Congenital malformations of pulmonary and tricuspid valves (Q22)

ICD-10 code Q22 covers congenital malformations involving the pulmonary and tricuspid heart valves. These codes are specifically used to identify and classify birth defects of these heart valves, including conditions such as pulmonary valve atresia, tricuspid stenosis, and Ebstein's anomaly.

The section begins with Q22.0 for pulmonary valve atresia, which is also known as congenital atresia of the pulmonary valve or hypoplasia of the pulmonary valve. This code is essential for capturing complex defects like Tetralogy of Fallot with pulmonary valve issues. Q22.1 denotes congenital pulmonary valve stenosis, often linked with double outlet right ventricle or Tetralogy of Fallot variations. Insufficiency or leaking of the pulmonary valve is coded as Q22.2. Other abnormalities affecting the pulmonary valve, including cusp abnormalities and valve dysplasia, fall under Q22.3. For tricuspid valve issues, congenital tricuspid stenosis (Q22.4) includes Ebstein’s anomaly and valve atresia, while Q22.5 specifically codes for Ebstein’s anomaly itself, which may present with atrial septal defects. Hypoplastic right heart syndrome is identified by Q22.6. Additional congenital problems such as accessory tissues, valve clefts, and chordae abnormalities of the tricuspid valve are classified under Q22.8, and unspecified congenital tricuspid malformations are coded as Q22.9. Using these codes accurately helps medical professionals and coders pinpoint rare pediatric heart valve defects and tailor clinical care and reporting accordingly.