Other congenital malformations of skull and face bones (Q75) ICD-10-CM
The Q75 code range covers other congenital malformations of skull and face bones with 28 ICD-10-CM diagnosis codes. 22 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- congenital malformation of face NOS Q18
- congenital malformation syndromes classified to Q87
- dentofacial anomalies [including malocclusion] M26
- musculoskeletal deformities of head and face Q67.0 Q67.4
- skull defects associated with congenital anomalies of brain such as:
- anencephaly Q00.0
- encephalocele Q01
- hydrocephalus Q03
- microcephaly Q02
Codes in the Q75 Range 28 codes · 22 billable
- Q75 Other congenital malformations of skull and face bonesNon-billable
- Q75.0 CraniosynostosisNon-billable
- Q75.00 Craniosynostosis, unspecifiedNon-billable
- Q75.001 Craniosynostosis, unspecified type, unilateral
- Q75.002 Craniosynostosis, unspecified type, bilateral
- Q75.009 Craniosynostosis, unspecified
- Q75.01 Sagittal craniosynostosis
- Q75.02 Coronal craniosynostosisNon-billable
- Q75.021 Coronal craniosynostosis, unilateral
- Q75.022 Coronal craniosynostosis, bilateral
- Q75.029 Coronal craniosynostosis, unspecified
- Q75.03 Metopic craniosynostosis
- Q75.04 Lambdoid craniosynostosisNon-billable
- Q75.041 Lambdoid craniosynostosis, unilateral
- Q75.042 Lambdoid craniosynostosis, bilateral
- Q75.049 Lambdoid craniosynostosis, unspecified
- Q75.05 Multi-suture craniosynostosisNon-billable
- Q75.051 Cloverleaf skull
- Q75.052 Pansynostosis
- Q75.058 Other multi-suture craniosynostosis
- Q75.08 Other single-suture craniosynostosis
- Q75.1 Craniofacial dysostosis
- Q75.2 Hypertelorism
- Q75.3 Macrocephaly
- Q75.4 Mandibulofacial dysostosis
- Q75.5 Oculomandibular dysostosis
- Q75.8 Other specified congenital malformations of skull and face bones
- Q75.9 Congenital malformation of skull and face bones, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q75 range.
Brachycephaly
Premature closing of both sides of the coronal sutures.
Craniofacial Dysostosis
Autosomal dominant CRANIOSYNOSTOSIS with shallow ORBITS; EXOPHTHALMOS; and maxillary hypoplasia.
Craniosynostoses
Premature closure of one or more CRANIAL SUTURES. It often results in plagiocephaly. Craniosynostoses that involve multiple sutures are sometimes associated with congenital syndromes such as ACROCEPHALOSYNDACTYLIA; and CRANIOFACIAL DYSOSTOSIS.
Hypertelorism
Abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid.
Mandibulofacial Dysostosis
A hereditary disorder occurring in two forms: the complete form (Franceschetti's syndrome) is characterized by a slant of the palpebral fissures, COLOBOMA of the lower lid, MICROGNATHIA and hypoplasia of the ZYGOMATIC ARCHES, and CONGENITAL MICROTIA. It is transmitted as an autosomal trait. The incomplete form (Treacher Collins syndrome) is characterized by the same anomalies in less pronounced degree. It occurs sporadically, but an autosomal dominant mode of transmission is suspected. (Dorland, 27th ed)
Megalencephaly
A congenital abnormality in which the occipitofrontal circumference is greater than two standard deviations above the mean for a given age. It is associated with HYDROCEPHALUS; SUBDURAL EFFUSION; ARACHNOID CYSTS; or is part of a genetic condition (e.g., ALEXANDER DISEASE; SOTOS SYNDROME).
Platybasia
A developmental deformity of the occipital bone and upper end of the cervical spine, in which the latter appears to have pushed the floor of the occipital bone upward. (Dorland, 27th ed)
Scaphocephaly
Premature fusion of the sagittal suture.
Trigonocephaly
Premature fusion of the metopic suture.
About the Q75 Code Range
These are malformations of the skull and face bones present from birth. They sit within the larger group of musculoskeletal malformations.
The Q75.0 branch separates craniosynostosis by named form or by single-suture versus multi-suture form. Some subdivisions also distinguish one-sided from two-sided forms. Other branches name distinct skull and face bone malformations. Q75.8 identifies other specified malformations, while Q75.9 leaves the malformation unspecified.
Questions About This Page
How many billable codes are in the Q75 range?
Of the 28 codes in this range, 22 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q75 range classify?
The range classifies other congenital malformations of skull and face bones. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
