2026 ICD-10-CM Diagnosis Code Q25.79Other congenital malformations of pulmonary artery

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.79
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q25.79 is a billable ICD-10-CM diagnosis code for other congenital malformations of pulmonary artery. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.79
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of pulmonary artery
Short Description
Other congenital malformations of pulmonary artery
Same as the full description in the CMS dataset.
Parent Code
Q25.7
Other congenital malformations of pulmonary artery

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.79Other congenital malformations of pulmonary artery

Present on Admission (POA)Billing

Q25.79 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal origin of left pulmonary artery
  • Abnormal origin of right pulmonary artery
  • Agenesis of artery
  • Agenesis of pulmonary artery
  • Agenesis of pulmonary trunk
  • Anomalous origin of left pulmonary artery from ascending aorta
  • Anomalous origin of left pulmonary artery from ductus arteriosus
  • Anomalous origin of left pulmonary artery from right pulmonary artery
  • Anomalous origin of pulmonary artery
  • Anomalous origin of pulmonary artery from ascending aorta
  • Anomalous origin of pulmonary artery from patent arterial duct
  • Anomalous origin of right pulmonary artery from ascending aorta
  • Anomalous origin of right pulmonary artery from ductus arteriosus
  • Arterial duct dependent pulmonary circulation
  • Atresia of pulmonary trunk with absent left pulmonary artery
  • Atresia of pulmonary trunk with absent right pulmonary artery
  • Bronchopulmonary collateral artery
  • Collaterals to pulmonary arteries
  • Complete congenital absence of pulmonary trunk with complete congenital absence of left pulmonary artery
  • Complete congenital absence of pulmonary trunk with complete congenital absence of pulmonary artery
  • Complete congenital absence of pulmonary trunk with complete congenital absence of right pulmonary artery
  • Confluent pulmonary arteries
  • Congenital abnormality of pulmonary trunk
  • Congenital abnormality of thoracic aorta and pulmonary arteries
  • Congenital absence of left pulmonary artery
  • Congenital absence of pulmonary artery
  • Congenital absence of pulmonary trunk
  • Congenital absence of pulmonary trunk with confluent pulmonary arteries
  • Congenital absence of pulmonary trunk with non-confluent pulmonary arteries
  • Congenital absence of right pulmonary artery
  • Congenital anomaly of abdominal aorta
  • Congenital anomaly of descending thoracic aorta
  • Congenital anomaly of left renal artery
  • Congenital anomaly of pulmonary artery
  • Congenital anomaly of right renal artery
  • Congenital atresia of pulmonary artery
  • Congenital atresia of pulmonary valve
  • Congenital dilatation of pulmonary artery
  • Congenital dilation of left pulmonary artery
  • Congenital dilation of right pulmonary artery
  • Congenital hypoplasia of left pulmonary artery
  • Congenital hypoplasia of left side of chest
  • Congenital hypoplasia of pulmonary artery
  • Congenital hypoplasia of right pulmonary artery
  • Congenital hypoplasia of right side of chest
  • Congenital malposition of lung
  • Congenital malposition of pulmonary artery
  • Congenital pulmonary artery conduit
  • Dilatation of pulmonary artery
  • Discontinuous pulmonary arteries
  • Major aortopulmonary collateral artery
  • Major systemic to pulmonary collateral artery
  • Major systemic to pulmonary collateral artery supplying both lungs
  • Major systemic to pulmonary collateral artery supplying entire left lung
  • Major systemic to pulmonary collateral artery supplying entire right lung
  • Major systemic to pulmonary collateral artery supplying part of left lung
  • Major systemic to pulmonary collateral artery supplying part of right lung
  • Major systemic to pulmonary collateral artery supplying unknown zone of distribution
  • Major systemic to pulmonary collateral artery with absent pulmonary arteries proximal to hilar bifurcation
  • Major systemic to pulmonary collateral artery with pulmonary artery proximal to hilar bifurcation
  • Pulmonary artery connecting to coronary artery via collateral artery
  • Pulmonary artery with absent proximal arterial connection
  • Pulmonary atresia with absent pulmonary artery
  • Pulmonary atresia with confluent pulmonary arteries
  • Pulmonary atresia with ventricular septal defect
  • Pulmonary trunk abnormality
  • Pulmonary trunk atresia
  • Pulmonary trunk hypoplasia
  • Retroesophageal pulmonary artery
  • Right pulmonary artery with absent proximal arterial connection
  • Right-sided pulmonary arterial trunk
  • Stenosis of systemic to pulmonary artery collateral artery
  • Systemic to pulmonary collateral artery
  • Systemic to pulmonary collateral artery connecting with artery
  • Systemic to pulmonary collateral artery connecting with central pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with isolated intraparenchymal pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with tracheobronchial arteries
  • Systemic to pulmonary collateral artery contributing to dual lung supply
  • Systemic to pulmonary collateral artery from abdominal aorta
  • Systemic to pulmonary collateral artery from coronary artery
  • Systemic to pulmonary collateral artery from descending thoracic aorta
  • Systemic to pulmonary collateral artery from left brachiocephalic artery
  • Systemic to pulmonary collateral artery from left carotid artery
  • Systemic to pulmonary collateral artery from left renal artery
  • Systemic to pulmonary collateral artery from right brachiocephalic artery
  • Systemic to pulmonary collateral artery from right carotid artery
  • Systemic to pulmonary collateral artery from right renal artery
  • Tetralogy of Fallot
  • Tetralogy of Fallot with atresia of pulmonary valve
  • Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery
  • Vascular ring with right aortic arch and right arterial ligament with absent left pulmonary artery
  • Vascular ring with right aortic arch and right patent arterial duct with absent left pulmonary artery

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Aberrant pulmonary artery
  • Agenesis of pulmonary artery
  • Congenital aneurysm of pulmonary artery
  • Congenital anomaly of pulmonary artery
  • Hypoplasia of pulmonary artery

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aberrant(congenital)
      • artery (peripheral)
        • pulmonary
    • Abnormal, abnormality, abnormalities
      • pulmonary
        • artery, congenital
    • Absence(of) (organ or part) (complete or partial)
      • artery (congenital) (peripheral)
        • pulmonary
    • Agenesis
      • artery (peripheral)
        • pulmonary
    • Aneurysm(anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular)
      • congenital (peripheral)
        • pulmonary
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • pulmonary NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • origin
        • artery
          • pulmonary
    • Anomaly, anomalous(congenital) (unspecified type)
      • pulmonary
        • artery NEC
    • Hypoplasia, hypoplastic
      • artery (peripheral)
        • pulmonary
    • Malformation(congenital)
      • pulmonary
        • artery
          • specified type NEC
    • Malposition
      • congenital
        • artery (peripheral)
          • pulmonary

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Tetralogy of Fallot

    a combination of congenital heart defects consisting of four key features including ventricular septal defects; pulmonary stenosis; right ventricular hypertrophy; and a dextro-positioned aorta. in this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing cyanosis.

  • Pulmonary Trunk Hypoplasia

    underdeveloped pulmonary arteries.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.79 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.39 Oth anom pul artery/circ
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q25.79Overview

Is Q25.79 (Other congenital malformations of pulmonary artery) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of pulmonary artery on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q25.79 group to?

When other congenital malformations of pulmonary artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.79 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of pulmonary artery on inpatient claims.

What is the ICD-9 equivalent of Q25.79?

Under the General Equivalence Mappings, other congenital malformations of pulmonary artery converts to ICD-9-CM 747.39 (oth anom pul artery/circ). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.