Congenital malformations of esophagus (Q39)

ICD-10 code Q39 covers congenital malformations of the esophagus, which are structural abnormalities present from birth affecting the esophagus. These codes specify different types of esophageal defects such as atresia, fistula, stenosis, webs, and dilatations.

The ICD-10 codes from Q39.0 to Q39.9 are used to identify specific congenital esophageal conditions. For example, Q39.0 refers to atresia of the esophagus without fistula, often called "long gap esophageal atresia." Q39.1 describes atresia with tracheoesophageal fistula, known by synonyms like "congenital esophageal fistula" or "tracheoesophageal fistula." Q39.2 captures congenital tracheoesophageal fistula without atresia, often termed “H-type fistula.” Other codes include Q39.3 for congenital esophageal stenosis or strictures, Q39.4 for esophageal web, and Q39.5 for congenital dilatation also known as achalasia of the esophagus. Less commonly, codes like Q39.6 for congenital diverticulum and Q39.8 for other rare malformations cover a range of congenital anomalies. Q39.9 is used when the malformation is unspecified. These codes help medical coders and clinicians accurately report and classify congenital esophageal defects for diagnosis and treatment planning.

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Tracheoesophageal Fistula

Abnormal passage between the ESOPHAGUS and the TRACHEA, acquired or congenital, often associated with ESOPHAGEAL ATRESIA.