Other congenital malformations of upper alimentary tract (Q40) ICD-10-CM
The Q40 code range covers other congenital malformations of upper alimentary tract with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the Q40 Range 7 codes · 6 billable
- Q40 Other congenital malformations of upper alimentary tractNon-billable
- Q40.0 Congenital hypertrophic pyloric stenosis
- Q40.1 Congenital hiatus hernia
- Q40.2 Other specified congenital malformations of stomach
- Q40.3 Congenital malformation of stomach, unspecified
- Q40.8 Other specified congenital malformations of upper alimentary tract
- Q40.9 Congenital malformation of upper alimentary tract, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q40 range.
Hypertrophy
General increase in bulk of a part or organ due to CELL ENLARGEMENT and accumulation of FLUIDS AND SECRETIONS, not due to tumor formation, nor to an increase in the number of cells (HYPERPLASIA).
Pyloric Stenosis
Narrowing of the pyloric canal with varied etiology. A common form is due to muscle hypertrophy (PYLORIC STENOSIS, HYPERTROPHIC) seen in infants.
Pyloric Stenosis, Hypertrophic
Narrowing of the pyloric canal due to HYPERTROPHY of the surrounding circular muscle. It is usually seen in infants or young children.
About the Q40 Code Range
The ICD-10 code Q40 group is used to identify various congenital malformations of the upper alimentary tract, including specific conditions affecting the stomach and pylorus present from birth.
This section covers detailed conditions like Q40.0 for congenital hypertrophic pyloric stenosis, also known by synonyms such as congenital pyloric spasm and pyloric obstruction. This condition involves abnormal narrowing that affects stomach emptying. Q40.1 codes for congenital hiatus hernia (also called congenital diaphragmatic hernia), involving structural defects where part of the stomach pushes into the chest. Codes Q40.2 and Q40.3 cover other specified or unspecified congenital stomach malformations, including rare anomalies like gastric volvulus, agenesis, or ectopic gastric tissue, mentioned in synonyms such as gastric atresia and congenital pyloric membrane. Finally, Q40.8 and Q40.9 address other or unspecified congenital defects of the upper digestive tract, including tonsil asymmetry or congenital absence of stomach muscle. These codes are essential for precisely documenting congenital anatomical abnormalities in the upper digestive system for medical care and billing.
Questions About This Page
How many billable codes are in the Q40 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q40 range classify?
The range classifies other congenital malformations of upper alimentary tract. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
