Q44.6 - Cystic disease of liver

Version 2023

ICD-10:	Q44.6
Short Description:	Cystic disease of liver
Long Description:	Cystic disease of liver
Status:	Valid for Submission
Version:	ICD-10-CM 2023
Code Classification:	Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99) Other congenital malformations of the digestive system (Q38-Q45) Congenital malform of gallbladder, bile ducts and liver (Q44)

1. Approximate Synonyms
2. Clinical Information
3. Tabular List of Diseases and Injuries
4. Index to Diseases and Injuries References
5. Diagnostic Related Groups - MS-DRG Mapping
6. Present on Admission (POA)
7. Convert to ICD-9 Code
8. Patient Education
9. Related Codes Browser
10. Code History

Q44.6 is a billable ICD-10 code used to specify a medical diagnosis of cystic disease of liver. The code is valid during the fiscal year 2023 from October 01, 2022 through September 30, 2023 for the submission of HIPAA-covered transactions. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

Autosomal dominant polycystic liver disease
Congenital cystic disease of liver
Congenital hepatic fibrosis
Isolated polycystic liver disease
Liver cyst
Liver cyst
Liver cyst

Clinical Information

Congenital Hepatic Fibrosis-. a congenital disorder usually inherited in an autosomal recessive pattern. it affects the hepatobiliary system and the kidneys. it is characterized by liver fibrosis, portal hypertension, and renal cysts.

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to this diagnosis code:

Inclusion Terms

Fibrocystic disease of liver

Index to Diseases and Injuries References

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for this diagnosis code are found in the injuries and diseases index:

- Cyst (colloid) (mucous) (simple) (retention)
- - congenital NEC - Q89.8
  - - liver - Q44.6
- - liver (idiopathic) (simple) - K76.89
  - - congenital - Q44.6

- Cystic - See Also: condition;
- - liver, congenital - Q44.6

- Degeneration, degenerative
- - liver (diffuse) NEC - K76.89
  - - cystic - K76.89
    - - congenital - Q44.6

- Disease, diseased - See Also: Syndrome;
- - cystic
  - - liver, congenital - Q44.6
- - liver (chronic) (organic) - K76.9
  - - cystic, congenital - Q44.6
  - - fibrocystic (congenital) - Q44.6
  - - polycystic (congenital) - Q44.6
- - polycystic
  - - liver or hepatic - Q44.6

- Fibrocystic
- - disease - See Also: Fibrosis, cystic;
  - - liver - Q44.6

- Polycystic (disease)
- - liver - Q44.6

Diagnostic Related Groups - MS-DRG Mapping

The is diagnosis code is grouped in the following groups for version MS-DRG V40.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC). applicable from 10/01/2022 through 09/30/2023.

MS-DRG	MS-DRG Title	MCD	Relative Weight
441	DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITH MCC	07	1.8948
442	DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITH CC	07	0.946
443	DISORDERS OF LIVER EXCEPT MALIGNANCY, CIRRHOSIS OR ALCOHOLIC HEPATITIS WITHOUT CC/MCC	07	0.6519

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Present on Admission (POA)

Q44.6 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA Indicator Code	POA Reason for Code	CMS will pay the CC/MCC DRG?
Y	Diagnosis was present at time of inpatient admission.	YES
N	Diagnosis was not present at time of inpatient admission.	NO
U	Documentation insufficient to determine if the condition was present at the time of inpatient admission.	NO
W	Clinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.	YES
1	Unreported/Not used - Exempt from POA reporting.	NO

Convert to ICD-9 Code

Source ICD-10 Code		Target ICD-9 Code
Q44.6		751.62 - Cong cystic liver dis

Patient Education

Birth Defects

What are birth defects?

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works, or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. Others, like heart disease, are found using special tests. Birth defects can range from mild to severe. How a birth defect affects a child's life depends mostly on which organ or body part is involved and how severe the defect is.

What causes birth defects?

For some birth defects, researchers know the cause. But for many birth defects, the exact cause is unknown. Researchers think that most birth defects are caused by a complex mix of factors, which can include:

Genetics. One or more genes might have a change or mutation that prevents them from working properly. For example, this happens in Fragile X syndrome. With some defects, a gene or part of the gene might be missing.
Chromosomal problems. In some cases, a chromosome or part of a chromosome might be missing. This is what happens in Turner syndrome. In other cases, such as with Down syndrome, the child has an extra chromosome.
Exposures to medicines, chemicals, or other toxic substances. For example, alcohol misuse can cause fetal alcohol spectrum disorders.
Infections during pregnancy. For example, infection with Zika virus during pregnancy can cause a serious defect in the brain.
Lack of certain nutrients. Not getting enough folic acid before and during pregnancy is a key factor in causing neural tube defects.

Who is at risk of having a baby with birth defects?

Certain factors may might increase the chances of having a baby with a birth defect, such as:

Smoking, drinking alcohol, or taking certain "street" drugs during pregnancy
Having certain medical conditions, such as obesity or uncontrolled diabetes, before and during pregnancy
Taking certain medicines
Having someone in your family with a birth defect. To learn more about your risk of having a baby with a birth defect, you can talk with a genetic counselor,
Being an older mother, typically over the age of 34 years

How are birth defects diagnosed?

Health care providers can diagnose some birth defects during pregnancy, using prenatal testing. That's why it important to get regular prenatal care.

Other birth defects may not be found until after the baby is born. Providers may find them through newborn screening. Some defects, such as club foot, are obvious right away. Other times, the health care provider may not discover a defect until later in life, when the child has symptoms.

What are the treatments for birth defects?

Children with birth defects often need special care and treatments. Because the symptoms and problems caused by birth defects vary, the treatments also vary. Possible treatments may include surgery, medicines, assistive devices, physical therapy, and speech therapy.

Often, children with birth defects need a variety of services and may need to see several specialists. The primary health care provider can coordinate the special care that the child needs.

Can birth defects be prevented?

Not all birth defects can be prevented. But there are things you can do before and during pregnancy to increase your chance of having a healthy baby:

Start prenatal care as soon as you think you might be pregnant, and see your health care provider regularly during pregnancy
Get 400 micrograms (mcg) of folic acid every day. If possible, you should start taking it at least one month before you get pregnant.
Don't drink alcohol, smoke, or use "street" drugs
Talk to your health care provider about any medicines you are taking or thinking about taking. This includes prescription and over-the-counter medicines, as well as dietary or herbal supplements.
Learn how to prevent infections during pregnancy
If you have any medical conditions, try to get them under control before you get pregnant

Centers for Disease Control and Prevention

[Learn More in MedlinePlus]

Liver Diseases

Your liver is the largest organ inside your body. It helps your body digest food, store energy, and remove poisons.

There are many kinds of liver diseases:

Diseases caused by viruses, such as hepatitis A, hepatitis B, and hepatitis C
Diseases caused by drugs, poisons, or too much alcohol. Examples include fatty liver disease and cirrhosis.
Liver cancer
Inherited diseases, such as hemochromatosis and Wilson disease

Symptoms of liver disease can vary, but they often include swelling of the abdomen and legs, bruising easily, changes in the color of your stool and urine, and jaundice, or yellowing of the skin and eyes. Sometimes there are no symptoms. Tests such as imaging tests and liver function tests can check for liver damage and help to diagnose liver diseases.