Other congenital malformations of intestine (Q43) ICD-10-CM
The Q43 code range covers other congenital malformations of intestine with 11 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the Q43 Range 11 codes · 10 billable
- Q43 Other congenital malformations of intestineNon-billable
- Q43.0 Meckel's diverticulum (displaced) (hypertrophic)
- Q43.1 Hirschsprung's disease
- Q43.2 Other congenital functional disorders of colon
- Q43.3 Congenital malformations of intestinal fixation
- Q43.4 Duplication of intestine
- Q43.5 Ectopic anus
- Q43.6 Congenital fistula of rectum and anus
- Q43.7 Persistent cloaca
- Q43.8 Other specified congenital malformations of intestine
- Q43.9 Congenital malformation of intestine, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q43 range.
Blind Loop Syndrome
A malabsorption syndrome that is associated with a blind loop in the upper SMALL INTESTINE that is characterized by the lack of peristaltic movement, stasis of INTESTINAL CONTENTS, and the overgrowth of BACTERIA. Such bacterial overgrowth interferes with BILE SALTS action, FATTY ACIDS processing, MICROVILLI integrity, and the ABSORPTION of nutrients such as VITAMIN B12 and FOLIC ACID.
Intestinal Volvulus
A twisting in the intestine (INTESTINES) that can cause INTESTINAL OBSTRUCTION.
Rectal Prolapse
Protrusion of the rectal mucous membrane through the anus. There are various degrees: incomplete with no displacement of the anal sphincter muscle; complete with displacement of the anal sphincter muscle; complete with no displacement of the anal sphincter muscle but with herniation of the bowel; and internal complete with rectosigmoid or upper rectum intussusception into the lower rectum.
Short Bowel Syndrome
A malabsorption syndrome resulting from extensive operative resection of the SMALL INTESTINE, the absorptive region of the GASTROINTESTINAL TRACT.
Waardenburg Syndrome
Rare, autosomal dominant disease with variable penetrance and several known clinical types. Characteristics may include depigmentation of the hair and skin, congenital deafness, heterochromia iridis, medial eyebrow hyperplasia, hypertrophy of the nasal root, and especially dystopia canthorum. The underlying cause may be defective development of the neural crest (neurocristopathy). Waardenburg's syndrome may be closely related to piebaldism. Klein-Waardenburg Syndrome refers to a disorder that also includes upper limb abnormalities.
About the Q43 Code Range
The ICD-10 code Q43 covers various congenital malformations of the intestine, including specific anomalies like Meckel's diverticulum (Q43.0), Hirschsprung's disease (Q43.1), and other structural or functional intestinal disorders present from birth.
These codes are used to classify unique conditions involving abnormal development of the intestine that infants are born with. For example, Q43.0 includes displaced or hypertrophic Meckel's diverticulum, also known as intra-abdominal vitelline remnants or bleeding Meckel's diverticulitis. Q43.1 identifies Hirschsprung's disease, which is also called congenital aganglionic megacolon or primary megacolon, characterized by missing nerve cells in parts of the colon. Other codes like Q43.3 address congenital malformations of intestinal fixation such as malrotation or volvulus, while Q43.4 covers duplications of the intestines. Less common anomalies like ectopic anus (Q43.5) and persistent cloaca (Q43.7) are also included. This ICD-10 code range allows precise documentation for a wide spectrum of congenital intestinal malformations, aiding accurate diagnosis and treatment planning.
Questions About This Page
How many billable codes are in the Q43 range?
Of the 11 codes in this range, 10 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q43 range classify?
The range classifies other congenital malformations of intestine. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
