2026 ICD-10-CM Diagnosis Code Q43.8Other specified congenital malformations of intestine

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q43

ICD-10-CM Q43.8
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q43.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of intestine. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 393 through 395. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q43.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of intestine
Short Description
Other specified congenital malformations of intestine
Same as the full description in the CMS dataset.
Parent Code
Q43
Other congenital malformations of intestine

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ43Other congenital malformations of intestine
This CodeQ43.8Other specified congenital malformations of intestine

Present on Admission (POA)Billing

Q43.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Anal fissure
  • Anorectal fissure
  • Aphalangy, hemivertebra, urogenital, intestinal dysgenesis syndrome
  • Asplenia
  • Band of Ladd
  • Blind loop syndrome
  • Cecum in left sided position
  • Cloacal disease
  • Congenital absence of spleen
  • Congenital anal fissure
  • Congenital anomaly of appendix
  • Congenital blind loop syndrome
  • Congenital diaphragmatic hernia
  • Congenital dilatation of intestinal tract
  • Congenital dilatation of urinary bladder
  • Congenital diverticulitis of small intestine
  • Congenital diverticulosis
  • Congenital diverticulosis of small intestine
  • Congenital diverticulum of colon
  • Congenital diverticulum of duodenum
  • Congenital diverticulum of intestinal tract
  • Congenital diverticulum of large intestine
  • Congenital diverticulum of small intestine
  • Congenital dysmotility of small intestine
  • Congenital enterocyte heparan sulfate deficiency
  • Congenital fistula of intestinal tract
  • Congenital fistula of rectum
  • Congenital functional disorders of the colon
  • Congenital functional disorders of the small intestine
  • Congenital gastric heterotopia of duodenum
  • Congenital hypoganglionosis of large intestine
  • Congenital hypoplasia of intestinal tract
  • Congenital interstitial cell of Cajal hyperplasia with neuronal intestinal dysplasia
  • Congenital malposition of intestinal tract
  • Congenital malrotation of duodenum
  • Congenital megaduodenum
  • Congenital microvillous atrophy
  • Congenital neurogenic ileus syndrome
  • Congenital prolapsed rectum
  • Congenital rectal fissure
  • Congenital rectocloacal fistula
  • Congenital redundant colon
  • Congenital redundant rectal mucosa
  • Congenital short bowel syndrome
  • Congenital small anus
  • Congenital volvulus
  • Diaphragmatic hernia, short bowel, asplenia syndrome
  • Distension of urinary bladder
  • Diverticulum of duodenum
  • Diverticulum of large intestine
  • Dolichocolon
  • Duodenal web
  • Ectopic gastric tissue
  • Ectopic intestinal mucosa
  • Enterogenous cyst
  • Familial absence of villi
  • Gastroduodenal disorder
  • Generalized congenital intestinal dysmotility
  • High anorectal malformation
  • Intermediate anorectal malformation
  • Intestinal epithelial dysplasia
  • Intestinal volvulus
  • Low anorectal malformation
  • Malrotation of small intestine
  • Malrotation of the intestine type IIA
  • Megacystis, microcolon, hypoperistalsis syndrome
  • Megaduodenum
  • Megaloappendix
  • Microcolon
  • Motility disorder of small intestine
  • Neuronal intestinal dysplasia
  • Rectal prolapse
  • Short bowel syndrome
  • Situs inversus abdominalis
  • Situs inversus viscerum
  • Tortuous colon
  • Transposition of appendix
  • Transposition of cecum
  • Transposition of colon
  • Transposition of intestine

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital blind loop syndrome
  • Congenital diverticulitis, colon
  • Congenital diverticulum, intestine
  • Dolichocolon
  • Megaloappendix
  • Megaloduodenum
  • Microcolon
  • Transposition of appendix
  • Transposition of colon
  • Transposition of intestine

