Congenital absence, atresia and stenosis of large intestine (Q42) ICD-10-CM
The Q42 code range covers congenital absence, atresia and stenosis of large intestine with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- congenital obstruction, occlusion and stricture of large intestine
Codes in the Q42 Range 7 codes · 6 billable
- Q42 Congenital absence, atresia and stenosis of large intestineNon-billable
- Q42.0 Congenital absence, atresia and stenosis of rectum with fistula
- Q42.1 Congenital absence, atresia and stenosis of rectum without fistula
- Q42.2 Congenital absence, atresia and stenosis of anus with fistula
- Q42.3 Congenital absence, atresia and stenosis of anus without fistula
- Q42.8 Congenital absence, atresia and stenosis of other parts of large intestine
- Q42.9 Congenital absence, atresia and stenosis of large intestine, part unspecified
About the Q42 Code Range
The ICD-10 code Q42 covers congenital conditions involving the absence, atresia (closure), or narrowing (stenosis) of the large intestine. These codes are specifically used to document birth defects affecting various parts of the large bowel, including the rectum and anus, with or without associated fistulas.
This group includes detailed subcodes such as Q42.0 for congenital absence or narrowing of the rectum with fistula, and Q42.1 for similar conditions without fistula. Codes Q42.2 and Q42.3 describe congenital anomalies of the anus, either with or without fistula. Other parts of the large intestine, including the appendix, are categorized under Q42.8. When the specific part is not specified, Q42.9 applies. These codes help medical coders accurately capture diagnoses such as congenital rectal or anal stenosis, anorectal stricture, anal atresia, and other large intestine malformations, assisting in clear clinical communication and appropriate treatment planning. Searches for the ICD-10 code for congenital absence or atresia of the large intestine will reference these exact codes to identify precise defects present at birth.
Questions About This Page
How many billable codes are in the Q42 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q42 range classify?
The range classifies congenital absence, atresia and stenosis of large intestine. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
