2021 ICD-10-CM Code Q25.4

Other congenital malformations of aorta

Version 2021
Replaced Code
Non-Billable Code

Not Valid for Submission

Q25.4 is a "header" nonspecific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of other congenital malformations of aorta. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

ICD-10:Q25.4
Short Description:Other congenital malformations of aorta
Long Description:Other congenital malformations of aorta

Code Classification

Specific Coding for Other congenital malformations of aorta

Header codes like Q25.4 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for other congenital malformations of aorta:

  • Q25.40 - Congenital malformation of aorta unspecified
  • Q25.41 - Absence and aplasia of aorta
  • Q25.42 - Hypoplasia of aorta
  • Q25.43 - Congenital aneurysm of aorta
  • Q25.44 - Congenital dilation of aorta
  • Q25.45 - Double aortic arch
  • Q25.46 - Tortuous aortic arch
  • Q25.47 - Right aortic arch
  • Q25.48 - Anomalous origin of subclavian artery
  • Q25.49 - Other congenital malformations of aorta

Replaced Code

This code was replaced in the 2021 ICD-10 code set with the code(s) listed below. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2020. This code was replaced for the FY 2021 (October 1, 2020 - September 30, 2021).


  • Q25.40 - Congenital malformation of aorta unspecified
  • Q25.40 - Congenital malformation of aorta unspecified
  • Q25.41 - Absence and aplasia of aorta
  • Q25.41 - Absence and aplasia of aorta
  • Q25.42 - Hypoplasia of aorta
  • Q25.42 - Hypoplasia of aorta
  • Q25.43 - Congenital aneurysm of aorta
  • Q25.43 - Congenital aneurysm of aorta
  • Q25.44 - Congenital dilation of aorta
  • Q25.44 - Congenital dilation of aorta
  • Q25.45 - Double aortic arch
  • Q25.45 - Double aortic arch
  • Q25.46 - Tortuous aortic arch
  • Q25.46 - Tortuous aortic arch
  • Q25.47 - Right aortic arch
  • Q25.47 - Right aortic arch
  • Q25.48 - Anomalous origin of subclavian artery
  • Q25.48 - Anomalous origin of subclavian artery
  • Q25.49 - Other congenital malformations of aorta
  • Q25.49 - Other congenital malformations of aorta

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q25.4:


Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Information for Patients


Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute


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Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)