Other congenital malformations of digestive system (Q45)

The ICD-10 code section Q45 covers other congenital malformations of the digestive system, focusing on rare birth defects affecting digestive organs such as the pancreas and surrounding structures.

This group includes codes for specific conditions like Q45.0 (agenesis, aplasia, and hypoplasia of the pancreas), which refers to incomplete or absent pancreas development often called pancreatic agenesis or congenital hypoplasia of the pancreas. Q45.1 addresses annular pancreas, a congenital condition causing duodenal obstruction due to pancreatic tissue encircling the duodenum. Q45.2 identifies congenital pancreatic cysts, including polycystic disease of the pancreas. Other anomalies, such as pancreatic duct irregularities and accessory pancreatic tissue, fall under Q45.3. The code Q45.8 covers various specified digestive system malformations like mesenteric cysts and ectopic pancreatic tissue. Lastly, Q45.9 is used for unspecified congenital malformations of the digestive tract. These codes help healthcare professionals accurately classify and document unusual congenital digestive system conditions encountered in clinical practice.

Instructional Notations

Type 2 Excludes

A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

  • congenital diaphragmatic hernia Q79.0
  • congenital hiatus hernia Q40.1

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Mesenteric Cyst

A rare intra-abdominal tumor in the MESENTERY. Mesenteric cysts are usually benign and can be very large fluid-filled (2000 mL) lesions.

Pancreas Divisum

Anatomic variants in PANCREATIC DUCTS characterized by failure of fusion of the ventral and dorsal endodermal buds. Pancreas divisum results in inadequate or no communication between dorsal and ventral ducts. While most cases are asymptomatic, it may be associated with recurrent PANCREATITIS.