Congenital malformations of pulmonary and tricuspid valves (Q22) ICD-10-CM
The Q22 code range covers congenital malformations of pulmonary and tricuspid valves with 10 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the Q22 Range 10 codes · 9 billable
- Q22 Congenital malformations of pulmonary and tricuspid valvesNon-billable
- Q22.0 Pulmonary valve atresia
- Q22.1 Congenital pulmonary valve stenosis
- Q22.2 Congenital pulmonary valve insufficiency
- Q22.3 Other congenital malformations of pulmonary valve
- Q22.4 Congenital tricuspid stenosis
- Q22.5 Ebstein's anomaly
- Q22.6 Hypoplastic right heart syndrome
- Q22.8 Other congenital malformations of tricuspid valve
- Q22.9 Congenital malformation of tricuspid valve, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q22 range.
Congenital Malformation of Tricuspid Valve
A defect of the tricuspid valve present at birth.
Congenital Pulmonary Valve Insufficiency
Dysfunction of the pulmonary valve characterized by incomplete valve closure that is present at birth.
Congenital Pulmonary Valve Stenosis
Pulmonary valve stenosis that is present at birth.
Congenital Tricuspid Valve Stenosis
Tricuspid valve stenosis that is present at birth.
Ebstein Anomaly
A congenital heart defect characterized by downward or apical displacement of the TRICUSPID VALVE, usually with the septal and posterior leaflets being attached to the wall of the RIGHT VENTRICLE. It is characterized by a huge RIGHT ATRIUM and a small and less effective right ventricle.
Hypoplastic Right Heart Syndrome
A rare congenital cardiovascular disorder characterized by severe underdevelopment of the right side of the heart. The infants develop cyanosis shortly after birth. It is a condition that requires immediate emergency treatment.
Pulmonary Atresia
A congenital heart defect characterized by the narrowing or complete absence of the opening between the RIGHT VENTRICLE and the PULMONARY ARTERY. Lacking a normal PULMONARY VALVE, unoxygenated blood in the right ventricle can not be effectively pumped into the lung for oxygenation. Clinical features include rapid breathing, CYANOSIS, right ventricle atrophy, and abnormal heart sounds (HEART MURMURS).
About the Q22 Code Range
These conditions involve pulmonary or tricuspid valves that formed differently before birth.
The pulmonary valve entries separate named conditions (Q22.0, Q22.1, and Q22.2) from other malformations (Q22.3). The remaining entries identify named tricuspid valve conditions (Q22.4 and Q22.5), a right-heart condition (Q22.6), and other or unspecified tricuspid valve malformations (Q22.8 and Q22.9).
Questions About This Page
How many billable codes are in the Q22 range?
Of the 10 codes in this range, 9 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q22 range classify?
The range classifies congenital malformations of pulmonary and tricuspid valves. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