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • appendix
    • Anomaly, anomalous(congenital) (unspecified type)
      • jejunum
    • Appendage
      • intestine (epiploic)
    • Blind
      • loop syndrome
        • congenital
    • Cyst(colloid) (mucous) (simple) (retention)
      • enterogenous
    • Disease, diseased
      • microvillus
        • atrophy
    • Disease, diseased
      • microvillus
        • inclusion (MVD)
    • Displacement, displaced
      • appendix, retrocecal (congenital)
    • Diverticulitis(acute)
      • intestine
        • congenital
    • Diverticulum, diverticula(multiple)
      • cecum
        • congenital
    • Diverticulum, diverticula(multiple)
      • colon
        • congenital
    • Diverticulum, diverticula(multiple)
      • duodenum
        • congenital
    • Diverticulum, diverticula(multiple)
      • rectosigmoid
        • congenital
    • Diverticulum, diverticula(multiple)
      • sigmoid
        • congenital
    • Dolichocolon
    • Elongated, elongation(congenital)
      • colon
    • Excess, excessive, excessively
      • large
        • colon
          • congenital
    • Fissure, fissured
      • anus, anal
        • congenital
    • Formation
      • valve
        • colon, congenital
    • Imperfect
      • closure (congenital)
        • alimentary tract NEC
          • lower
    • Intussusception(bowel) (colon) (enteric) (ileocecal) (ileocolic) (intestine) ( rectum)
      • congenital
    • Malformation(congenital)
      • intestine
        • specified type NEC
    • Malposition
      • congenital
        • alimentary tract
          • lower
    • Malposition
      • congenital
        • appendix
    • Malposition
      • congenital
        • cecum
    • Malposition
      • congenital
        • colon
    • Malposition
      • congenital
        • digestive organ or tract NEC
          • lower
    • Malposition
      • congenital
        • intestine (large) (small)
    • Megaloappendix
    • Megaloduodenum
    • Microcolon(congenital)
    • Microvillus inclusion disease(MVD) (MVID)
    • MVD(microvillus inclusion disease)
    • MVID(microvillus inclusion disease)
    • Patulous
      • alimentary tract
        • lower
    • Persistence, persistent(congenital)
      • pancreatic tissue in intestinal tract
    • Redundant, redundancy
      • anus (congenital)
    • Redundant, redundancy
      • colon (congenital)
    • Redundant, redundancy
      • intestine (congenital)
    • Redundant, redundancy
      • rectum (congenital)
    • Redundant, redundancy
      • sigmoid (congenital)
    • Syndrome
      • blind loop
        • congenital
    • Telescoped bowel or intestine
      • congenital
    • Transposition(congenital)
      • appendix
    • Transposition(congenital)
      • colon
    • Transposition(congenital)
      • intestine (large) (small)
    • Volvulus(bowel) (colon) (intestine)
      • congenital
    • Web, webbed(congenital)
      • duodenal

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Short Bowel Syndrome

    a malabsorption syndrome resulting from extensive operative resection of the small intestine, the absorptive region of the gastrointestinal tract.

  • Rectal Prolapse

    protrusion of the rectal mucous membrane through the anus. there are various degrees: incomplete with no displacement of the anal sphincter muscle; complete with displacement of the anal sphincter muscle; complete with no displacement of the anal sphincter muscle but with herniation of the bowel; and internal complete with rectosigmoid or upper rectum intussusception into the lower rectum.

  • Blind Loop Syndrome

    a malabsorption syndrome that is associated with a blind loop in the upper small intestine that is characterized by the lack of peristaltic movement, stasis of intestinal contents, and the overgrowth of bacteria. such bacterial overgrowth interferes with bile salts action, fatty acids processing, microvilli integrity, and the absorption of nutrients such as vitamin b12 and folic acid.

  • Intestinal Volvulus

    a twisting in the intestine (intestines) that can cause intestinal obstruction.

  • Tortuous Colon

    a colon that is longer than a normal colon, with additional bends and twists.

  • Congenital Diaphragmatic Hernia

    diaphragmatic hernia that is present at birth.

  • Microcolon

    a rare congenital abnormality characterized by the presence of an abnormally small colon. it is the result of intestinal underutilization during fetal development.

  • MMIH Syndrome|Megacystis, Microcolon, Hypoperistalsis Syndrome|Megacystis, Microcolon, Intestinal Hypoperistalsis Syndrome|Megacystis, Microcolon, Intestinal Hypoperistalsis Syndrome

    a rare syndrome characterized by the presence of an enlarged and weak bladder (megacystis), a very small large intestine (microcolon), and weak small intestine that does not function properly (hypoperistalsis). it is caused by a disorder of the smooth muscles of the abdomen and gastrointestinal tract.

  • Low Anorectal Malformation

    congenital malformations in the anorectal region that include the perineal fistula, anteriorly placed anus, and anorecto-vestibular fistula.

  • Short Bowel Syndrome

    malabsorption that results from the removal of a large segment of the small intestine or, less frequently, from the complete dysfunction of a large portion of the small intestine. signs and symptoms include diarrhea, steatorrhea, and weight loss.

  • Duodenal Web

    partial or complete obstruction of the duodenal lumen due to the presence of a membranous web.

  • Rectal Prolapse

    protrusion of the rectum through the anus.

  • Intestinal Volvulus

    twisting of a loop of bowel that results in intestinal obstruction.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q43.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
751.5 Intestinal anomaly NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q43.8Overview

Is Q43.8 (Other congenital malformations of intestine) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of intestine on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q43.8 group to?

When other specified congenital malformations of intestine is the principal diagnosis on an inpatient stay, it groups to MS-DRG 393, 394, 395, with relative weights from 0.6490 to 1.5993 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q43.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of intestine on inpatient claims.

What is the ICD-9 equivalent of Q43.8?

Under the General Equivalence Mappings, other specified congenital malformations of intestine converts to ICD-9-CM 751.5 (intestinal anomaly NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.