2027 ICD-10-CM Diagnosis Code Q43.8Other specified congenital malformations of intestine

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q43

ICD-10-CM Q43.8
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q43.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of intestine. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 393 through 395. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 21 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q43.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of intestine
Short Description
Other specified congenital malformations of intestine
Same as the full description in the CMS dataset.
Parent Code
Q43
Other congenital malformations of intestine

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ43Other congenital malformations of intestine
This CodeQ43.8Other specified congenital malformations of intestine

Present on Admission (POA)Billing

Q43.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations of the digestive system (Q38-Q45).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Anal fissure
  • Anorectal fissure
  • Aphalangy, hemivertebra, urogenital, intestinal dysgenesis syndrome
  • Asplenia
  • Band of Ladd
  • Blind loop syndrome
  • Cecum in left sided position
  • Cloacal disease
  • Congenital absence of spleen
  • Congenital anal fissure
  • Congenital anomaly of appendix
  • Congenital blind loop syndrome
  • Congenital diaphragmatic hernia
  • Congenital dilatation of intestinal tract
  • Congenital dilatation of urinary bladder
  • Congenital diverticulitis of small intestine
  • Congenital diverticulosis
  • Congenital diverticulosis of small intestine
  • Congenital diverticulum of colon
  • Congenital diverticulum of duodenum
  • Congenital diverticulum of intestinal tract
  • Congenital diverticulum of large intestine
  • Congenital diverticulum of small intestine
  • Congenital dysmotility of small intestine
  • Congenital enterocyte heparan sulfate deficiency
  • Congenital fistula of intestinal tract
  • Congenital fistula of rectum
  • Congenital functional disorders of the colon
  • Congenital functional disorders of the small intestine
  • Congenital gastric heterotopia of duodenum
  • Congenital hypoganglionosis of large intestine
  • Congenital hypoplasia of intestinal tract
  • Congenital interstitial cell of Cajal hyperplasia with neuronal intestinal dysplasia
  • Congenital malposition of intestinal tract
  • Congenital malrotation of duodenum
  • Congenital megaduodenum
  • Congenital microvillous atrophy
  • Congenital neurogenic ileus syndrome
  • Congenital prolapsed rectum
  • Congenital rectal fissure
  • Congenital rectocloacal fistula
  • Congenital redundant colon
  • Congenital redundant rectal mucosa
  • Congenital short bowel syndrome
  • Congenital small anus
  • Congenital volvulus
  • Diaphragmatic hernia, short bowel, asplenia syndrome
  • Distension of urinary bladder
  • Diverticulum of duodenum
  • Diverticulum of large intestine
  • Dolichocolon
  • Duodenal web
  • Ectopic gastric tissue
  • Ectopic intestinal mucosa
  • Enterogenous cyst
  • Familial absence of villi
  • Gastroduodenal disorder
  • Generalized congenital intestinal dysmotility
  • High anorectal malformation
  • Intermediate anorectal malformation
  • Intestinal epithelial dysplasia
  • Intestinal volvulus
  • Low anorectal malformation
  • Malrotation of small intestine
  • Malrotation of the intestine type IIA
  • Megacystis, microcolon, hypoperistalsis syndrome
  • Megaduodenum
  • Megaloappendix
  • Microcolon
  • Motility disorder of small intestine
  • Neuronal intestinal dysplasia
  • Rectal prolapse
  • Short bowel syndrome
  • Situs inversus abdominalis
  • Situs inversus viscerum
  • Structural abnormality of Auerbach plexus
  • Structural abnormality of Meissner plexus
  • Structural abnormality of small intestinal villus
  • Tortuous colon
  • Transposition of appendix
  • Transposition of cecum
  • Transposition of colon
  • Transposition of intestine

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q43.8: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital blind loop syndrome
  • Congenital diverticulitis, colon
  • Congenital diverticulum, intestine
  • Dolichocolon
  • Megaloappendix
  • Megaloduodenum
  • Microcolon
  • Transposition of appendix
  • Transposition of colon
  • Transposition of intestine

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q43.8, its category, or a range that includes it.

Excludes1 2

These codes carry an Excludes1 note naming Q43.8: they are not reported together with it, unless the two conditions are unrelated.

  • K57 Diverticular disease of intestine
    congenital diverticulum of intestine (Q43.8)
  • K90.2 Blind loop syndrome, not elsewhere classified
    congenital blind loop syndrome (Q43.8)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q43.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
751.5 Intestinal anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q43.8Overview

What is the ICD-10 code for other specified congenital malformations of intestine?

The ICD-10-CM code for other specified congenital malformations of intestine is Q43.8 (sometimes written as Q438). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q43.8 (Other congenital malformations of intestine) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of intestine on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q43.8 group to?

When other specified congenital malformations of intestine is the principal diagnosis on an inpatient stay, it groups to MS-DRG 394, 395, 393, with relative weights from 0.6379 to 1.5877 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q43.8 a CC or MCC?

CMS lists Q43.8 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 21 closely related codes in its exclusion list.

Is Q43.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of intestine on inpatient claims. The code appears in the Other congenital malformations of the digestive system (Q38-Q45) range of the CMS exempt list.