.03 Metopic craniosynostosis
- Q75.04 Lambdoid craniosynostosisNon-billable
- Q75.041 Lambdoid craniosynostosis, unilateral
- Q75.042 Lambdoid craniosynostosis, bilateral
- Q75.049 Lambdoid craniosynostosis, unspecified
- Q75.05 Multi-suture craniosynostosisNon-billable
- Q75.051 Cloverleaf skull
- Q75.052 Pansynostosis
- Q75.058 Other multi-suture craniosynostosis
- Q75.08 Other single-suture craniosynostosis
- Q75.1 Craniofacial dysostosis
- Q75.2 Hypertelorism
- Q75.3 Macrocephaly
- Q75.4 Mandibulofacial dysostosis
- Q75.5 Oculomandibular dysostosis
- Q75.8 Other specified congenital malformations of skull and face bones
- Q75.9 Congenital malformation of skull and face bones, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q75 range.
Acanthosis Nigricans
A circumscribed melanosis consisting of a brown-pigmented, velvety verrucosity or fine papillomatosis appearing in the axillae and other body folds. It occurs in association with endocrine disorders, underlying malignancy, administration of certain drugs, or as in inherited disorder.
Choanal Atresia
A congenital abnormality that is characterized by a blocked CHOANAE, the opening between the nose and the NASOPHARYNX. Blockage can be unilateral or bilateral; bony or membranous.
Craniofacial Dysostosis
Autosomal dominant CRANIOSYNOSTOSIS with shallow ORBITS; EXOPHTHALMOS; and maxillary hypoplasia.
Craniosynostoses
Premature closure of one or more CRANIAL SUTURES. It often results in plagiocephaly. Craniosynostoses that involve multiple sutures are sometimes associated with congenital syndromes such as ACROCEPHALOSYNDACTYLIA; and CRANIOFACIAL DYSOSTOSIS.
Exocrine Pancreatic Insufficiency
A malabsorption condition resulting from greater than 10% reduction in the secretion of pancreatic digestive enzymes (LIPASE; PROTEASES; and AMYLASE) by the EXOCRINE PANCREAS into the DUODENUM. This condition is often associated with CYSTIC FIBROSIS and with chronic PANCREATITIS.
Hypertelorism
Abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid.
Mandibulofacial Dysostosis
A hereditary disorder occurring in two forms: the complete form (Franceschetti's syndrome) is characterized by a slant of the palpebral fissures, COLOBOMA of the lower lid, MICROGNATHIA and hypoplasia of the ZYGOMATIC ARCHES, and CONGENITAL MICROTIA. It is transmitted as an autosomal trait. The incomplete form (Treacher Collins syndrome) is characterized by the same anomalies in less pronounced degree. It occurs sporadically, but an autosomal dominant mode of transmission is suspected. (Dorland, 27th ed)
Osteopetrosis
Excessive formation of dense trabecular bone leading to pathological fractures; OSTEITIS; SPLENOMEGALY with infarct; ANEMIA; and extramedullary hemopoiesis (HEMATOPOIESIS, EXTRAMEDULLARY).
Osteosclerosis
An abnormal hardening or increased density of bone tissue.
Plagiocephaly
The condition characterized by uneven or irregular shape of the head often in parallelogram shape with a flat spot on the back or one side of the head. It can either result from the premature CRANIAL SUTURE closure (CRANIOSYNOSTOSIS) or from external forces (NONSYNOSTOTIC PLAGIOCEPHALY).
Plagiocephaly, Nonsynostotic
A deformity of the SKULL that is not due to bone fusion (SYNOSTOSIS), such as craniosynostoses, and is characterized by an asymmetric skull and face. It is observed with an increased frequency in INFANTS after the adoption of supine sleeping recommendations to prevent SUDDEN INFANT DEATH SYNDROME.
Platybasia
A developmental deformity of the occipital bone and upper end of the cervical spine, in which the latter appears to have pushed the floor of the occipital bone upward. (Dorland, 27th ed)
About the Q75 Code Range
The Q75 ICD-10 codes classify various congenital malformations of the skull and face bones. These include different forms of craniosynostosis—premature fusion of skull sutures—as well as specific developmental abnormalities like craniofacial dysostosis and hypertelorism, aiding precise diagnosis and treatment.
This section covers conditions such as craniosynostosis (Q75.0), including types like sagittal (Q75.01), coronal (Q75.02), metopic (Q75.03), and lambdoid craniosynostosis (Q75.04). For example, the term acrorcephaly or simple craniosynostosis corresponds to specific codes like Q75.009, helping coders identify these unique variants. Craniofacial dysostosis (Q75.1) includes Crouzon syndrome among its synonyms, providing clarity for those seeking the exact ICD-10 code for these syndromes. The codes also include mandibulofacial dysostosis (Q75.4), known as Treacher Collins syndrome, and other conditions like hypertelorism(Q75.2) and macrocephaly (Q75.3). The grouping aids healthcare providers in documenting skull and facial bone abnormalities accurately, facilitating tailored medical care and insurance processing.
Questions About This Page
How many billable codes are in the Q75 range?
Of the 28 codes in this range, 22 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q75 range classify?
The range classifies other congenital malformations of skull and face bones. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
