Other congenital malformations of intestine (Q43) ICD-10-CM
The Q43 code range covers other congenital malformations of intestine with 11 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the Q43 Range 11 codes · 10 billable
- Q43 Other congenital malformations of intestineNon-billable
- Q43.0 Meckel's diverticulum (displaced) (hypertrophic)
- Q43.1 Hirschsprung's disease
- Q43.2 Other congenital functional disorders of colon
- Q43.3 Congenital malformations of intestinal fixation
- Q43.4 Duplication of intestine
- Q43.5 Ectopic anus
- Q43.6 Congenital fistula of rectum and anus
- Q43.7 Persistent cloaca
- Q43.8 Other specified congenital malformations of intestine
- Q43.9 Congenital malformation of intestine, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q43 range.
Chilaiditi Syndrome
Interposition of a portion of the colon (e.g., SIGMOID COLON) between the liver and the diaphragm. It is associated with abdominal pain, vomiting, constipation, anorexia and volvulus. Chilaiditi anomaly refers to asymptomatic interposition.
Hirschsprung Disease
Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON.
Meckel Diverticulum
A congenital abnormality characterized by the outpouching or sac formation in the ILEUM. It is a remnant of the embryonic YOLK SAC in which the VITELLINE DUCT failed to close.
Persistent Cloaca
A congenital abnormality in which the rectum, vagina, and urethra fuse and form a common channel.
About the Q43 Code Range
These conditions are differences in the intestine present at birth. They sit within the broader group of digestive system malformations.
Q43.0 and Q43.1 identify named conditions. Other subdivisions distinguish colon function, how the intestine is fixed in place, and intestinal duplication. They also separate conditions involving the anus, rectum, or cloaca. The final subdivisions cover other specified intestinal malformations and those left unspecified.
Questions About This Page
How many billable codes are in the Q43 range?
Of the 11 codes in this range, 10 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q43 range classify?
The range classifies other congenital malformations of intestine. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
