Q44.3 is a billable ICD-10 code used to specify a medical diagnosis of congenital stenosis and stricture of bile ducts. The code is valid during the fiscal year 2023 from October 01, 2022 through September 30, 2023 for the submission of HIPAA-covered transactions. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Arthrogryposis with renal dysfunction and cholestasis syndrome
- Biliary stricture
- Cholestasis in newborn
- Congenital developmental anomaly of cystic duct
- Congenital kink of cystic duct
- Congenital obstruction of bile duct
- Congenital stricture of bile duct
- Congenital stricture of common bile duct
- Inherited disorder of bilirubin metabolism
- Neurogenic arthrogryposis multiplex congenita
- Perinatal jaundice due to congenital obstruction of bile duct
- Stenosis of bile duct
- Stenosis of bile duct
- Stenosis of cystic duct
- Stricture of bile duct
- Alagille Syndrome-. a multisystem disorder that is characterized by aplasia of intrahepatic bile ducts (bile ducts, intrahepatic), and malformations in the cardiovascular system, the eyes, the vertebral column, and the facies. major clinical features include jaundice, and congenital heart disease with peripheral pulmonary stenosis. alagille syndrome may result from heterogeneous gene mutations, including mutations in jag1 on chromosome 20 (type 1) and notch2 on chromosome 1 (type 2).
- Cholestasis-. impairment of bile flow due to obstruction in small bile ducts (intrahepatic cholestasis) or obstruction in large bile ducts (extrahepatic cholestasis).
- Cholestasis, Extrahepatic-. impairment of bile flow in the large bile ducts by mechanical obstruction or stricture due to benign or malignant processes.
- Cholestasis, Intrahepatic-. impairment of bile flow due to injury to the hepatocytes; bile canaliculi; or the intrahepatic bile ducts (bile ducts, intrahepatic).
- Bile Ducts-. the channels that collect and transport the bile secretion from the bile canaliculi, the smallest branch of the biliary tract in the liver, through the bile ductules, the bile ducts out the liver, and to the gallbladder for storage.
Index to Diseases and Injuries References
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for this diagnosis code are found in the injuries and diseases index:
- - Obstruction, obstructed, obstructive
- - Stenosis, stenotic (cicatricial) - See Also: Stricture;
Present on Admission (POA)
Convert to ICD-9 Code
|Source ICD-10 Code||Target ICD-9 Code|
|Q44.3||751.61 - Biliary atresia|
|Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.|
Bile Duct Diseases
Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.
Different diseases can block the bile ducts and cause a problem with the flow of bile:
- Gallstones, which can increase pressure in the gallbladder and cause a gallbladder attack. The pain usually lasts from one to several hours.
- Birth defects, such as biliary atresia. It is the most common reason for liver transplants in children in the United States.
- Inflammation, which can cause scarring. Over time, this can lead to liver failure.
NIH: National Institute of Diabetes and Digestive and Kidney Diseases
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What are birth defects?
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
A birth defect may affect how the body looks, works, or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. Others, like heart disease, are found using special tests. Birth defects can range from mild to severe. How a birth defect affects a child's life depends mostly on which organ or body part is involved and how severe the defect is.
What causes birth defects?
For some birth defects, researchers know the cause. But for many birth defects, the exact cause is unknown. Researchers think that most birth defects are caused by a complex mix of factors, which can include:
- Genetics. One or more genes might have a change or mutation that prevents them from working properly. For example, this happens in Fragile X syndrome. With some defects, a gene or part of the gene might be missing.
- Chromosomal problems. In some cases, a chromosome or part of a chromosome might be missing. This is what happens in Turner syndrome. In other cases, such as with Down syndrome, the child has an extra chromosome.
- Exposures to medicines, chemicals, or other toxic substances. For example, alcohol misuse can cause fetal alcohol spectrum disorders.
- Infections during pregnancy. For example, infection with Zika virus during pregnancy can cause a serious defect in the brain.
- Lack of certain nutrients. Not getting enough folic acid before and during pregnancy is a key factor in causing neural tube defects.
Who is at risk of having a baby with birth defects?
Certain factors may might increase the chances of having a baby with a birth defect, such as:
- Smoking, drinking alcohol, or taking certain "street" drugs during pregnancy
- Having certain medical conditions, such as obesity or uncontrolled diabetes, before and during pregnancy
- Taking certain medicines
- Having someone in your family with a birth defect. To learn more about your risk of having a baby with a birth defect, you can talk with a genetic counselor,
- Being an older mother, typically over the age of 34 years
How are birth defects diagnosed?
Health care providers can diagnose some birth defects during pregnancy, using prenatal testing. That's why it important to get regular prenatal care.
Other birth defects may not be found until after the baby is born. Providers may find them through newborn screening. Some defects, such as club foot, are obvious right away. Other times, the health care provider may not discover a defect until later in life, when the child has symptoms.
What are the treatments for birth defects?
Children with birth defects often need special care and treatments. Because the symptoms and problems caused by birth defects vary, the treatments also vary. Possible treatments may include surgery, medicines, assistive devices, physical therapy, and speech therapy.
Often, children with birth defects need a variety of services and may need to see several specialists. The primary health care provider can coordinate the special care that the child needs.
Can birth defects be prevented?
Not all birth defects can be prevented. But there are things you can do before and during pregnancy to increase your chance of having a healthy baby:
- Start prenatal care as soon as you think you might be pregnant, and see your health care provider regularly during pregnancy
- Get 400 micrograms (mcg) of folic acid every day. If possible, you should start taking it at least one month before you get pregnant.
- Don't drink alcohol, smoke, or use "street" drugs
- Talk to your health care provider about any medicines you are taking or thinking about taking. This includes prescription and over-the-counter medicines, as well as dietary or herbal supplements.
- Learn how to prevent infections during pregnancy
- If you have any medical conditions, try to get them under control before you get pregnant
Centers for Disease Control and Prevention
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- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
- FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
- FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)