Congenital absence, atresia and stenosis of large intestine (Q42) ICD-10-CM
The Q42 code range covers congenital absence, atresia and stenosis of large intestine with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- congenital obstruction, occlusion and stricture of large intestine
Codes in the Q42 Range 7 codes · 6 billable
- Q42 Congenital absence, atresia and stenosis of large intestineNon-billable
- Q42.0 Congenital absence, atresia and stenosis of rectum with fistula
- Q42.1 Congenital absence, atresia and stenosis of rectum without fistula
- Q42.2 Congenital absence, atresia and stenosis of anus with fistula
- Q42.3 Congenital absence, atresia and stenosis of anus without fistula
- Q42.8 Congenital absence, atresia and stenosis of other parts of large intestine
- Q42.9 Congenital absence, atresia and stenosis of large intestine, part unspecified
About the Q42 Code Range
These conditions are present at birth: part of the large intestine is absent, closed or narrowed.
Q42 separates conditions by the affected part. Rectal codes Q42.0 and Q42.1 distinguish whether a fistula, an abnormal connection, is present. Anal codes Q42.2 and Q42.3 make the same distinction. Q42.8 identifies other parts of the large intestine; Q42.9 leaves the part unspecified.
Questions About This Page
How many billable codes are in the Q42 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q42 range classify?
The range classifies congenital absence, atresia and stenosis of large intestine. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
