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  5. Other congenital malformations of heart (Q24)

Other congenital malformations of heart (Q24)

ICD-10 codes in the Q24 section classify various rare and specific congenital malformations of the heart, including structural and conduction abnormalities present from birth. These codes capture conditions such as dextrocardia (Q24.0), pulmonary infundibular stenosis (Q24.3), and congenital heart block (Q24.6). The system also covers complex deformities of coronary vessels (Q24.5), subaortic stenosis (Q24.4), and other specified congenital heart malformations (Q24.8), as well as unspecified congenital heart defects (Q24.9).

This grouping includes unique cardiac anomalies such as dextrocardia, also known as congenital malposition or mirror-imaged heart, and cor triatriatum (Q24.2), a condition involving division of the atrium. Injuries to heart function like congenital conduction defects are captured under congenital heart block (Q24.6). The code for malformations of coronary vessels (Q24.5) includes anomalies like congenital coronary artery fistulas and abnormal artery origins. The extensive Q24.8 code encompasses a wide range of other less common or complex malformations, aiding precise classification of rare cardiac structural abnormalities, which facilitates accurate documentation and coding of congenital heart disease cases. Coders searching for the ICD-10 code for specific congenital heart conditions will find this section essential for detailed and precise diagnosis reporting.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • endocardial fibroelastosis I42.4

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Cardiomegaly

Enlargement of the HEART, usually indicated by a cardiothoracic ratio above 0.50. Heart enlargement may involve the right, the left, or both HEART VENTRICLES or HEART ATRIA. Cardiomegaly is a nonspecific symptom seen in patients with chronic systolic heart failure (HEART FAILURE) or several forms of CARDIOMYOPATHIES.

Cardiomegaly, Exercise-Induced

Non-pathological heart enlargement and other remodeling in cardiac morphology and electrical circuitry found in individuals who participate in intense repeated exercises.

Choanal Atresia

A congenital abnormality that is characterized by a blocked CHOANAE, the opening between the nose and the NASOPHARYNX. Blockage can be unilateral or bilateral; bony or membranous.

Cor Triatriatum

A malformation of the heart in which the embryonic common PULMONARY VEIN was not incorporated into the LEFT ATRIUM leaving behind a perforated fibromuscular membrane bisecting the left atrium, a three-atrium heart. The opening between the two left atrium sections determines the degree of obstruction to pulmonary venous return, pulmonary venous and pulmonary arterial hypertension.

Dextrocardia

A congenital defect in which the heart is located on the right side of the THORAX instead of on the left side (levocardia, the normal position). When dextrocardia is accompanied with inverted HEART ATRIA, a right-sided STOMACH, and a left-sided LIVER, the combination is called dextrocardia with SITUS INVERSUS. Dextrocardia may adversely affect other thoracic organs.

Ectopia Cordis

A rare developmental defect in which the heart is abnormally located partially or totally outside the THORAX. It is the result of defective fusion of the anterior chest wall. Depending on the location of the heart, ectopia cordis can be thoracic, thoracoabdominal, abdominal, and cervical.

Kartagener Syndrome

An autosomal recessive disorder characterized by a triad of DEXTROCARDIA; INFERTILITY; and SINUSITIS. The syndrome is caused by mutations of DYNEIN genes encoding motility proteins which are components of sperm tails, and CILIA in the respiratory and the reproductive tracts.

Levocardia

Congenital abnormalities in which the HEART is in the normal position (levocardia) in the left side of the chest but some or all of the THORAX or ABDOMEN viscera are transposed laterally (SITUS INVERSUS). It is also known as situs inversus with levocardia, or isolated levocardia. This condition is often associated with severe heart defects and splenic abnormalities such as asplenia or polysplenia.

Thorax

The upper part of the trunk between the NECK and the ABDOMEN. It contains the chief organs of the circulatory and respiratory systems. (From Stedman, 25th ed)