2027 ICD-10-CM Diagnosis Code Q25.79Other congenital malformations of pulmonary artery

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.79
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q25.79 is a billable ICD-10-CM diagnosis code for other congenital malformations of pulmonary artery. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 11 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.79
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of pulmonary artery
Short Description
Other congenital malformations of pulmonary artery
Same as the full description in the CMS dataset.
Parent Code
Q25.7
Other congenital malformations of pulmonary artery

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.79Other congenital malformations of pulmonary artery

Present on Admission (POA)Billing

Q25.79 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal origin of left pulmonary artery
  • Abnormal origin of right pulmonary artery
  • Agenesis of artery
  • Agenesis of pulmonary artery
  • Agenesis of pulmonary trunk
  • Anomalous origin of left pulmonary artery from ascending aorta
  • Anomalous origin of left pulmonary artery from ductus arteriosus
  • Anomalous origin of left pulmonary artery from right pulmonary artery
  • Anomalous origin of pulmonary artery
  • Anomalous origin of pulmonary artery from ascending aorta
  • Anomalous origin of pulmonary artery from patent arterial duct
  • Anomalous origin of right pulmonary artery from ascending aorta
  • Anomalous origin of right pulmonary artery from ductus arteriosus
  • Arterial duct dependent pulmonary circulation
  • Atresia of pulmonary trunk with absent left pulmonary artery
  • Atresia of pulmonary trunk with absent right pulmonary artery
  • Bronchopulmonary collateral artery
  • Collaterals to pulmonary arteries
  • Complete congenital absence of pulmonary trunk with complete congenital absence of left pulmonary artery
  • Complete congenital absence of pulmonary trunk with complete congenital absence of pulmonary artery
  • Complete congenital absence of pulmonary trunk with complete congenital absence of right pulmonary artery
  • Confluent pulmonary arteries
  • Congenital abnormality of pulmonary trunk
  • Congenital abnormality of thoracic aorta and pulmonary arteries
  • Congenital absence of left pulmonary artery
  • Congenital absence of pulmonary artery
  • Congenital absence of pulmonary trunk
  • Congenital absence of pulmonary trunk with confluent pulmonary arteries
  • Congenital absence of pulmonary trunk with non-confluent pulmonary arteries
  • Congenital absence of right pulmonary artery
  • Congenital anomaly of abdominal aorta
  • Congenital anomaly of descending thoracic aorta
  • Congenital anomaly of left renal artery
  • Congenital anomaly of pulmonary artery
  • Congenital anomaly of right renal artery
  • Congenital atresia of pulmonary artery
  • Congenital atresia of pulmonary valve
  • Congenital critical stenosis of pulmonary valve with ductus arteriosus dependent pulmonary circulation
  • Congenital dilatation of pulmonary artery
  • Congenital dilation of left pulmonary artery
  • Congenital dilation of right pulmonary artery
  • Congenital hypoplasia of left pulmonary artery
  • Congenital hypoplasia of left side of chest
  • Congenital hypoplasia of pulmonary artery
  • Congenital hypoplasia of right pulmonary artery
  • Congenital hypoplasia of right side of chest
  • Congenital malposition of lung
  • Congenital malposition of pulmonary artery
  • Congenital pulmonary artery conduit
  • Dilatation of pulmonary artery
  • Discontinuous pulmonary arteries
  • Major aortopulmonary collateral artery
  • Major systemic to pulmonary collateral artery
  • Major systemic to pulmonary collateral artery supplying both lungs
  • Major systemic to pulmonary collateral artery supplying entire left lung
  • Major systemic to pulmonary collateral artery supplying entire right lung
  • Major systemic to pulmonary collateral artery supplying part of left lung
  • Major systemic to pulmonary collateral artery supplying part of right lung
  • Major systemic to pulmonary collateral artery supplying unknown zone of distribution
  • Major systemic to pulmonary collateral artery with absent pulmonary arteries proximal to hilar bifurcation
  • Major systemic to pulmonary collateral artery with pulmonary artery proximal to hilar bifurcation
  • Pulmonary artery connecting to coronary artery via collateral artery
  • Pulmonary artery with absent proximal arterial connection
  • Pulmonary atresia with absent pulmonary artery
  • Pulmonary atresia with confluent pulmonary arteries
  • Pulmonary atresia with ventricular septal defect
  • Pulmonary trunk abnormality
  • Pulmonary trunk atresia
  • Pulmonary trunk hypoplasia
  • Retroesophageal pulmonary artery
  • Right pulmonary artery with absent proximal arterial connection
  • Right-sided pulmonary arterial trunk
  • Stenosis of systemic to pulmonary artery collateral artery
  • Systemic to pulmonary collateral artery
  • Systemic to pulmonary collateral artery connecting with artery
  • Systemic to pulmonary collateral artery connecting with central pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with isolated intraparenchymal pulmonary arteries
  • Systemic to pulmonary collateral artery connecting with tracheobronchial arteries
  • Systemic to pulmonary collateral artery contributing to dual lung supply
  • Systemic to pulmonary collateral artery from abdominal aorta
  • Systemic to pulmonary collateral artery from coronary artery
  • Systemic to pulmonary collateral artery from descending thoracic aorta
  • Systemic to pulmonary collateral artery from left brachiocephalic artery
  • Systemic to pulmonary collateral artery from left carotid artery
  • Systemic to pulmonary collateral artery from left renal artery
  • Systemic to pulmonary collateral artery from right brachiocephalic artery
  • Systemic to pulmonary collateral artery from right carotid artery
  • Systemic to pulmonary collateral artery from right renal artery
  • Tetralogy of Fallot
  • Tetralogy of Fallot with atresia of pulmonary valve
  • Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery
  • Vascular ring with right aortic arch and right arterial ligament with absent left pulmonary artery
  • Vascular ring with right aortic arch and right patent arterial duct with absent left pulmonary artery

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q25.79: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Aberrant pulmonary artery
  • Agenesis of pulmonary artery
  • Congenital aneurysm of pulmonary artery
  • Congenital anomaly of pulmonary artery
  • Hypoplasia of pulmonary artery

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q25.79, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q25.79: they are not reported together with it, unless the two conditions are unrelated.

  • I28.1 Aneurysm of pulmonary artery
    congenital aneurysm (Q25.79)

Excludes2 2

These codes carry an Excludes2 note naming Q25.79: its condition is not part of those codes, and both may be reported when the patient has both.

  • Q28 Other congenital malformations of circulatory system
    congenital pulmonary aneurysm (Q25.79)
  • Q27 Other congenital malformations of peripheral vascular system
    anomalies of pulmonary artery (Q25.5-Q25.7) names Q25.5-Q25.7, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.79 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.39 Oth anom pul artery/circ
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q25.79Overview

What is the ICD-10 code for other congenital malformations of pulmonary artery?

The ICD-10-CM code for other congenital malformations of pulmonary artery is Q25.79 (sometimes written as Q2579). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q25.79 (Other congenital malformations of pulmonary artery) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of pulmonary artery on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q25.79 group to?

When other congenital malformations of pulmonary artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.79 a CC or MCC?

CMS lists Q25.79 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 11 closely related codes in its exclusion list.

Is Q25.79 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of pulmonary artery on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.