2026 ICD-10-CM Diagnosis Code Q44.5Other congenital malformations of bile ducts

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q44

ICD-10-CM Q44.5
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q44.5 is a billable ICD-10-CM diagnosis code for other congenital malformations of bile ducts. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 441 through 443. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q44.5
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of bile ducts
Short Description
Other congenital malformations of bile ducts
Same as the full description in the CMS dataset.
Parent Code
Q44
Congenital malformations of gallbladder, bile ducts and liver

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ44Congenital malformations of gallbladder, bile ducts and liver
This CodeQ44.5Other congenital malformations of bile ducts

Present on Admission (POA)Billing

Q44.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Accessory hepatic duct
  • Agenesis of bile duct
  • Biliary anomalies
  • Bronchobiliary fistula
  • Caroli disease
  • Caroli syndrome
  • Choledochal cyst
  • Congenital abnormal long growth of bile duct
  • Congenital abnormality of liver and/or biliary tract
  • Congenital absence of bile duct
  • Congenital absence of cystic duct
  • Congenital absence of hepatic ducts
  • Congenital anomalous arrangement of pancreatobiliary duct
  • Congenital anomaly of bile ducts
  • Congenital anomaly of biliary tract
  • Congenital bronchobiliary fistula
  • Congenital choledochal cyst
  • Congenital cystic dilatation of common bile duct
  • Congenital developmental anomaly of cystic duct
  • Congenital dilatation of common bile duct
  • Congenital dilatation of lobar intrahepatic bile duct
  • Congenital dilatation of lobar intrahepatic bile duct with obstruction
  • Congenital disorder of gallbladder and biliary tract
  • Congenital diverticulum of bile duct
  • Congenital duplication of biliary duct
  • Congenital duplication of cystic duct
  • Congenital hepatic fibrosis
  • Congenital hyperplasia of intrahepatic bile duct
  • Congenital hypoplasia of bile duct
  • Congenital paucity of intrahepatic bile ducts
  • Congenital respiratory biliary fistula
  • Congenital tracheal fistula
  • Congenital tracheobiliary fistula
  • Cystic dilatation of common bile duct
  • Cystic dilation of intrahepatic duct
  • Fistula of bile duct
  • Intrahepatic biliary hypoplasia
  • Liver and/or biliary duplication
  • Pancreatic duct anomaly
  • Tracheobiliary fistula

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Accessory hepatic duct
  • Biliary duct duplication
  • Congenital malformation of bile duct NOS
  • Cystic duct duplication

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aberrant(congenital)
      • hepatic duct
    • Absence(of) (organ or part) (complete or partial)
      • bile, biliary duct, congenital
    • Accessory(congenital)
      • biliary duct or passage
    • Accessory(congenital)
      • cystic duct
    • Accessory(congenital)
      • hepatic ducts
    • Accessory(congenital)
      • liver
        • duct
    • Agenesis
      • bile duct or passage
    • Anomaly, anomalous(congenital) (unspecified type)
      • biliary duct or passage
    • Anomaly, anomalous(congenital) (unspecified type)
      • common duct
    • Anomaly, anomalous(congenital) (unspecified type)
      • cystic duct
    • Anomaly, anomalous(congenital) (unspecified type)
      • hepatic duct
    • Anomaly, anomalous(congenital) (unspecified type)
      • liver
        • duct
    • Deformity
      • bile duct (common) (congenital) (hepatic)
    • Deformity
      • biliary duct or passage (congenital)
    • Deformity
      • cystic duct (congenital)
    • Deformity
      • hepatic duct (congenital)
    • Dilatation
      • common duct (acquired)
        • congenital
    • Dilatation
      • cystic duct (acquired)
        • congenital
    • Distortion(s) (congenital)
      • bile duct or passage
    • Distortion(s) (congenital)
      • common duct
    • Distortion(s) (congenital)
      • cystic duct
    • Distortion(s) (congenital)
      • hepatic duct
    • Duplication, duplex
      • biliary duct (any)
    • Duplication, duplex
      • cystic duct
    • Elongated, elongation(congenital)
      • common bile duct
    • Elongated, elongation(congenital)
      • cystic duct
    • Fistula(cutaneous)
      • cystic duct
        • congenital
    • Hypoplasia, hypoplastic
      • biliary duct or passage
    • Malformation(congenital)
      • bile duct
    • Malposition
      • congenital
        • biliary duct or passage
    • Malposition
      • congenital
        • hepatic duct
    • Short, shortening, shortness
      • common bile duct, congenital
    • Short, shortening, shortness
      • cystic duct, congenital
    • Torsion
      • bile duct (common) (hepatic)
        • congenital

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Choledochal Cyst

    a congenital anatomic malformation of a bile duct, including cystic dilatation of the extrahepatic bile duct or the large intrahepatic bile duct. classification is based on the site and type of dilatation. type i is most common.

  • Caroli Disease

    congenital cystic dilatation of the intrahepatic bile ducts (bile ducts, intrahepatic). it consists of 2 types: simple caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (hypertension, portal). benign renal tubular ectasia is associated with both types of caroli disease.

  • Choledochal Cyst

    cystic dilatation of the hepatic duct or bile duct.

  • Caroli Disease

    a rare congenital disorder characterized by cystic dilatation of the intrahepatic bile ducts. it is associated with cholangitis and the formation of stones.

  • Congenital Hepatic Fibrosis

    a congenital disorder usually inherited in an autosomal recessive pattern. it affects the hepatobiliary system and the kidneys. it is characterized by liver fibrosis, portal hypertension, and renal cysts.

Patient EducationClinical

Bile Duct Diseases

Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q44.5 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
751.60 Biliary & liver anom NOS
Approximate The match is approximate rather than exact.
ICD-9-CM
751.69 Biliary & liver anom NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q44.5Overview

Is Q44.5 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of bile ducts on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q44.5 group to?

When other congenital malformations of bile ducts is the principal diagnosis on an inpatient stay, it groups to MS-DRG 441, 442, 443, with relative weights from 0.6997 to 1.7947 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q44.5 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of bile ducts on inpatient claims.

What is the ICD-9 equivalent of Q44.5?

Under the General Equivalence Mappings, other congenital malformations of bile ducts converts to ICD-9-CM 751.60 (biliary & liver anom NOS) and 751.69 (biliary & liver anom NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.